Pulmonary homograft failure presents as abdominal ascites.


Journal

BMJ case reports
ISSN: 1757-790X
Titre abrégé: BMJ Case Rep
Pays: England
ID NLM: 101526291

Informations de publication

Date de publication:
16 Aug 2023
Historique:
pmc-release: 16 08 2025
medline: 18 8 2023
pubmed: 17 8 2023
entrez: 16 8 2023
Statut: epublish

Résumé

Ascites is a condition typically attributed to liver disease but can be cardiac in aetiology as well. We report of an atypical case of pulmonary homograft failure status-post the Ross-Yacoub procedure as an underlying cause of anasarca. A man in his mid-30s with a history of congenital heart disease presented with abdominal distension and exercise intolerance. His prior history was relevant for congenital bicuspid aortic valve with critical aortic stenosis. Abdomen and pelvis CT revealed a grossly dilated inferior vena cava while transthoracic echocardiogram showed severe homograft pulmonary stenosis and regurgitation. Further investigation with cardiac MRI demonstrated severe pulmonary valve stenosis and regurgitation with significant tricuspid regurgitation and right ventricular dilatation. The transcatheter stent in the right ventricular to pulmonary artery conduit followed by transcatheter valve replacement, which resulted in full resolution of his presenting symptoms.

Identifiants

pubmed: 37586754
pii: 16/8/e255128
doi: 10.1136/bcr-2023-255128
pmc: PMC10432667
pii:
doi:

Types de publication

Case Reports Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© BMJ Publishing Group Limited 2023. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: None declared.

Auteurs

Kimberly Renae Ding (KR)

Internal Medicine, Harbor-UCLA Medical Center, Torrance, California, USA kding247@gmail.com.

Jamil Aboulhosn (J)

Department of Medicine, Division of Cardiology, Ahmanson/UCLA Adult Congenital Cardiology Center, University of California Los Angeles, Los Angeles, California, USA.

Priya Pillutla (P)

Department of Medicine, Division of Cardiology, Harbor-UCLA Medical Center, Torrance, California, USA.

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