Simona Boncompagni

Affiliations

Department of Neuroscience, Imaging and Clinical Sciences and Center for Advanced Studies and Technology, University G. d'Annunzio, Chieti, Italy.

Publications (30)

Ablation of palladin in adult heart causes dilated cardiomyopathy associated with intercalated disc abnormalities.

eLife

Avec: Giuseppina Mastrototaro , Pierluigi Carullo , Jianlin Zhang , Beatrice Scellini , Nicoletta Piroddi , Simona Nemska , Maria Carmela Filomena , Simone Serio , Carol A Otey , Chiara Tesi , Fabian Emrich , Wolfgang A Linke , Corrado Poggesi , Simona Boncompagni , Marie-Louise Bang

Quantitative RyR1 reduction and loss of calcium sensitivity of RyR1Q1970fsX16+A4329D cause cores and loss of muscle strength.

Human molecular genetics

Avec: Moran Elbaz , Alexis Ruiz , Christoph Bachmann , Jan Eckhardt , Pawel Pelczar , Elisa Venturi , Chris Lindsay , Abigail D Wilson , Ahmed Alhussni , Thomas Humberstone , Laura Pietrangelo , Simona Boncompagni , Rebecca Sitsapesan , Susan Treves , Francesco Zorzato

Transverse tubule remodeling enhances Orai1-dependent Ca

eLife

Avec: Antonio Michelucci , Simona Boncompagni , Laura Pietrangelo , Maricela García-Castañeda , Takahiro Takano , Sundeep Malik , Robert T Dirksen , Feliciano Protasi

Electron Microscopy (EM) Analysis of Collagen Fibers in the Peri-Implant Soft Tissues around Two Different Abutments.

Journal of functional biomaterials

Avec: Ugo Covani , Enrica Giammarinaro , Natalia Di Pietro , Simona Boncompagni , Giorgia Rastelli , Tea Romasco , Eugenio Velasco-Ortega , Alvaro Jimenez-Guerra , Giovanna Iezzi , Adriano Piattelli , Simone Marconcini

Mitochondria can substitute for parvalbumin to lower cytosolic calcium levels in the murine fast skeletal muscle.

Acta physiologica (Oxford, England)

Avec: Lorenzo Marcucci , Leonardo Nogara , Marta Canato , Elena Germinario , Anna Raffaello , Michela Carraro , Paolo Bernardi , Laura Pietrangelo , Simona Boncompagni , Feliciano Protasi , Nazareno Paolocci , Carlo Reggiani

An Orai1 gain-of-function tubular aggregate myopathy mouse model phenocopies key features of the human disease.

The EMBO journal

Avec: Nan Zhao , Antonio Michelucci , Laura Pietrangelo , Sundeep Malik , Linda Groom , Jennifer Leigh , Thomas N O'Connor , Takahiro Takano , Paul D Kingsley , James Palis , Simona Boncompagni , Feliciano Protasi , Robert T Dirksen

Long-Term Exercise Reduces Formation of Tubular Aggregates and Promotes Maintenance of Ca

Frontiers in physiology

Avec: Simona Boncompagni , Claudia Pecorai , Antonio Michelucci , Laura Pietrangelo , Feliciano Protasi

Skeletal muscle mTORC1 regulates neuromuscular junction stability.

Journal of cachexia, sarcopenia and muscle

Avec: Martina Baraldo , Alessia Geremia , Marco Pirazzini , Leonardo Nogara , Francesca Solagna , Clara Türk , Hendrik Nolte , Vanina Romanello , Aram Megighian , Simona Boncompagni , Marcus Kruger , Marco Sandri , Bert Blaauw

Pre-assembled Ca2+ entry units and constitutively active Ca2+ entry in skeletal muscle of calsequestrin-1 knockout mice.

The Journal of general physiology

Avec: Antonio Michelucci , Simona Boncompagni , Laura Pietrangelo , Takahiro Takano , Feliciano Protasi , Robert T Dirksen

Redox-Sensitive Glyoxalase 1 Up-Regulation Is Crucial for Protecting Human Lung Cells from Gold Nanoparticles Toxicity.

Antioxidants (Basel, Switzerland)

Avec: Angela Gambelunghe , Stefano Giovagnoli , Alessandro Di Michele , Simona Boncompagni , Marco Dell'Omo , Kerstin Leopold , Ivo Iavicoli , Vincenzo Nicola Talesa , Cinzia Antognelli

Defective endoplasmic reticulum-mitochondria contacts and bioenergetics in SEPN1-related myopathy.

Cell death and differentiation

Avec: Anne Filipe , Alexander Chernorudskiy , Sandrine Arbogast , Ersilia Varone , Rocío-Nur Villar-Quiles , Diego Pozzer , Maryline Moulin , Stefano Fumagalli , Eva Cabet , Swati Dudhal , Maria-Grazia De Simoni , Raphaël Denis , Nathalie Vadrot , Corinne Dill , Matteo Giovarelli , Luke Szweda , Clara De Palma , Paolo Pinton , Carlotta Giorgi , Carlo Viscomi , Emilio Clementi , Sonia Missiroli , Simona Boncompagni , Ester Zito , Ana Ferreiro

Improper Remodeling of Organelles Deputed to Ca

International journal of molecular sciences

Avec: Feliciano Protasi , Laura Pietrangelo , Simona Boncompagni

Loss of calpain 3 dysregulates store-operated calcium entry and its exercise response in mice.

bioRxiv : the preprint server for biology

Avec: Katelyn R Villani , Renjia Zhong , C Spencer Henley-Beasley , Giorgia Rastelli , Simona Boncompagni , Elisabeth R Barton , Lan Wei-LaPierre

Tailored Ag-Cu-Mg multielemental nanoparticles for wide-spectrum antibacterial coating.

Nanoscale

Avec: Giulio Benetti , Emanuele Cavaliere , Rosaria Brescia , Sebastian Salassi , Riccardo Ferrando , André Vantomme , Lucia Pallecchi , Simona Pollini , Selene Boncompagni , Beatrice Fortuni , Margriet J Van Bael , Francesco Banfi , Luca Gavioli

Quantitative reduction of RyR1 protein caused by a single-allele frameshift mutation in RYR1 ex36 impairs the strength of adult skeletal muscle fibres.

Human molecular genetics

Avec: Moran Elbaz , Alexis Ruiz , Jan Eckhardt , Pawel Pelczar , Francesco Muntoni , Simona Boncompagni , Susan Treves , Francesco Zorzato

Muscle activity prevents the uncoupling of mitochondria from Ca

Archives of biochemistry and biophysics

Avec: Laura Pietrangelo , Antonio Michelucci , Patrizia Ambrogini , Stefano Sartini , Flavia A Guarnier , Aurora Fusella , Ilaria Zamparo , Cristina Mammucari , Feliciano Protasi , Simona Boncompagni

Effects of Titanium Dioxide Nanoparticles on Porcine Prepubertal Sertoli Cells: An "

Frontiers in endocrinology

Avec: Francesca Mancuso , Iva Arato , Alessandro Di Michele , Cinzia Antognelli , Luca Angelini , Catia Bellucci , Cinzia Lilli , Simona Boncompagni , Aurora Fusella , Desirée Bartolini , Carla Russo , Massimo Moretti , Morena Nocchetti , Angela Gambelunghe , Giacomo Muzi , Tiziano Baroni , Stefano Giovagnoli , Giovanni Luca

Parvalbumin affects skeletal muscle trophism through modulation of mitochondrial calcium uptake.

Cell reports

Avec: Gaia Butera , Denis Vecellio Reane , Marta Canato , Laura Pietrangelo , Simona Boncompagni , Feliciano Protasi , Rosario Rizzuto , Carlo Reggiani , Anna Raffaello

Ageing Causes Ultrastructural Modification to Calcium Release Units and Mitochondria in Cardiomyocytes.

International journal of molecular sciences

Avec: Alessia Di Fonso , Laura Pietrangelo , Laura D'Onofrio , Antonio Michelucci , Simona Boncompagni , Feliciano Protasi

Impaired Binding to Junctophilin-2 and Nanostructural Alteration in CPVT Mutation.

Circulation research

Avec: Liheng Yin , Alexandra Zahradnikova , Riccardo Rizzetto , Simona Boncompagni , Camille Rabesahala de Meritens , Yadan Zhang , Pierre Joanne , Elena Marqués-Sulé , Yuriana Aguilar-Sánchez , Miguel Fernández-Tenorio , Olivier Villejoubert , Linwei Li , Yue Yi Wang , Philippe Mateo , Valérie Nicolas , Pascale Gerbaud , F Anthony Lai , Romain Perrier , Julio L Álvarez , Ernst Niggli , Héctor H Valdivia , Carmen R Valdivia , Josefina Ramos-Franco , Esther Zorio , Spyros Zissimopoulos , Feliciano Protasi , Jean-Pierre Benitah , Ana M Gómez

Constitutive assembly of Ca2+ entry units in soleus muscle from calsequestrin knockout mice.

The Journal of general physiology

Avec: Antonio Michelucci , Laura Pietrangelo , Giorgia Rastelli , Feliciano Protasi , Robert T Dirksen , Simona Boncompagni

Program with last minute abstracts of the Padua Days on Muscle and Mobility Medicine, 27 February - 2 March, 2024 (2024Pdm3).

European journal of translational myology

Avec: Sandra Zampieri , Ines Bersch , Piera Smeriglio , Elena Barbieri , Simona Boncompagni , Maria Chiara Maccarone , Ugo Carraro

Loss of Calpain 3 dysregulates store-operated calcium entry and its exercise response in mice.

FASEB journal : official publication of the Federation of American Societies for Experimental Biology

Avec: Katelyn R Villani , Renjia Zhong , C Spencer Henley-Beasley , Giorgia Rastelli , Erin Harris , Simona Boncompagni , Elisabeth R Barton , Lan Wei-LaPierre

An aged-related structural study of DHPR tetrads in peripheral couplings of human skeletal muscle.

European journal of translational myology

Avec: Laura Pietrangelo , Rosa Mancinelli , Stefania Fulle , Simona Boncompagni

Calcium entry units (CEUs): perspectives in skeletal muscle function and disease.

Journal of muscle research and cell motility

Avec: Feliciano Protasi , Laura Pietrangelo , Simona Boncompagni

Functional Electrical Stimulation: A Possible Strategy to Improve Muscle Function in Central Core Disease?

Frontiers in neurology

Avec: Pierpaolo Iodice , Simona Boncompagni , Laura Pietrangelo , Lucia Galli , Enrico Pierantozzi , Daniela Rossi , Aurora Fusella , Massimo Caulo , Helmut Kern , Vincenzo Sorrentino , Feliciano Protasi

DRP1-mediated mitochondrial shape controls calcium homeostasis and muscle mass.

Nature communications

Avec: Giulia Favaro , Vanina Romanello , Tatiana Varanita , Maria Andrea Desbats , Valeria Morbidoni , Caterina Tezze , Mattia Albiero , Marta Canato , Gaia Gherardi , Diego De Stefani , Cristina Mammucari , Bert Blaauw , Simona Boncompagni , Feliciano Protasi , Carlo Reggiani , Luca Scorrano , Leonardo Salviati , Marco Sandri

Ca

Frontiers in physiology

Avec: J Matthew Kittelberger , Clara Franzini-Armstrong , Simona Boncompagni

Diaphragm Fatigue in SMNΔ7 Mice and Its Molecular Determinants: An Underestimated Issue.

International journal of molecular sciences

Avec: Francesca Cadile , Deborah Recchia , Massimiliano Ansaldo , Paola Rossi , Giorgia Rastelli , Simona Boncompagni , Lorenza Brocca , Maria Antonietta Pellegrino , Monica Canepari

SEPN1-related myopathy depends on the oxidoreductase ERO1A and is druggable with the chemical chaperone TUDCA.

Cell reports. Medicine

Avec: Serena Germani , Andrew Tri Van Ho , Alessandro Cherubini , Ersilia Varone , Alexander Chernorudskiy , Giorgia Maria Renna , Stefano Fumagalli , Marco Gobbi , Jacopo Lucchetti , Marco Bolis , Luca Guarrera , Ilaria Craparotta , Giorgia Rastelli , Giorgia Piccoli , Cosimo de Napoli , Leonardo Nogara , Elena Poggio , Marisa Brini , Angela Cattaneo , Angela Bachi , Thomas Simmen , Tito Calì , Susana Quijano-Roy , Simona Boncompagni , Bert Blaauw , Ana Ferreiro , Ester Zito

Réseau de co-auteurs

Laura Pietrangelo 14 collaborations

Feliciano Protasi 14 collaborations

Antonio Michelucci 7 collaborations

Giorgia Rastelli 6 collaborations

Robert T Dirksen 4 collaborations

Takahiro Takano 3 collaborations

Leonardo Nogara 3 collaborations

Marta Canato 3 collaborations

Carlo Reggiani 3 collaborations

Bert Blaauw 3 collaborations

Aurora Fusella 3 collaborations

Moran Elbaz 2 collaborations

Alexis Ruiz 2 collaborations

Jan Eckhardt 2 collaborations

Pawel Pelczar 2 collaborations

Susan Treves 2 collaborations

Francesco Zorzato 2 collaborations

Sundeep Malik 2 collaborations

Anna Raffaello 2 collaborations

Vanina Romanello 2 collaborations

Marco Sandri 2 collaborations

Angela Gambelunghe 2 collaborations

Stefano Giovagnoli 2 collaborations

Alessandro Di Michele 2 collaborations

Cinzia Antognelli 2 collaborations

Alexander Chernorudskiy 2 collaborations

Ersilia Varone 2 collaborations

Stefano Fumagalli 2 collaborations

Ester Zito 2 collaborations

Ana Ferreiro 2 collaborations

Katelyn R Villani 2 collaborations

Renjia Zhong 2 collaborations

C Spencer Henley-Beasley 2 collaborations

Elisabeth R Barton 2 collaborations

Lan Wei-LaPierre 2 collaborations

Cristina Mammucari 2 collaborations

Giuseppina Mastrototaro 1 collaboration

Pierluigi Carullo 1 collaboration

Jianlin Zhang 1 collaboration

Beatrice Scellini 1 collaboration

Nicoletta Piroddi 1 collaboration

Simona Nemska 1 collaboration

Maria Carmela Filomena 1 collaboration

Simone Serio 1 collaboration

Carol A Otey 1 collaboration

Chiara Tesi 1 collaboration

Fabian Emrich 1 collaboration

Wolfgang A Linke 1 collaboration

Corrado Poggesi 1 collaboration

Marie-Louise Bang 1 collaboration

Christoph Bachmann 1 collaboration

Elisa Venturi 1 collaboration

Chris Lindsay 1 collaboration

Abigail D Wilson 1 collaboration

Ahmed Alhussni 1 collaboration

Thomas Humberstone 1 collaboration

Rebecca Sitsapesan 1 collaboration

Maricela García-Castañeda 1 collaboration

Ugo Covani 1 collaboration

Enrica Giammarinaro 1 collaboration

Natalia Di Pietro 1 collaboration

Tea Romasco 1 collaboration

Eugenio Velasco-Ortega 1 collaboration

Alvaro Jimenez-Guerra 1 collaboration

Giovanna Iezzi 1 collaboration

Adriano Piattelli 1 collaboration

Simone Marconcini 1 collaboration

Lorenzo Marcucci 1 collaboration

Elena Germinario 1 collaboration

Michela Carraro 1 collaboration

Paolo Bernardi 1 collaboration

Nazareno Paolocci 1 collaboration

Nan Zhao 1 collaboration

Linda Groom 1 collaboration

Jennifer Leigh 1 collaboration

Thomas N O'Connor 1 collaboration

Paul D Kingsley 1 collaboration

James Palis 1 collaboration

Claudia Pecorai 1 collaboration

Martina Baraldo 1 collaboration

Alessia Geremia 1 collaboration

Marco Pirazzini 1 collaboration

Francesca Solagna 1 collaboration

Clara Türk 1 collaboration

Hendrik Nolte 1 collaboration

Aram Megighian 1 collaboration

Marcus Kruger 1 collaboration

Marco Dell'Omo 1 collaboration

Kerstin Leopold 1 collaboration

Ivo Iavicoli 1 collaboration

Vincenzo Nicola Talesa 1 collaboration

Anne Filipe 1 collaboration

Sandrine Arbogast 1 collaboration

Rocío-Nur Villar-Quiles 1 collaboration

Diego Pozzer 1 collaboration

Maryline Moulin 1 collaboration

Eva Cabet 1 collaboration

Swati Dudhal 1 collaboration

Maria-Grazia De Simoni 1 collaboration

Raphaël Denis 1 collaboration

Nathalie Vadrot 1 collaboration

Corinne Dill 1 collaboration

Matteo Giovarelli 1 collaboration

Luke Szweda 1 collaboration

Clara De Palma 1 collaboration

Paolo Pinton 1 collaboration

Carlotta Giorgi 1 collaboration

Carlo Viscomi 1 collaboration

Emilio Clementi 1 collaboration

Sonia Missiroli 1 collaboration

Giulio Benetti 1 collaboration

Emanuele Cavaliere 1 collaboration

Rosaria Brescia 1 collaboration

Sebastian Salassi 1 collaboration

Riccardo Ferrando 1 collaboration

André Vantomme 1 collaboration

Lucia Pallecchi 1 collaboration

Simona Pollini 1 collaboration

Selene Boncompagni 1 collaboration

Beatrice Fortuni 1 collaboration

Margriet J Van Bael 1 collaboration

Francesco Banfi 1 collaboration

Luca Gavioli 1 collaboration

Francesco Muntoni 1 collaboration

Patrizia Ambrogini 1 collaboration

Stefano Sartini 1 collaboration

Flavia A Guarnier 1 collaboration

Ilaria Zamparo 1 collaboration

Francesca Mancuso 1 collaboration

Iva Arato 1 collaboration

Luca Angelini 1 collaboration

Catia Bellucci 1 collaboration

Cinzia Lilli 1 collaboration

Desirée Bartolini 1 collaboration

Carla Russo 1 collaboration

Massimo Moretti 1 collaboration

Morena Nocchetti 1 collaboration

Giacomo Muzi 1 collaboration

Tiziano Baroni 1 collaboration

Giovanni Luca 1 collaboration

Gaia Butera 1 collaboration

Denis Vecellio Reane 1 collaboration

Rosario Rizzuto 1 collaboration

Alessia Di Fonso 1 collaboration

Laura D'Onofrio 1 collaboration

Liheng Yin 1 collaboration

Alexandra Zahradnikova 1 collaboration

Riccardo Rizzetto 1 collaboration

Camille Rabesahala de Meritens 1 collaboration

Yadan Zhang 1 collaboration

Pierre Joanne 1 collaboration

Elena Marqués-Sulé 1 collaboration

Yuriana Aguilar-Sánchez 1 collaboration

Miguel Fernández-Tenorio 1 collaboration

Olivier Villejoubert 1 collaboration

Linwei Li 1 collaboration

Yue Yi Wang 1 collaboration

Philippe Mateo 1 collaboration

Valérie Nicolas 1 collaboration

Pascale Gerbaud 1 collaboration

F Anthony Lai 1 collaboration

Romain Perrier 1 collaboration

Julio L Álvarez 1 collaboration

Ernst Niggli 1 collaboration

Héctor H Valdivia 1 collaboration

Carmen R Valdivia 1 collaboration

Josefina Ramos-Franco 1 collaboration

Esther Zorio 1 collaboration

Spyros Zissimopoulos 1 collaboration

Jean-Pierre Benitah 1 collaboration

Ana M Gómez 1 collaboration

Sandra Zampieri 1 collaboration

Ines Bersch 1 collaboration

Piera Smeriglio 1 collaboration

Elena Barbieri 1 collaboration

Maria Chiara Maccarone 1 collaboration

Ugo Carraro 1 collaboration

Erin Harris 1 collaboration

Rosa Mancinelli 1 collaboration

Stefania Fulle 1 collaboration

Pierpaolo Iodice 1 collaboration

Lucia Galli 1 collaboration

Enrico Pierantozzi 1 collaboration

Daniela Rossi 1 collaboration

Massimo Caulo 1 collaboration

Helmut Kern 1 collaboration

Vincenzo Sorrentino 1 collaboration

Giulia Favaro 1 collaboration

Tatiana Varanita 1 collaboration

Maria Andrea Desbats 1 collaboration

Valeria Morbidoni 1 collaboration

Caterina Tezze 1 collaboration

Mattia Albiero 1 collaboration

Gaia Gherardi 1 collaboration

Diego De Stefani 1 collaboration

Luca Scorrano 1 collaboration

Leonardo Salviati 1 collaboration

J Matthew Kittelberger 1 collaboration

Clara Franzini-Armstrong 1 collaboration

Francesca Cadile 1 collaboration

Deborah Recchia 1 collaboration

Massimiliano Ansaldo 1 collaboration

Paola Rossi 1 collaboration

Lorenza Brocca 1 collaboration

Maria Antonietta Pellegrino 1 collaboration

Monica Canepari 1 collaboration

Serena Germani 1 collaboration

Andrew Tri Van Ho 1 collaboration

Alessandro Cherubini 1 collaboration

Giorgia Maria Renna 1 collaboration

Marco Gobbi 1 collaboration

Jacopo Lucchetti 1 collaboration

Marco Bolis 1 collaboration

Luca Guarrera 1 collaboration

Ilaria Craparotta 1 collaboration

Giorgia Piccoli 1 collaboration

Cosimo de Napoli 1 collaboration

Elena Poggio 1 collaboration

Marisa Brini 1 collaboration

Angela Cattaneo 1 collaboration

Angela Bachi 1 collaboration

Thomas Simmen 1 collaboration

Tito Calì 1 collaboration

Susana Quijano-Roy 1 collaboration