questionsmedicales.fr
Maladies du système immunitaire
Déficits immunitaires
Maladies d'immunodéficience primaire
Syndrome de Job
Syndrome de Job : Questions médicales fréquentes
Termes MeSH sélectionnés :
Diagnostic
5
Syndrome de Job
Immunodéficience
IgE
IgE
Tests sanguins
Infections
Syndrome de Job
Hérédité
Génétique
Infections cutanées
Pneumonie
Éruptions cutanées
Immunodéficience
Diagnostic différentiel
Tests spécifiques
Symptômes
5
Symptômes
Infections
Allergies
Éruptions cutanées
Prurit
Symptômes
Pneumonie
Infections respiratoires
Symptômes
Problèmes dentaires
Infections
Syndrome de Job
Allergies
Acariens
Pollens
Prévention
5
Prévention
Hygiène
Vaccination
Alimentation
Prévention
Santé
Vaccination
Prévention
Infections
Allergies
Antihistaminiques
Gestion
Soins dentaires
Infections
Prévention
Traitements
5
Antibiotiques
Antihistaminiques
Traitement
Immunothérapie
Allergies
Réponse immunitaire
Suivi médical
Infections
Traitement
Syndrome de Job
Traitement
Symptômes
Prévention
Vaccins
Infections
Complications
5
Complications
Infections
Problèmes respiratoires
Cancer
Lymphome
Syndrome de Job
Infections
Mortalité
Traitement
Complications dermatologiques
Infections cutanées
Abcès
Complications respiratoires
Pneumonie
Infections
Facteurs de risque
5
Facteurs de risque
Antécédents familiaux
Mutations génétiques
Enfants
Syndrome de Job
Infections
Immunodépression
Facteurs de risque
Syndrome de Job
Allergies
Facteurs de risque
Syndrome de Job
Infections fréquentes
Syndrome de Job
Facteurs de risque
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"name": "Quels signes cliniques indiquent ce syndrome ?",
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"position": 8,
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{
"@type": "Question",
"name": "Le syndrome de Job cause-t-il des problèmes dentaires ?",
"position": 9,
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{
"@type": "Question",
"name": "Les allergies sont-elles fréquentes dans ce syndrome ?",
"position": 10,
"acceptedAnswer": {
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{
"@type": "Question",
"name": "Comment prévenir les infections chez les patients ?",
"position": 11,
"acceptedAnswer": {
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}
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{
"@type": "Question",
"name": "Les patients doivent-ils éviter certains aliments ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'y a pas de restrictions alimentaires spécifiques, mais une alimentation équilibrée est conseillée."
}
},
{
"@type": "Question",
"name": "Les vaccinations sont-elles importantes ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les vaccinations sont essentielles pour prévenir les infections graves chez ces patients."
}
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{
"@type": "Question",
"name": "Comment gérer les allergies dans ce syndrome ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Éviter les allergènes connus et utiliser des antihistaminiques peut aider à gérer les allergies."
}
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"@type": "Question",
"name": "Les soins dentaires sont-ils importants ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des soins dentaires réguliers sont cruciaux pour prévenir les infections buccales."
}
},
{
"@type": "Question",
"name": "Quel est le traitement principal du syndrome de Job ?",
"position": 16,
"acceptedAnswer": {
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"text": "Le traitement inclut des antibiotiques pour les infections et des antihistaminiques pour les allergies."
}
},
{
"@type": "Question",
"name": "Des immunothérapies sont-elles recommandées ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'immunothérapie peut être envisagée pour gérer les allergies et améliorer la réponse immunitaire."
}
},
{
"@type": "Question",
"name": "Les patients ont-ils besoin de soins réguliers ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un suivi régulier est essentiel pour surveiller les infections et ajuster le traitement."
}
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{
"@type": "Question",
"name": "Peut-on guérir le syndrome de Job ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'existe pas de cure, mais les traitements peuvent aider à gérer les symptômes et les infections."
}
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{
"@type": "Question",
"name": "Des traitements préventifs sont-ils disponibles ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des traitements préventifs, comme les vaccins, peuvent aider à réduire les infections."
}
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{
"@type": "Question",
"name": "Quelles complications peuvent survenir ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent des infections graves, des abcès et des problèmes respiratoires chroniques."
}
},
{
"@type": "Question",
"name": "Le syndrome de Job augmente-t-il le risque de cancer ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il existe un risque accru de certains cancers, notamment les lymphomes, chez ces patients."
}
},
{
"@type": "Question",
"name": "Les infections peuvent-elles être mortelles ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des infections graves peuvent être mortelles si elles ne sont pas traitées rapidement."
}
},
{
"@type": "Question",
"name": "Y a-t-il des complications dermatologiques ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des infections cutanées récurrentes et des abcès peuvent survenir fréquemment."
}
},
{
"@type": "Question",
"name": "Les complications respiratoires sont-elles fréquentes ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les patients souffrent souvent de pneumonies et d'autres infections respiratoires."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque du syndrome de Job ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des antécédents familiaux, des mutations génétiques et des infections fréquentes."
}
},
{
"@type": "Question",
"name": "Les enfants sont-ils plus à risque ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le syndrome de Job se manifeste souvent dans l'enfance, avec des infections récurrentes."
}
},
{
"@type": "Question",
"name": "Les personnes immunodéprimées sont-elles plus à risque ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les personnes immunodéprimées peuvent avoir un risque accru de développer ce syndrome."
}
},
{
"@type": "Question",
"name": "Les allergies augmentent-elles le risque ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les antécédents d'allergies peuvent être un facteur de risque pour le syndrome de Job."
}
},
{
"@type": "Question",
"name": "Les infections fréquentes sont-elles un indicateur ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des infections fréquentes peuvent indiquer un risque accru de syndrome de Job."
}
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}
Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 06/04/2025
Contenu vérifié selon les dernières recommandations médicales
2 publications dans cette catégorie
Affiliations :
Department of Social Medicine and Health Management, School of Public Health, Jilin University , Changchun, China.
Publications dans "Syndrome de Job" :
2 publications dans cette catégorie
Affiliations :
School of Business, Hanyang University, Seoul 04763, Korea.
Publications dans "Syndrome de Job" :
2 publications dans cette catégorie
Affiliations :
Department of Business, Law, Economics and Consumer Behaviour "Carlo A. Ricciardi", Università IULM (International University of Languages and Media), 20143 Milan, Italy. margherita.zito@iulm.it.
Publications dans "Syndrome de Job" :
2 publications dans cette catégorie
Affiliations :
Department of Psychology, University of Turin, 10124 Turin, Italy. lara.colombo@unito.it.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Department of Endocrinology, Al Mouwasat University Hospital, Damascus University, Damascus, Syria.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Damascus University, Damascus, Syria.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Department of Dermatology, Venereology and Leprosy, Dr Ram Manohar Lohia Hospital and Post Graduate Institute of Medical Education and Research, New Delhi, India. sinurose@gmail.com.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Department of Dermatology, Venereology and Leprosy, Dr Ram Manohar Lohia Hospital and Post Graduate Institute of Medical Education and Research, New Delhi, India.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Ludwigsburg University of Education, Germany. Electronic address: tobias.tempel@ph-ludwigsburg.de.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Ludwigsburg University of Education, Germany.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Deptt. of Pathology, North DMC Medical College and Hindu Rao Hospital, New Delhi, India.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Deptt. of Pathology, North DMC Medical College and Hindu Rao Hospital, New Delhi, India.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Deptt. of Pathology, North DMC Medical College and Hindu Rao Hospital, New Delhi, India.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Deptt. of Pediatric Surgery, PGIMS Rohtak, Haryana, India.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Occupational Medicine Unit, Department of Public Health, Experimental and Forensic Sciences, University of Pavia, Italy.
Istituti Clinici Scientifici Maugeri IRCCS, Occupational Medicine Unit of Pavia Institute, Italy.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Occupational Medicine Unit, Department of Public Health, Experimental and Forensic Sciences, University of Pavia, Italy.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Istituti Clinici Scientifici Maugeri IRCCS, Molecular Cardiology of Pavia Institute, Italy.
Department of Molecular Medicine, University of Pavia, Italy.
Molecular Cardiology, Centro Nacional de Investigaciones Cardiovasculares (CNIC), Spain.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Occupational Medicine Unit, Department of Public Health, Experimental and Forensic Sciences, University of Pavia, Italy.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Istituti Clinici Scientifici Maugeri IRCCS, Molecular Cardiology of Pavia Institute, Italy.
Department of Molecular Medicine, University of Pavia, Italy.
Publications dans "Syndrome de Job" :
1 publication dans cette catégorie
Affiliations :
Istituti Clinici Scientifici Maugeri IRCCS, Occupational Medicine Unit of Pavia Institute, Italy.
Publications dans "Syndrome de Job" :
Deep brain stimulation of the subthalamic nucleus (STN-DBS) is a promising palliative option for patients with refractory epilepsy. However, crucial questions remain unanswered: Which patients are the...
Adapting actions to changing goals and environments is central to intelligent behavior. There is evidence that the basal ganglia play a crucial role in reinforcing or adapting actions depending on the...
Disruption of subthalamic nucleus dynamics in Parkinson's disease leads to impairments during walking. Here, we aimed to uncover the principles through which the subthalamic nucleus encodes functional...
Subthalamic nucleus (STN) stimulation is an effective treatment for Parkinson's disease and induced local field potential (LFP) changes that have been linked with clinical improvement. STN stimulation...
We aimed to explore if enhanced theta power was also present in STN and if stimulation-induced spectral changes that were previously reported for Parkinson's disease would occur in dystonia....
We recorded LFPs from 7 patients (12 hemispheres) with isolated craniocervical dystonia whose electrodes were placed such that inferior, middle, and superior contacts covered STN, zona incerta, and th...
We did not observe prominent theta power in STN at rest. STN stimulation induced similar spectral changes in dystonia as in Parkinson's disease, such as broadband power suppression, evoked resonant ne...
Our results show that STN stimulation-induced spectral changes are a nondisease-specific response to high-frequency stimulation, which can serve as placement markers for STN. This broadens the scope o...
There is an ongoing debate about differential clinical outcome and associated adverse effects of deep brain stimulation (DBS) in Parkinson's disease (PD) targeting the subthalamic nucleus (STN) or the...
The landscape of neurophysiological symptoms and behavioral biomarkers in basal ganglia signals for movement disorders is expanding. The clinical translation of sensing-based deep brain stimulation (D...
The aims were to systematically investigate the spectral topography, including a wide range of sub-bands in STN local field potentials (LFP) of Parkinson's disease (PD) patients, and to evaluate its p...
STN-LFPs were recorded from 70 PD patients (130 hemispheres) awake and at rest using multicontact DBS electrodes. A comprehensive spatial characterization, including hot spot localization and focality...
The STN shows a heterogeneous topographic distribution of different spectral biomarkers, with the strongest segregation in the inferior-superior axis. Relative to the superiorly localized beta hot spo...
The spatial segregation and properties of spectral biomarkers within the DBS target structure can additionally be informative for the implementation of next-generation sensing-based DBS. © 2023 The Au...
Common cortico-basal ganglia models of motor control suggest a key role for the subthalamic nucleus (STN) in motor inhibition....
Speech is a complex behavior that can be used to study unique contributions of the basal ganglia to motor control in the human brain. Computational models suggest that the basal ganglia encode either ...
Subthalamic nucleus (STN) deep brain stimulation (DBS) has been proven to be an alternative target choice for refractory isolated cervical dystonia (CD). However, assessments of its short and long-ter...
Gait freezing is a common, disabling symptom of Parkinson's disease characterized by sudden motor arrest during walking. Adaptive deep brain stimulation devices that detect freezing and deliver real-t...
We obtained subthalamic nucleus microelectrode recordings from eight Parkinson's disease patients performing a validated virtual reality gait task, requiring responses to on-screen cognitive cues whil...
Signal analysis during 15 trials containing freezing or significant motor output slowing precipitated by dual-tasking demonstrated reduced θ frequency (3-8 Hz) firing compared to 18 unaffected trials....
These preliminary results reveal a potential neurobiological basis for the interplay between cognitive factors and gait disturbances including freezing in Parkinson's disease, informing development of...