Impact of concurrent tumour events on the prostate cancer outcomes of germline BRCA2 mutation carriers.


Journal

European journal of cancer (Oxford, England : 1990)
ISSN: 1879-0852
Titre abrégé: Eur J Cancer
Pays: England
ID NLM: 9005373

Informations de publication

Date de publication:
05 2023
Historique:
received: 07 12 2022
revised: 21 02 2023
accepted: 22 02 2023
medline: 16 5 2023
pubmed: 28 3 2023
entrez: 27 3 2023
Statut: ppublish

Résumé

Several studies have reported the association of germline BRCA2 (gBRCA2) mutations with poor clinical outcomes in prostate cancer (PCa), but the impact of concurrent somatic events on gBRCA2 carriers survival and disease progression is unknown. To ascertain the role of frequent somatic genomic alterations and histology subtypes in the outcomes of gBRCA2 mutation carriers and non-carriers, we correlated the tumour characteristics and clinical outcomes of 73 gBRCA2 and 127 non-carriers. Fluorescent in-situ hybridisation and next-generation sequencing were used to detect copy number variations in BRCA2, RB1, MYC and PTEN. Presence of intraductal and cribriform subtypes was also assessed. The independent impact of these events on cause-specific survival (CSS), metastasis-free survival and time to castration-resistant disease was assessed using cox-regression models. Somatic BRCA2-RB1 co-deletion (41% versus 12%, p < 0.001) and MYC amplification (53.4% versus 18.8%, p < 0.001) were enriched in gBRCA2 compared to sporadic tumours. Median CSS from diagnosis of PCa was 9.1 versus 17.6 years in gBRCA2 carriers and non-carriers, respectively (HR 2.12; p = 0.002), Median CSS in gBRCA2 carriers increased to 11.3 and 13.4 years in the absence of BRCA2-RB1 deletion or MYC amplification, respectively. Median CSS of non-carriers decreased to 8 and 2.6 years if BRCA2-RB1 deletion or MYC amplification were detected. gBRCA2-related prostate tumours are enriched for aggressive genomic features, such as BRCA2-RB1 co-deletion and MYC amplification. The presence or absence of these events modify the outcomes of gBRCA2 carriers.

Sections du résumé

BACKGROUND
Several studies have reported the association of germline BRCA2 (gBRCA2) mutations with poor clinical outcomes in prostate cancer (PCa), but the impact of concurrent somatic events on gBRCA2 carriers survival and disease progression is unknown.
PATIENTS AND METHODS
To ascertain the role of frequent somatic genomic alterations and histology subtypes in the outcomes of gBRCA2 mutation carriers and non-carriers, we correlated the tumour characteristics and clinical outcomes of 73 gBRCA2 and 127 non-carriers. Fluorescent in-situ hybridisation and next-generation sequencing were used to detect copy number variations in BRCA2, RB1, MYC and PTEN. Presence of intraductal and cribriform subtypes was also assessed. The independent impact of these events on cause-specific survival (CSS), metastasis-free survival and time to castration-resistant disease was assessed using cox-regression models.
RESULTS
Somatic BRCA2-RB1 co-deletion (41% versus 12%, p < 0.001) and MYC amplification (53.4% versus 18.8%, p < 0.001) were enriched in gBRCA2 compared to sporadic tumours. Median CSS from diagnosis of PCa was 9.1 versus 17.6 years in gBRCA2 carriers and non-carriers, respectively (HR 2.12; p = 0.002), Median CSS in gBRCA2 carriers increased to 11.3 and 13.4 years in the absence of BRCA2-RB1 deletion or MYC amplification, respectively. Median CSS of non-carriers decreased to 8 and 2.6 years if BRCA2-RB1 deletion or MYC amplification were detected.
CONCLUSIONS
gBRCA2-related prostate tumours are enriched for aggressive genomic features, such as BRCA2-RB1 co-deletion and MYC amplification. The presence or absence of these events modify the outcomes of gBRCA2 carriers.

Identifiants

pubmed: 36972661
pii: S0959-8049(23)00116-8
doi: 10.1016/j.ejca.2023.02.022
pii:
doi:

Substances chimiques

BRCA2 Protein 0
BRCA2 protein, human 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't Research Support, U.S. Gov't, P.H.S.

Langues

eng

Sous-ensembles de citation

IM

Pagination

105-118

Informations de copyright

Copyright © 2023 Elsevier Ltd. All rights reserved.

Auteurs

Rebeca Lozano (R)

Genitourinary Cancer Translational Research Unit, Instituto de Investigación Biomédica de Málaga (IBIMA), Málaga, Spain; Department of Medical Oncology, Hospital Universitario de Salamanca, Salamanca, Spain.

Elena Castro (E)

Genitourinary Cancer Translational Research Unit, Instituto de Investigación Biomédica de Málaga (IBIMA), Málaga, Spain; Translational Cancer Genetics Group, Hospital Universitario 12 de Octubre, Madrid, Spain. Electronic address: ecastro.imas12@h12o.es.

Fernando Lopez-Campos (F)

Department of Radiation Oncology, Hospital Universitario Ramón y Cajal, Madrid, Spain.

Heather Thorne (H)

kConFab, The Peter MacCallum Cancer Centre, Melbourne, Australia.

Miguel Ramirez-Backhaus (M)

Urology Department, Fundación Instituto Valenciano de Oncología, Valencia, Spain.

Isabel M Aragon (IM)

Genitourinary Cancer Translational Research Unit, Instituto de Investigación Biomédica de Málaga (IBIMA), Málaga, Spain.

Ylenia Cendón-Florez (Y)

Genitourinary Cancer Translational Research Unit, Instituto de Investigación Biomédica de Málaga (IBIMA), Málaga, Spain.

Ana Gutierrez-Pecharroman (A)

Genitourinary Cancer Translational Research Unit, Instituto de Investigación Biomédica de Málaga (IBIMA), Málaga, Spain; Department of Pathology, Hospital de Getafe, Getafe, Spain.

Daniela C Salles (DC)

Department of Pathology, John Hopkins University School of Medicine, Baltimore, USA.

Nuria Romero-Laorden (N)

Medical Oncology Department, Hospital Universitario La Princesa, Madrid, Spain.

David Lorente (D)

Medical Oncology Department, Hospital Provincial de Castellón, Castellón de la Plana, Spain.

Pilar González-Peramato (P)

Pathology Department, Hospital Universitario La Paz, Universidad Autónoma de Madrid, Madrid, Spain.

Ana Calatrava (A)

Pathology Department, Fundación Instituto Valenciano de Oncología, Valencia, Spain.

Concepción Alonso (C)

Genetics Department, Hospital Universitario La Princesa, Madrid, Spain.

Urbano Anido (U)

Medical Oncology Department, Hospital Clínico Universitario de Santiago, Santiago de Compostela, Spain.

Sara Arévalo-Lobera (S)

Medical Oncology Department, Hospital Universitario de Donostia, Donostia, Spain.

Judith Balmaña (J)

Vall d'Hebron Institute of Oncology (VHIO), Barcelona, Spain; Vall d´HebronUniversity Hospital, Barcelona, Spain.

Isabel Chirivella (I)

Medical Oncology Department, Hospital Clínico Universitario de Valencia, Valencia, Spain.

María José Juan-Fita (MJ)

Medical Oncology Department, Fundación Instituto Valenciano de Oncología, Valencia, Spain.

Gemma Llort (G)

Medical Oncology Department, Parc Taulí Hospital Universitari, Sabadell, Spain.

Teresa Ramón Y Cajal (TR)

Medical Oncology Department, Hospital de la Santa Creu i Sant Pau, Barcelona, Spain.

Elena Almagro (E)

Medical Oncology Department, Hospital Universitario Quirón, Pozuelo de Alarcón, Madrid, Spain.

Daniel Alameda (D)

Genitourinary Cancer Translational Research Unit, Instituto de Investigación Biomédica de Málaga (IBIMA), Málaga, Spain.

Pedro P López-Casas (PP)

Genomics and Therapeutics in Prostate Cancer Group, Medical Oncology Department, Hospital Universitario 12 de Octubre, Instituto de Investigación Sanitaria 12 de Octubre (Imas12), Madrid, Spain.

Bernardo Herrera (B)

Genitourinary Cancer Translational Research Unit, Instituto de Investigación Biomédica de Málaga (IBIMA), Málaga, Spain; Urology Department, Hospital Universitario Virgen de la Victoria, Málaga, Spain.

Joaquin Mateo (J)

Vall d'Hebron Institute of Oncology (VHIO), Barcelona, Spain; Vall d´HebronUniversity Hospital, Barcelona, Spain.

Colin C Pritchard (CC)

Department of Laboratory Medicine and Pathology, University of Washington, Seattle, USA.

Emmanuel S Antonarakis (ES)

Department of Medical Oncology, John Hopkins University School of Medicine, Baltimore, USA.

Tamara L Lotan (TL)

Department of Pathology, John Hopkins University School of Medicine, Baltimore, USA.

José Rubio-Briones (J)

Urology Department, Fundación Instituto Valenciano de Oncología, Valencia, Spain.

Shahneen Sandhu (S)

Sir Peter MacCallum Department of Oncology, The University of Melbourne, Parkville, Victoria, Australia.

David Olmos (D)

Genomics and Therapeutics in Prostate Cancer Group, Medical Oncology Department, Hospital Universitario 12 de Octubre, Instituto de Investigación Sanitaria 12 de Octubre (Imas12), Madrid, Spain.

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