Anesthesia management in a child with mucopolysaccharidosis and toxic epidermal necrolysis: A case report.
airway management
anesthesia
child
mucopolysaccharidosis type II
ophthalmic surgical procedures
toxic epidermal necrolysis
Journal
Paediatric anaesthesia
ISSN: 1460-9592
Titre abrégé: Paediatr Anaesth
Pays: France
ID NLM: 9206575
Informations de publication
Date de publication:
Jan 2024
Jan 2024
Historique:
revised:
13
07
2023
received:
04
04
2023
accepted:
31
07
2023
medline:
7
12
2023
pubmed:
14
8
2023
entrez:
14
8
2023
Statut:
ppublish
Résumé
Toxic epidermal necrolysis and mucopolysaccharidosis are both rare diseases that pose significant airway maintenance challenges to anesthesiologists. In this report, we describe the anesthesia management in a 4-year-old male with mucopolysaccharidosis type II who developed toxic epidermal necrolysis and presented for ophthalmic surgical procedures. Combined use of propofol and ketamine with the support of high-flow nasal oxygen enabled adequate analgesia and sedation while maintaining spontaneous ventilation and airway patency. The strategy presented in this report may contribute to enhancing the safety of sedation in spontaneously breathing children with abnormal airways.
Substances chimiques
Propofol
YI7VU623SF
Ketamine
690G0D6V8H
Types de publication
Case Reports
Langues
eng
Sous-ensembles de citation
IM
Pagination
89-91Informations de copyright
© 2023 John Wiley & Sons Ltd.
Références
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Foo YT, Noor MN, Yazid BM, et al. Ketamine-propofol (Ketofol) for procedural sedation and analgesia in children: a systematic review and meta-analysis. BMC Emerg Med. 2020;20:1-14.
Hillman RD, Platt RP, Eastwood RP. The upper airway during anaesthesia. Br J Anaesth. 2003;91:31-39.
Milési C, Boubal M, Jacquot A, et al. High-flow nasal cannula: recommendations for daily practice in pediatrics. Ann Intensive Care. 2014;4:1-7.