Invasive fungal diseases in patients with autoimmune diseases: a case series from the French RESSIF network.


Journal

RMD open
ISSN: 2056-5933
Titre abrégé: RMD Open
Pays: England
ID NLM: 101662038

Informations de publication

Date de publication:
08 2023
Historique:
received: 03 05 2023
accepted: 28 07 2023
medline: 11 8 2023
pubmed: 10 8 2023
entrez: 9 8 2023
Statut: ppublish

Résumé

We aimed to describe patients with autoimmune diseases (AID) developing invasive fungal disease (IFD) and identify factors associated with short-term mortality. We analysed cases of IFD associated with AID from the surveillance network of invasive fungal diseases (Réseau de surveillance des infections fongiques invasives, RESSIF) registry of the French national reference centre for invasive mycoses. We studied association of AID-specific treatments with 30-day mortality. We analysed total lymphocyte and CD4-T cell counts in patients with From 2012 to 2018, 549 individuals with IFD and AID were included, mainly with PCP (n=227, 41.3%), fungemia (n=167, 30.4%) and invasive aspergillosis (n=84, 15.5%). Rheumatoid arthritis (RA) and anti-neutrophil cytoplasmic antibodies (ANCA)-associated vasculitides (AAV) were the most frequent AID in PCP (n=55 and 25, respectively) and invasive aspergillosis (n=15 and 10, respectively), inflammatory bowel diseases (IBDs) were predominant in fungemia (n=36). At IFD diagnosis, 365 (66.5%) patients received glucocorticoids (GCs), 285 (51.9%) immunosuppressants, 42 (7.7%) tumor necrosis factor (TNF)-α blockers, 75 (13.7%) other biologics. Mortality at 30 days was 28.1% (143/508). Fungemia and high-dose GCs were independently associated with higher 30-day mortality. In PCP patients, lymphopenia <1500/mm IFD associated with AID occurs primarily in RA, AAV and IBD, especially when treated with GCs and immunosuppressants. Mortality is high, especially for patients on high-dose GCs. Lymphopenia may help identify risk of PCP, but normal CD4+T cell count does not rule out the risk. Further studies are needed to assess the individual risk factors for IFD.

Identifiants

pubmed: 37558492
pii: rmdopen-2023-003281
doi: 10.1136/rmdopen-2023-003281
pmc: PMC10414070
pii:
doi:

Substances chimiques

Glucocorticoids 0
Immunosuppressive Agents 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Investigateurs

Eric Bailly (E)
Caroline Mahinc (C)
Marc Pihet (M)
Magalie Demar (M)
Lilia Merabet (L)
Valery Salle (V)
Céline Damiani (C)
Marie-Fleur Durieux (MF)
Nassim Kamar (N)
Elena Charpentier (E)
François Maillot (F)
Cécile Nourrisson (C)
Benoit Suzon (B)

Informations de copyright

© Author(s) (or their employer(s)) 2023. Re-use permitted under CC BY-NC. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: None declared.

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Auteurs

Simon Galmiche (S)

Emerging Diseases Epidemiology Unit, Institut Pasteur, Université Paris Cité, Paris, Île-de-France, France simon.galmiche@pasteur.fr.
Ecole doctorale Pierre Louis de santé publique, Sorbonne Université, Paris, France.

Benjamin Thoreau (B)

National Referral Center for Rare Systemic Autoimmune Diseases, Department of Internal Medicine, Cochin Hospital, AP-HP, Université Paris Cité, Paris, Île-de-France, France.
INSERM U1016, Cochin Institute, Paris, Université Paris Cité, CNRS UMR 8104, Paris, Île-de-France, France.

Stéphane Bretagne (S)

Parasitologie - Mycologie, Hôpital St Louis, APHP, Paris, Île-de-France, France.
Institut Pasteur, Université Paris Cité, CNRS, National Reference Center for Invasive Mycoses and Antifungals, Translational Mycology Research Group, Mycology Department, Paris, Île-de-France, France.

Alexandre Alanio (A)

Parasitologie - Mycologie, Hôpital St Louis, APHP, Paris, Île-de-France, France.
Institut Pasteur, Université Paris Cité, CNRS, National Reference Center for Invasive Mycoses and Antifungals, Translational Mycology Research Group, Mycology Department, Paris, Île-de-France, France.

André Paugam (A)

Parasitologie - Mycologie, Université Paris Cité, Cochin Hospital, APHP, Paris, Île-de-France, France.

Valérie Letscher-Bru (V)

Laboratoire de Parasitologie et Mycologie Médicale, Les Hôpitaux Universitaires de Strasbourg, Strasbourg, France.
Institut de Parasitologie et Pathologie Tropicale, UR7292 Dynamique des interactions hôte pathogène, Fédération de Médecine Translationnelle, Université de Strasbourg, Strasbourg, France.

Sophie Cassaing (S)

Parasitologie - Mycologie, Université de Toulouse, CHU Toulouse, Toulouse, Occitanie, France.
PharmaDev, Faculté de Pharmacie, Université de Toulouse, UPS, IRD, Toulouse, Occitanie, France.

Jean-Pierre Gangneux (JP)

Université de Rennes, CHU, INSERM, Irset: Institut de Recherche en Santé, Environnement et Travail, UMR_S 1085, Rennes, France.

Hélène Guegan (H)

Université de Rennes, CHU, INSERM, Irset: Institut de Recherche en Santé, Environnement et Travail, UMR_S 1085, Rennes, France.

Loïc Favennec (L)

French National Cryptosporidiosis Reference Center, CHU de Rouen, Rouen, Normandie, France.
EA 7510, UFR Santé, University of Rouen Normandy, Normandy University, Rouen, France.

Alida Minoza (A)

Faculté de Médecine et Pharmacie, Université de Poitiers, Poitiers, Nouvelle-Aquitaine, France.
Département des agents anti-infectieux, Service de Mycologie-Parasitologie, CHU Poitiers, Poitiers, France.

Florent Morio (F)

Parasitologie - Mycologie, CHU Nantes, Nantes, Pays de la Loire, France.
UR 1155 IICiMed, Institut de Recherche en Santé 2, Université de Nantes, Nantes, Pays de la Loire, France.

Julie Bonhomme (J)

Microbiologie, CHU de Caen, ToxEMAC-ABTE Unicaen, Caen, Normandie, France.

Guillaume Desoubeaux (G)

Centre d'Étude des Pathologies Respiratoires - Inserm UMR1100, Université de Tours, Tours, France.
Parasitologie - Mycologie - Médecine tropicale, CHU de Tours, Tours, Centre-Val de Loire, France.

Odile Eloy (O)

Microbiologie, CH Versailles, Le Chesnay, Île-de-France, France.

Lilia Hasseine (L)

Parasitologie - Mycologie, hôpital de l'Archet, CHU Nice, Nice, Provence-Alpes-Côte d'Azur, France.

Milène Sasso (M)

Laboratoire de Parasitologie - Mycologie, CHU Nîmes, Université de Montpellier, CNRS, IRD, MiVEGEC, Nimes, Occitanie, France.

Laurence Millon (L)

Laboratoire de Parasitologie - Mycologie, CHU de Besançon, Besançon, Bourgogne-Franche-Comté, France.
UMR 6249 CNRS Chrono-Environnement, Université Bourgogne Franche-Comté, Besançon, Bourgogne - Franche-Comté, France.

Anne-Pauline Bellanger (AP)

Laboratoire de Parasitologie - Mycologie, CHU de Besançon, Besançon, Bourgogne-Franche-Comté, France.

Philippe Poirier (P)

Parasitologie - Mycologie, CHU Clermont-Ferrand, Clermont-Ferrand, France.
Microbes, Intestin, Inflammation et Susceptibilité de l'Hôte (M2iSH), UMR Inserm/Université Clermont Auvergne U1071, USC INRA 2018, Clermont-Ferrand, Auvergne-Rhône-Alpes, France.

Maxime Moniot (M)

Parasitologie - Mycologie, CHU Clermont-Ferrand, Clermont-Ferrand, France.

Taieb Chouaki (T)

Mycologie - parasitologie, CHU Amiens-Picardie, Amiens, Hauts-de-France, France.

Antoine Huguenin (A)

Parasitologie - Mycologie, hôpital Maison-Blanche, CHU de Reims, Reims, France.

Frédéric Dalle (F)

Parasitologie - Mycologie, Plateforme de Biologie Hospitalo-Universitaire Gérard Mack, Dijon, Bourgogne-Franche-Comté, France.
UMR PAM Univ Bourgogne Franche-Comté - AgroSup Dijon - Equipe Vin, Aliment, Microbiologie, Stress, Université Bourgogne Franche-Comté, Dijon, Bourgogne-Franche-Comté, France.

Bernard Bouteille (B)

Parasitologie - Mycologie, Centre de Biologie et de Recherche en Santé, CHU Limoges, Limoges, Nouvelle-Aquitaine, France.

Muriel Nicolas (M)

Mycologie - Parasitologie, Centre Hospitalier Universitaire Pointe-à-Pitre Abymes, Pointe-à-Pitre, Guadeloupe.

Nicole Desbois-Nogard (N)

Parasitologie - Mycologie, CHU de Martinique, Fort-de-France, Martinique.

Marie-Elisabeth Bougnoux (ME)

Laboratoire de Parasitologie - Mycologie, Service de Microbiologie, Necker-Enfants Malades University Hospital, APHP, Paris, Île-de-France, France.
Institut Pasteur, Université Paris Cité, Unité Biologie et Pathogénicité Fongiques, Département Mycologie, Paris, Île-de-France, France.

François Danion (F)

Maladies infectieuses et tropicales, Les Hôpitaux Universitaires de Strasbourg, Strasbourg, Grand Est, France.
Laboratoire d'Immuno-rhumatologie moléculaire UMR_S 1109, INSERM, Strasbourg, Grand Est, France.

Vincent Poindron (V)

Service d'Immunologie clinique, Hopitaux universitaires de Strasbourg, Strasbourg, France.

Antoine Néel (A)

CRTI UMR 1064, INSERM, Université de Nantes, Nantes, France.
Service de Médecine interne, CHU Nantes, Nantes, Pays de la Loire, France.

Karine Boukris-Sitbon (K)

Institut Pasteur, Université Paris Cité, CNRS, National Reference Center for Invasive Mycoses and Antifungals, Translational Mycology Research Group, Mycology Department, Paris, Île-de-France, France.

Fanny Lanternier (F)

Institut Pasteur, Université Paris Cité, CNRS, National Reference Center for Invasive Mycoses and Antifungals, Translational Mycology Research Group, Mycology Department, Paris, Île-de-France, France.
Infectious Diseases Unit, Necker-Enfants Malades University Hospital, AP-HP, Paris, France.

Benjamin Terrier (B)

National Referral Center for Rare Systemic Autoimmune Diseases, Department of Internal Medicine, Cochin Hospital, AP-HP, Université Paris Cité, Paris, Île-de-France, France.
Université Paris Cité, U970, PARCC, INSERM, Paris, Île-de-France, France.

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Classifications MeSH