Une alimentation pauvre en cuivre peut aider à gérer la maladie et réduire les symptômes.
Régime alimentaireCuivre
#5
Les traitements sont-ils à vie ?
Oui, un traitement continu est souvent nécessaire pour contrôler la maladie.
Traitement à long termeDégénérescence hépatolenticulaire
Complications
5
#1
Quelles sont les complications possibles de la maladie ?
Les complications incluent des lésions hépatiques, des troubles neurologiques et psychiatriques.
ComplicationsDégénérescence hépatolenticulaire
#2
La cirrhose est-elle une complication fréquente ?
Oui, la cirrhose peut se développer en raison de l'accumulation de cuivre dans le foie.
CirrhoseDégénérescence hépatolenticulaire
#3
Les troubles mentaux peuvent-ils s'aggraver ?
Oui, sans traitement, les troubles mentaux peuvent s'aggraver et affecter la qualité de vie.
Troubles mentauxDégénérescence hépatolenticulaire
#4
Y a-t-il un risque accru de cancer du foie ?
Oui, les patients atteints de cirrhose ont un risque accru de développer un cancer du foie.
Cancer du foieCirrhose
#5
Les complications peuvent-elles être évitées ?
Un traitement précoce et régulier peut réduire le risque de complications graves.
Prévention des complicationsDégénérescence hépatolenticulaire
Facteurs de risque
5
#1
Quels sont les facteurs de risque de la maladie ?
Les antécédents familiaux et les mutations génétiques sont des facteurs de risque majeurs.
Facteurs de risqueDégénérescence hépatolenticulaire
#2
La consanguinité augmente-t-elle le risque ?
Oui, la consanguinité peut augmenter la probabilité de transmettre la maladie génétique.
ConsanguinitéDégénérescence hépatolenticulaire
#3
Les personnes d'ascendance spécifique sont-elles plus à risque ?
Oui, certaines populations, comme les Caucasiens, ont un risque plus élevé.
AscendanceDégénérescence hépatolenticulaire
#4
Les femmes sont-elles plus à risque que les hommes ?
Non, les deux sexes sont également affectés par la maladie de Wilson.
SexeDégénérescence hépatolenticulaire
#5
Les jeunes adultes sont-ils plus touchés ?
Oui, les symptômes apparaissent souvent entre 5 et 35 ans, mais peuvent survenir plus tôt.
Jeunes adultesDégénérescence hépatolenticulaire
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"position": 14,
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"@type": "Question",
"name": "Les personnes à risque doivent-elles être surveillées ?",
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"position": 17,
"acceptedAnswer": {
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"name": "La transplantation hépatique est-elle une option ?",
"position": 18,
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"@type": "Question",
"name": "Quel rôle joue la diététique dans le traitement ?",
"position": 19,
"acceptedAnswer": {
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"name": "Les traitements sont-ils à vie ?",
"position": 20,
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"name": "Quelles sont les complications possibles de la maladie ?",
"position": 21,
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"@type": "Question",
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"position": 23,
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"name": "Y a-t-il un risque accru de cancer du foie ?",
"position": 24,
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"position": 26,
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"name": "La consanguinité augmente-t-elle le risque ?",
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"@type": "Question",
"name": "Les personnes d'ascendance spécifique sont-elles plus à risque ?",
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}
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"position": 29,
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"@type": "Answer",
"text": "Non, les deux sexes sont également affectés par la maladie de Wilson."
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"@type": "Question",
"name": "Les jeunes adultes sont-ils plus touchés ?",
"position": 30,
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School of Pharmacy, Anhui University of Chinese Medicine, Hefei, China.
Anhui Province Key Laboratory of Research and Development of Chinese Medicine, Anhui Province Key Laboratory of Chinese Medicinal Formula, Hefei, China.
Publications dans "Dégénérescence hépatolenticulaire" :
The Experimental Research Center, Anhui University of Chinese Medicine, Hefei, China.
Anhui Province Key Laboratory of Research and Development of Chinese Medicine, Anhui Province Key Laboratory of Chinese Medicinal Formula, Hefei, China.
Publications dans "Dégénérescence hépatolenticulaire" :
Department of Gastroenterology, Xinhua Hospital Affiliated to Shanghai Jiaotong University School of Medicine, Shanghai Key Lab of Pediatric Gastroenterology and Nutrition, Shanghai 200092, China.
Publications dans "Dégénérescence hépatolenticulaire" :
Department of Gastroenterology, Xinhua Hospital Affiliated to Shanghai Jiaotong University School of Medicine, Shanghai Key Lab of Pediatric Gastroenterology and Nutrition, Shanghai 200092, China.
Publications dans "Dégénérescence hépatolenticulaire" :
School of Pharmacy, Anhui University of Chinese Medicine, Hefei, China.
Anhui Province Key Laboratory of Research and Development of Chinese Medicine, Anhui Province Key Laboratory of Chinese Medicinal Formula, Hefei, China.
Publications dans "Dégénérescence hépatolenticulaire" :
Difficult & Complicated Liver Diseases and Artificial Liver Center, Beijing You An Hospital, Capital Medical University & Beijing Municipal Key Laboratory of Liver Failure and Artificial Liver Treatment Research, Beijing 100069, China.
Publications dans "Dégénérescence hépatolenticulaire" :
Encephalopathy Center, the First Affiliated Hospital of Anhui University of Chinese Medicine, No 117 Meishan Road, Shushan District, Hefei, 230031, People's Republic of China.
Publications dans "Dégénérescence hépatolenticulaire" :
Encephalopathy Center, the First Affiliated Hospital of Anhui University of Chinese Medicine, No 117 Meishan Road, Shushan District, Hefei, 230031, People's Republic of China.
Publications dans "Dégénérescence hépatolenticulaire" :
Encephalopathy Center, the First Affiliated Hospital of Anhui University of Chinese Medicine, No 117 Meishan Road, Shushan District, Hefei, 230031, People's Republic of China.
Publications dans "Dégénérescence hépatolenticulaire" :
Neutrophilic eccrine hidradenitis (NEH) is a benign neutrophilic dermatosis not well recognized beyond an association with malignancy. Although the disease is commonly reported in adults with malignan...
A retrospective study was performed of adult and pediatric patients diagnosed with NEH at three Mayo Clinic sites from January 1, 1992, to January 1, 2022. The aim of this study was to elucidate risk ...
Of 47 patients identified, 33 had either histologic or clinical confirmation of the diagnosis; 21 were adults (64%), and 12 were children (36%). Most adults (16/21; 76%) had underlying malignancy and ...
Among adults, NEH is commonly associated with malignancy and chemotherapy. Among children, idiopathic NEH occurs primarily after overexertion, and malignancy is highly unlikely to be the cause of NEH....
although rare, gastrointestinal stromal tumors (GIST) are the most common mesenchymal tumors of the digestive tract. The aim of this work is to study the clinical, paraclinical, therapeutic and evolut...
we conducted a descriptive retrospective, monocentric study (April 2017-April 2021) collecting data from the medical records of all patients with GIST treated at the medical oncology department of the...
we collected data from the medical records of 23 patients, with a median age of 54.4 years, sex ratio 1.8, over a period of 4 years. Abdominal pain was the most frequent symptom (78.3%, n=18); 47.8% o...
the diagnosis of GIST is mainly based on histology and immunohistochemistry, which is often not performed by our pathologists. Molecular biology makes it possible to predict the prognosis and conseque...
Aotearoa New Zealand (AoNZ) guidelines suggest surveillance colonoscopy should be carefully considered after age 75. The authors noted a cluster of patients presenting in their 8th and 9th decade of l...
A 7-year retrospective analysis was performed of patients who underwent a colonoscopy aged between 71 and 75 years in the period between 2006 and 2012. Kaplan-Meier graphs were created with survival m...
A total of 623 patients met inclusion criteria; 461 (74%) had no indication for surveillance colonoscopy and 162 (26%) had an indication. Of the 162 patients with an indication, 91 (56.2%) underwent s...
This study found one quarter of patients who had a colonoscopy between the ages of 71-75 had an indication for surveillance colonoscopy. Most patients with a new CRC underwent surgery. This study sugg...
In box genioplasty it is possible to advance, retrude, impact, and elongate, as well as to correct asymmetry. The aim of this study was to analyse the stability of box genioplasty as part of orthognat...
World over studies are being done by different group of workers to understand the time of deliveries conducted. Surprisingly majority of deliveries were following a pattern, seasonally. Today in this ...
Present study conducted on semen quality included 12,408 semen samples collected from different laboratories of Bangalore city during 8 years (2000-2007) period of time and were analysed season wise....
Results showed sperm concentration was significantly lower in monsoon than in winter season. Humidity and pressure influenced sperm count. Forward moving sperms were influenced by temperature and pres...
The study concludes the change in birth rates seen during different season in a year is due to the quality of semen responsible for conception....
Rhabdomyolysis (RM) refers to a clinical syndrome in which muscle cells are damaged by various causes and the clinical manifestations are mainly muscle pain, weakness, and dark urine. Acute kidney inj...
Analysis of medical records of RM patients admitted to Tianjin Medical University General Hospital from October 2019 to October 2022. Statistical software SPSS 25.0 was used to analyze the data. The r...
Among the 71 patients, the median age of the patients was 53.0 (30.0, 71.0) years and was 2.5 times higher in men than in women. Infection was the most common etiology. History of alcohol consumption,...
Our study revealed the clinical and laboratory characteristics of RM in the population attending the Tianjin Medical University General Hospital in the last three years, which is a reference for futur...
Adolescent and young adult female patients receiving myelosuppressive cancer treatments are at risk of abnormal uterine bleeding (AUB). The frequency with which patients with cancer receive menstrual ...
We established a retrospective cohort of 90 females with a diagnosis of Hodgkin or non-Hodgkin lymphoma (n = 25), AML (n = 46), or sarcoma (n = 19) and treated with chemotherapy between 2008 and 2019 ...
The majority of patients (77.8%) received menstrual suppression. Compared with nonsuppressed patients, suppressed patients had similar rates of packed red blood cell transfusions but higher number of ...
Menstrual suppression was common in our cohort with variability in agents used. Pediatric and adult oncologists demonstrated different practice patterns....
The purpose of this study was to introduce the surgical process of Sommerlad-Furlow modified (S-F) palatoplasty and compare its surgical and functional outcomes with conventional Sommerlad (S) palatop...
This study aims to evaluate the surgical treatment and clinical outcomes of convergent dislocation of the elbow (CDE) in adults....
Between January 2017 and September 2022, we performed a retrospective study of patients with CDE presenting in XXX and XXX Hospital and receiving operative treatments after failed closed reductions. T...
Eleven patients were followed up for an average period of 9.8 months. Four males and seven females were enrolled, aged 31.5 ± 9.0 years. The average ROM of flexion-extension at the elbow was significa...
Our study showed several operative methods following failed closed reduction attempts where anatomical reduction of humeroulnar and proximal radioulnar joints and instant rehabilitation obtained relat...
Acromegaly is a multisystemic disease characterized by an excessive release of growth hormone (GH) and insulin-like growth factor-1. Obstructive sleep apnea (OSA) is a common consequence of acromegaly...
A retrospective analysis was conducted involving patients with acromegaly and OSA. The pharmacotherapy history for acromegaly before surgery, anthropometric measures, blood gas, sleep monitoring data,...
In this study, 94 patients with OSA and acromegaly were included. Among them, 25 (26.6%) had hypercapnia. The hypercapnic group had higher body mass index (92% vs. 62.3%; p = 0.005) and poorer nocturn...
Single-center evidence shows that hypercapnia alone may not be a risk factor for lower biochemical remission rates. Correcting hypercapnia does not appear to be required before surgery. More evidence ...