questionsmedicales.fr
Acides aminés, peptides et protéines
Protéines
Protéines de transport
Protéines AAA
ATPases associated with diverse cellular activities
ATP-dependent proteases
ATP-dependent proteases : Questions médicales fréquentes
Termes MeSH sélectionnés :
Fuchs' Endothelial Dystrophy
Diagnostic
5
Imagerie médicale
Protéases
Symptômes
5
Troubles neurologiques
Protéases
Maladies dégénératives
Inflammation
Douleurs musculaires
Protéines
Prévention
5
Prévention
Alimentation équilibrée
Exercice physique
Santé musculaire
Contrôles médicaux
Protéases
Traitements
5
Suppléments alimentaires
Protéases
Thérapie génique
Protéases
Médicaments anti-inflammatoires
Inflammation
Physiothérapie
Douleurs musculaires
Complications
5
Complications
Maladies dégénératives
Complications cardiovasculaires
Protéases
Système immunitaire
Infections
Troubles neurologiques
Complications
Facteurs de risque
5
Facteurs de risque
Maladies métaboliques
Maladies auto-immunes
Protéases
Stress chronique
Protéases
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"@type": "Question",
"name": "Comment diagnostiquer une dysfonction des protéases ATP-dépendantes ?",
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"text": "Des tests enzymatiques et des analyses protéomiques peuvent être utilisés."
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"@type": "Question",
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"name": "Les biopsies sont-elles nécessaires pour le diagnostic ?",
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"name": "Quels symptômes peuvent indiquer un problème avec ces enzymes ?",
"position": 4,
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"@type": "Question",
"name": "Peut-on utiliser l'imagerie pour diagnostiquer des troubles liés aux protéases ?",
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"@type": "Question",
"name": "Quels sont les symptômes d'une déficience en protéases ATP-dépendantes ?",
"position": 6,
"acceptedAnswer": {
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"text": "Fatigue, troubles digestifs, et accumulation de protéines mal repliées peuvent se manifester."
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"@type": "Question",
"name": "Les troubles neurologiques sont-ils liés à ces protéases ?",
"position": 7,
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"name": "Comment la dégradation des protéines affecte-t-elle la santé ?",
"position": 8,
"acceptedAnswer": {
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"text": "Une dégradation inappropriée peut mener à des maladies dégénératives et à l'inflammation."
}
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{
"@type": "Question",
"name": "Y a-t-il des signes cutanés associés à ces troubles ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des éruptions cutanées et des problèmes de cicatrisation peuvent être observés."
}
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{
"@type": "Question",
"name": "Les douleurs musculaires peuvent-elles être un symptôme ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des douleurs musculaires peuvent survenir en raison d'une dégradation protéique anormale."
}
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{
"@type": "Question",
"name": "Comment prévenir les troubles liés aux protéases ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Une alimentation équilibrée et un mode de vie sain peuvent aider à maintenir leur fonction."
}
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"@type": "Question",
"name": "L'exercice physique joue-t-il un rôle préventif ?",
"position": 12,
"acceptedAnswer": {
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}
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"@type": "Question",
"name": "Les contrôles médicaux réguliers sont-ils importants ?",
"position": 13,
"acceptedAnswer": {
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"text": "Oui, des bilans réguliers peuvent détecter précocement des anomalies protéolytiques."
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{
"@type": "Question",
"name": "Y a-t-il des vaccins pour prévenir ces troubles ?",
"position": 14,
"acceptedAnswer": {
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"@type": "Question",
"name": "Le stress peut-il affecter la fonction des protéases ?",
"position": 15,
"acceptedAnswer": {
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}
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{
"@type": "Question",
"name": "Quels traitements existent pour les troubles liés aux protéases ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des thérapies enzymatiques et des médicaments ciblant les voies protéolytiques sont utilisés."
}
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{
"@type": "Question",
"name": "Les suppléments alimentaires peuvent-ils aider ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
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{
"@type": "Question",
"name": "La thérapie génique est-elle une option ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "La thérapie génique est explorée pour corriger des déficiences enzymatiques spécifiques."
}
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{
"@type": "Question",
"name": "Les médicaments anti-inflammatoires sont-ils utiles ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, ils peuvent réduire l'inflammation causée par une dégradation protéique anormale."
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"@type": "Question",
"name": "Comment la physiothérapie peut-elle aider ?",
"position": 20,
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"@type": "Answer",
"text": "La physiothérapie peut améliorer la fonction musculaire et réduire la douleur associée."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir avec des troubles protéolytiques ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des maladies dégénératives, des troubles métaboliques et des infections peuvent survenir."
}
},
{
"@type": "Question",
"name": "Les complications cardiovasculaires sont-elles possibles ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des déséquilibres protéolytiques peuvent contribuer à des maladies cardiovasculaires."
}
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{
"@type": "Question",
"name": "Comment les troubles protéolytiques affectent-ils le système immunitaire ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Ils peuvent affaiblir le système immunitaire, rendant l'organisme plus vulnérable aux infections."
}
},
{
"@type": "Question",
"name": "Y a-t-il un risque accru de cancer ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des anomalies dans la dégradation des protéines peuvent être liées à certains cancers."
}
},
{
"@type": "Question",
"name": "Les troubles neurologiques peuvent-ils s'aggraver ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des troubles protéolytiques non traités peuvent aggraver les symptômes neurologiques."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque pour les troubles protéolytiques ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'âge avancé, des antécédents familiaux et des maladies métaboliques augmentent le risque."
}
},
{
"@type": "Question",
"name": "Le mode de vie influence-t-il ces risques ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un mode de vie sédentaire et une mauvaise alimentation augmentent les risques."
}
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{
"@type": "Question",
"name": "Les maladies auto-immunes sont-elles un facteur de risque ?",
"position": 28,
"acceptedAnswer": {
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"text": "Oui, elles peuvent perturber la fonction des protéases et entraîner des complications."
}
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"@type": "Question",
"name": "Le stress chronique est-il un facteur de risque ?",
"position": 29,
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"@type": "Question",
"name": "L'exposition à des toxines peut-elle augmenter le risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines toxines peuvent altérer la fonction des protéases et causer des dommages cellulaires."
}
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]
}
]
}
Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 17/02/2025
Contenu vérifié selon les dernières recommandations médicales
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, Case Western Reserve University, Cleveland, Ohio, 44106, USA.
Publications dans "ATP-dependent proteases" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry and Physics, Saint Mary's College, Notre Dame, Indiana, 46556, USA.
Publications dans "ATP-dependent proteases" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, Cleveland State University, Cleveland, Ohio, 44115, USA.
Lawrence J. Ellison Institute for Transformative Medicine of USC, University of Southern California, Beverly Hills, CA, 90211, USA.
Publications dans "ATP-dependent proteases" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, Cleveland State University, Cleveland, Ohio, 44115, USA.
Publications dans "ATP-dependent proteases" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, Case Western Reserve University, Cleveland, Ohio, 44106, USA.
Publications dans "ATP-dependent proteases" :
2 publications dans cette catégorie
Affiliations :
Institute of Physics, Chinese Academy of Sciences, Beijing 100190, People's Republic of China.
Publications dans "ATP-dependent proteases" :
2 publications dans cette catégorie
Affiliations :
Department of Biochemistry, North-Eastern Hill University, Shillong, 793022, India.
Publications dans "ATP-dependent proteases" :
2 publications dans cette catégorie
Affiliations :
Program in Molecular Medicine, University of Massachusetts Chan Medical School, Worcester, MA, 01605, USA.
Medical Scientist Training Program, University of Massachusetts Chan Medical School, Worcester, MA, 01605, USA.
Publications dans "ATP-dependent proteases" :
2 publications dans cette catégorie
Affiliations :
Program in Molecular Medicine, University of Massachusetts Chan Medical School, Worcester, MA, 01605, USA. Craig.Peterson@umassmed.edu.
Publications dans "ATP-dependent proteases" :
1 publication dans cette catégorie
Affiliations :
Department of Agricultural Biotechnology, Center for Food Safety and Toxicology, Center for Food and Bioconvergence, and Research Institute for Agriculture and Life Sciences, CALS, Seoul National University, Seoul 08826, Korea.
Publications dans "ATP-dependent proteases" :
1 publication dans cette catégorie
Affiliations :
Department of Agricultural Biotechnology, Center for Food Safety and Toxicology, Center for Food and Bioconvergence, and Research Institute for Agriculture and Life Sciences, CALS, Seoul National University, Seoul 08826, Korea.
Publications dans "ATP-dependent proteases" :
1 publication dans cette catégorie
Affiliations :
Department of Beauty Care, College of Medical Science, Daegu Haany University, Gyeongsan 38610, Korea.
Publications dans "ATP-dependent proteases" :
1 publication dans cette catégorie
Affiliations :
Department of Agricultural Biotechnology, Center for Food Safety and Toxicology, Center for Food and Bioconvergence, and Research Institute for Agriculture and Life Sciences, CALS, Seoul National University, Seoul 08826, Korea.
Publications dans "ATP-dependent proteases" :
1 publication dans cette catégorie
Affiliations :
Laboratoire de Chimie Bactérienne, UMR 7283, IMM, CNRS, Aix-Marseille Université, Marseille, France.
Publications dans "ATP-dependent proteases" :
1 publication dans cette catégorie
Affiliations :
Plateforme Protéomique de l'IMM, Marseille Protéomique (MaP), CNRS FR 3479, Aix-Marseille Université, Marseille, France.
Publications dans "ATP-dependent proteases" :
1 publication dans cette catégorie
Affiliations :
Laboratoire de Chimie Bactérienne, UMR 7283, IMM, CNRS, Aix-Marseille Université, Marseille, France.
Publications dans "ATP-dependent proteases" :
1 publication dans cette catégorie
Affiliations :
Laboratoire de Chimie Bactérienne, UMR 7283, IMM, CNRS, Aix-Marseille Université, Marseille, France.
Publications dans "ATP-dependent proteases" :
1 publication dans cette catégorie
Affiliations :
Laboratoire de Chimie Bactérienne, UMR 7283, IMM, CNRS, Aix-Marseille Université, Marseille, France. Electronic address: fpompeo@imm.cnrs.fr.
Publications dans "ATP-dependent proteases" :
1 publication dans cette catégorie
Affiliations :
Department of Chemistry, Michigan State University, East Lansing, Michigan, 48824.
Publications dans "ATP-dependent proteases" :
1 publication dans cette catégorie
Affiliations :
Department of Chemistry, Michigan State University, East Lansing, Michigan, 48824.
Publications dans "ATP-dependent proteases" :
Traditionally, corneal endothelium is considered post-mitotic, which means that spontaneous regeneration after loss of endothelial cells (e.g., in the context of Fuchs endothelial corneal dystrophy) i...
To characterise the phenotype and genotype of concurrent keratoconus and Fuchs endothelial corneal dystrophy (KC + FECD)....
We recruited 20 patients with concurrent KC + FECD for a retrospective observational case series from the United Kingdom and the Czech Republic. We compared eight parameters of corneal shape (Pentacam...
The median age at diagnosis of patients with KC + FECD was 54 (interquartile range 46 to 66) years, with no evidence of KC progression (median follow-up 84 months, range 12 to 120 months). The mean (s...
The KC + FECD phenotype is consistent with KC but with superimposed stromal swelling from endothelial disease. The proportion of cases with a TCF4 expansion is similar in concurrent KC + FECD and age-...
a review of miRNA expression connected to epithelial mesenchymal transition studies in Fuchs' endothelial corneal dystrophy (FECD)....
literature search strategy-PubMed central database, using "miRNA" or "microRNA" and "epithelial mesenchymal transition" or "EMT" and "Fuchs' endothelial corneal dystrophy" or "FECD" as keywords. Exper...
The publications regarding the miRNA profiles of epithelial mesenchymal transition in Fuchs' endothelial corneal dystrophy are scarce but provide some valuable information about the potential biomarke...
Fuchs endothelial corneal dystrophy (FECD) is the leading indication for corneal transplantation worldwide. Our aim was to investigate the role of transient receptor potential vanilloid subtype 1 (TRP...
Patients with advanced Fuchs endothelial corneal dystrophy frequently report poor vision in the morning, which improves as the day progresses. This study quantified the amount of variation in near and...
This was a prospective cohort study. Best-corrected distance visual acuity and near visual acuity were tested in participants with clinically advanced Fuchs dystrophy and in controls with healthy corn...
In Fuchs dystrophy, the mean distance visual acuity was worse by -3 letters (95% confidence interval, -4 to -1) directly after eye opening in the morning compared with late afternoon. No such differen...
Distance and near visual acuity and refraction changes over the course of the day in patients with advanced Fuchs dystrophy. Although small changes in refraction may not usually require a second set o...
The aim of this study was to assess risk for demographic variables and other health conditions that are associated with Fuchs endothelial corneal dystrophy (FECD)....
We developed a FECD case-control algorithm based on structured electronic health record data and confirmed accuracy by individual review of charts at 3 Veterans Affairs (VA) Medical Centers. This algo...
Being a FECD case was associated with female sex, European genetic ancestry, and a greater number of comorbidities. Of 1417 diagnostic phecodes evaluated, 213 had a significant association with FECD, ...
Female sex, European ancestry, and multimorbidity increased FECD risk. Endocrine/metabolic clinic encounter codes and altered patterns of laboratory values support DM increasing FECD risk. Our results...
To detect environmental factors, which may be possible risk factors in the disease course of Fuchs' endothelial corneal dystrophy (FECD). Evaluation of patients with FECD registered in the FECD geneti...
To identify factors associated with receipt of endothelial keratoplasty (EK) and penetrating keratoplasty (PK) in patients with Fuchs' endothelial corneal dystrophy (FECD)....
Retrospective cohort study....
Medicare beneficiaries 65 years of age or older with a FECD diagnosis between 2011 and 2019....
The 100% Medicare fee-for-service administrative claims database was queried for treatment-naïve FECD patients. A multivariate logistic regression model including age, race and ethnicity, sex, geograp...
Factors associated with receipt of an EK or PK, plus rate of EK after cataract or complex or other anterior segment surgery....
Of 719 066 beneficiaries identified, 31 372 (4.4%) received an EK and 2426 (0.3%) received a PK. In a multivariate analysis, female sex decreased likelihood of both EK and PK (adjusted odds ratio 0.83...
In a multivariate analysis, women beneficiaries are less likely to receive EK or PK for FECD compared with men, whereas non-White beneficiaries are less likely to receive EK and more likely to receive...
This study aims to evaluate the applicability of the high-resolution WaveFront Phase Imaging Sensor (WFPI) in eyes with Fuchs' Endothelial Corneal Dystrophy (FECD) through qualitative and quantitative...
There are no defined diagnostic criteria and severity classification for Fuchs endothelial corneal dystrophy (FECD), which are required for objective standardized assessments. Therefore, we performed ...
We searched the Ovid MEDLINE and Web of Science databases for studies published until January 13, 2021. We excluded review articles, conference abstracts, editorials, case reports with <5 patients, an...
Among 468 articles identified, we excluded 173 and 165 articles in the first and second screenings, respectively. Among the 130 included articles, 61 (47%) and 99 (76%) mentioned the diagnostic criter...
FECD is globally diagnosed by the corneal guttae using slitlamp examination, and its severity is predominantly determined by the original or modified Krachmer grading scale. Objective severity grading...