[Successful treatment of acquired hemophilia A with recombinant porcine factor VIII].
Erfolgreiche Behandlung einer erworbenen Hemmkörperhämophilie A mit rekombinantem porcinem Faktor VIII.
Acquired hemophilia A
Recombinant activated factor VII
Recombinant porcine factor VIII
Journal
Medizinische Klinik, Intensivmedizin und Notfallmedizin
ISSN: 2193-6226
Titre abrégé: Med Klin Intensivmed Notfmed
Pays: Germany
ID NLM: 101575086
Informations de publication
Date de publication:
Nov 2019
Nov 2019
Historique:
received:
18
02
2018
accepted:
01
04
2018
revised:
23
03
2018
pubmed:
19
5
2018
medline:
20
11
2019
entrez:
19
5
2018
Statut:
ppublish
Résumé
Acquired hemophilia A is a rare, potentially life-threatening disease resulting from autoantibodies against coagulation factor VIII. We report the case of a patient with acquired hemophilia A and severe bleeding after incision of a peritonsillar abscess. Treatment with high dose factor VIII and recombinant activated factor VII failed to control bleeding. However, a single infusion of recombinant porcine factor VIII stopped bleeding efficiently and resulted in measurable factor VIII levels.
Identifiants
pubmed: 29774375
doi: 10.1007/s00063-018-0444-8
pii: 10.1007/s00063-018-0444-8
doi:
Substances chimiques
Autoantibodies
0
Factor VIII
9001-27-8
Types de publication
Case Reports
Journal Article
Langues
ger
Sous-ensembles de citation
IM
Pagination
746-748Références
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pubmed: 27480782
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pubmed: 23373521
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pubmed: 25623166
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pubmed: 27511890
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pubmed: 19336751