Expansion of the Human Phenotype Ontology (HPO) knowledge base and resources.


Journal

Nucleic acids research
ISSN: 1362-4962
Titre abrégé: Nucleic Acids Res
Pays: England
ID NLM: 0411011

Informations de publication

Date de publication:
08 01 2019
Historique:
received: 17 09 2018
accepted: 24 10 2018
pubmed: 27 11 2018
medline: 19 5 2020
entrez: 27 11 2018
Statut: ppublish

Résumé

The Human Phenotype Ontology (HPO)-a standardized vocabulary of phenotypic abnormalities associated with 7000+ diseases-is used by thousands of researchers, clinicians, informaticians and electronic health record systems around the world. Its detailed descriptions of clinical abnormalities and computable disease definitions have made HPO the de facto standard for deep phenotyping in the field of rare disease. The HPO's interoperability with other ontologies has enabled it to be used to improve diagnostic accuracy by incorporating model organism data. It also plays a key role in the popular Exomiser tool, which identifies potential disease-causing variants from whole-exome or whole-genome sequencing data. Since the HPO was first introduced in 2008, its users have become both more numerous and more diverse. To meet these emerging needs, the project has added new content, language translations, mappings and computational tooling, as well as integrations with external community data. The HPO continues to collaborate with clinical adopters to improve specific areas of the ontology and extend standardized disease descriptions. The newly redesigned HPO website (www.human-phenotype-ontology.org) simplifies browsing terms and exploring clinical features, diseases, and human genes.

Identifiants

pubmed: 30476213
pii: 5198478
doi: 10.1093/nar/gky1105
pmc: PMC6324074
doi:

Types de publication

Journal Article Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

D1018-D1027

Subventions

Organisme : NHGRI NIH HHS
ID : U01 HG009453
Pays : United States
Organisme : NHGRI NIH HHS
ID : U41 HG000330
Pays : United States
Organisme : NIH HHS
ID : R24 OD011883
Pays : United States
Organisme : NHGRI NIH HHS
ID : U01 HG010218
Pays : United States
Organisme : British Heart Foundation
ID : RG/13/5/30112
Pays : United Kingdom
Organisme : NIAID NIH HHS
ID : P01 AI061093
Pays : United States

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Auteurs

Sebastian Köhler (S)

Charité Centrum für Therapieforschung, Charité-Universitätsmedizin Berlin Corporate Member of Freie Universität Berlin, Humboldt-Universität zu Berlin, and Berlin Institute of Health, Berlin 10117, Germany.
Einstein Center Digital Future, Berlin 10117, Germany.
Monarch Initiative, monarchinitiative.org.

Leigh Carmody (L)

Monarch Initiative, monarchinitiative.org.
The Jackson Laboratory for Genomic Medicine, Farmington, CT 06032, USA.

Nicole Vasilevsky (N)

Monarch Initiative, monarchinitiative.org.
Oregon Health & Science University, Portland, OR 97217, USA.

Julius O B Jacobsen (JOB)

Monarch Initiative, monarchinitiative.org.
Genomics England, Queen Mary University of London, Dawson Hall, Charterhouse Square, London EC1M 6BQ, UK.

Daniel Danis (D)

Monarch Initiative, monarchinitiative.org.
The Jackson Laboratory for Genomic Medicine, Farmington, CT 06032, USA.

Jean-Philippe Gourdine (JP)

Monarch Initiative, monarchinitiative.org.
Oregon Health & Science University, Portland, OR 97217, USA.

Michael Gargano (M)

Monarch Initiative, monarchinitiative.org.
The Jackson Laboratory for Genomic Medicine, Farmington, CT 06032, USA.

Nomi L Harris (NL)

Monarch Initiative, monarchinitiative.org.
Environmental Genomics and Systems Biology, Lawrence Berkeley National Laboratory, Berkeley, CA 94720, USA.

Nicolas Matentzoglu (N)

Monarch Initiative, monarchinitiative.org.
European Bioinformatics Institute (EMBL-EBI), Wellcome Trust Genome Campus, Cambridge, UK.

Julie A McMurry (JA)

Monarch Initiative, monarchinitiative.org.
Linus Pauling institute, Oregon State University, Corvallis, OR, USA.

David Osumi-Sutherland (D)

Monarch Initiative, monarchinitiative.org.
European Bioinformatics Institute (EMBL-EBI), Wellcome Trust Genome Campus, Cambridge, UK.

Valentina Cipriani (V)

Monarch Initiative, monarchinitiative.org.
William Harvey Research Institute, Queen Mary University College of London.
UCL Genetics Institute, University College of London.
UCL Institute of Ophthalmology, University College of London.

James P Balhoff (JP)

Monarch Initiative, monarchinitiative.org.
Renaissance Computing Institute, University of North Carolina at Chapel Hill.

Tom Conlin (T)

Monarch Initiative, monarchinitiative.org.
Linus Pauling institute, Oregon State University, Corvallis, OR, USA.

Hannah Blau (H)

Monarch Initiative, monarchinitiative.org.
The Jackson Laboratory for Genomic Medicine, Farmington, CT 06032, USA.

Gareth Baynam (G)

Western Australian Register of Developmental Anomalies and Genetic Services of Western Australia, Department of Health, Government of Western Australia, WA, Australia.
School of Paediatrics and Telethon Kids Institute, University of Western Australia, Perth, WA, Australia.
Institute for Immunology and Infectious Diseases, Murdoch University, Perth, WA, Australia.
Spatial Sciences, Department of Science and Engineering, Curtin University, Perth, WA, Australia.
The Office of Population Health Genomics, Department of Health, Government of Western Australia, Perth, WA, Australia.

Richard Palmer (R)

Spatial Sciences, Department of Science and Engineering, Curtin University, Perth, WA, Australia.

Dylan Gratian (D)

Western Australian Register of Developmental Anomalies and Genetic Services of Western Australia, Department of Health, Government of Western Australia, WA, Australia.

Hugh Dawkins (H)

The Office of Population Health Genomics, Department of Health, Government of Western Australia, Perth, WA, Australia.

Michael Segal (M)

SimulConsult, Chestnut Hill, MA, USA.

Anna C Jansen (AC)

Neurogenetics Research Group, Vrije Universiteit Brussel, Brussels, Belgium.
Pediatric Neurology Unit, Department of Pediatrics, UZ Brussel, Brussels, Belgium.

Ahmed Muaz (A)

Monarch Initiative, monarchinitiative.org.
Garvan Institute of Medical Research, Darlinghurst, Sydney, NSW 2010, Australia.

Willie H Chang (WH)

Centre for Computational Medicine, Hospital for Sick Children and Department of Computer Science, University of Toronto, Toronto, Canada.

Jenna Bergerson (J)

National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, USA.

Stanley J F Laulederkind (SJF)

Rat Genome Database, Department of Biomedical Engineering, Medical College of Wisconsin & Marquette University, 8701 Watertown Plank Road Milwaukee, WI 53226, USA.

Zafer Yüksel (Z)

Bioscientia GmbH, Ingelheim, Germany.

Sergi Beltran (S)

CNAG-CRG, Centre for Genomic Regulation (CRG), The Barcelona Institute of Science and Technology, Baldiri Reixac 4, Barcelona 08028, Spain.
Universitat Pompeu Fabra (UPF), Barcelona, Spain.

Alexandra F Freeman (AF)

National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, USA.

Panagiotis I Sergouniotis (PI)

University of Manchester & Manchester Royal Eye Hospital, Manchester, UK.

Daniel Durkin (D)

The Jackson Laboratory for Genomic Medicine, Farmington, CT 06032, USA.

Andrea L Storm (AL)

ICF, Rockville, MD, USA.
National Center for Advancing Translational Sciences, Office of Rare Diseases Research, National Institutes of Health, Bethesda, MD, USA.

Marc Hanauer (M)

INSERM, US14-Orphanet, Plateforme Maladies Rares, 75014 Paris, France.

Michael Brudno (M)

Centre for Computational Medicine, Hospital for Sick Children and Department of Computer Science, University of Toronto, Toronto, Canada.

Susan M Bello (SM)

The Jackson Laboratory, Bar Harbor, ME, USA.

Murat Sincan (M)

Sanford Imagenetics, Sanford Health, Sioux Falls, SD, USA.

Kayli Rageth (K)

Sanford Imagenetics, Sanford Health, Sioux Falls, SD, USA.

Matthew T Wheeler (MT)

Center for Undiagnosed Diseases, Stanford University School of Medicine, Stanford, CA, USA.

Renske Oegema (R)

Department of Genetics, University Medical Center Utrecht, the Netherlands.

Halima Lourghi (H)

INSERM, US14-Orphanet, Plateforme Maladies Rares, 75014 Paris, France.

Maria G Della Rocca (MG)

ICF, Rockville, MD, USA.
National Center for Advancing Translational Sciences, Office of Rare Diseases Research, National Institutes of Health, Bethesda, MD, USA.

Rachel Thompson (R)

Institute of Genetic Medicine, Newcastle University, Newcastle upon Tyne, UK.

Francisco Castellanos (F)

The Jackson Laboratory for Genomic Medicine, Farmington, CT 06032, USA.

James Priest (J)

Department of Pediatrics, Stanford University School of Medicine, Stanford, CA, USA.

Charlotte Cunningham-Rundles (C)

Mount Sinai School of Medicine, New York, NY, USA.

Ayushi Hegde (A)

The Jackson Laboratory for Genomic Medicine, Farmington, CT 06032, USA.

Ruth C Lovering (RC)

Institute of Cardiovascular Science, University College London, UK.

Catherine Hajek (C)

Sanford Imagenetics, Sanford Health, Sioux Falls, SD, USA.

Annie Olry (A)

INSERM, US14-Orphanet, Plateforme Maladies Rares, 75014 Paris, France.

Luigi Notarangelo (L)

National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, USA.

Morgan Similuk (M)

National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, USA.

Xingmin A Zhang (XA)

Monarch Initiative, monarchinitiative.org.
The Jackson Laboratory for Genomic Medicine, Farmington, CT 06032, USA.

David Gómez-Andrés (D)

Child Neurology Unit. Hospital Universitari Vall d'Hebron, Vall d'Hebron Research Institute (VHIR), Barcelona, Spain.

Hanns Lochmüller (H)

CNAG-CRG, Centre for Genomic Regulation (CRG), The Barcelona Institute of Science and Technology, Baldiri Reixac 4, Barcelona 08028, Spain.
Department of Neuropediatrics and Muscle Disorders, Medical Center-University of Freiburg, Faculty of Medicine, Freiburg, Germany.
Children's Hospital of Eastern Ontario Research Institute, University of Ottawa, Ottawa, Canada.
Division of Neurology, Department of Medicine, The Ottawa Hospital, Ottawa, Canada.

Hélène Dollfus (H)

Centre for Rare Eye Diseases CARGO, SENSGENE FSMR Network, Strasbourg University Hospital, Strasbourg, France.

Sergio Rosenzweig (S)

Immunology Service, Department of Laboratory Medicine, NIH Clinical Center, Bethesda, MD, USA.

Shruti Marwaha (S)

Center for Undiagnosed Diseases, Stanford University School of Medicine, Stanford, CA, USA.

Ana Rath (A)

INSERM, US14-Orphanet, Plateforme Maladies Rares, 75014 Paris, France.

Kathleen Sullivan (K)

Department of Pediatrics, Division of Allergy Immunology, The Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, 3615 Civic Center Boulevard, Philadelphia, PA 19104, USA.

Cynthia Smith (C)

The Jackson Laboratory, Bar Harbor, ME, USA.

Joshua D Milner (JD)

National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, USA.

Dorothée Leroux (D)

Centre for Rare Eye Diseases CARGO, SENSGENE FSMR Network, Strasbourg University Hospital, Strasbourg, France.

Cornelius F Boerkoel (CF)

Sanford Imagenetics, Sanford Health, Sioux Falls, SD, USA.

Amy Klion (A)

National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, USA.

Melody C Carter (MC)

National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, USA.

Tudor Groza (T)

Monarch Initiative, monarchinitiative.org.
Garvan Institute of Medical Research, Darlinghurst, Sydney, NSW 2010, Australia.

Damian Smedley (D)

Monarch Initiative, monarchinitiative.org.
Genomics England, Queen Mary University of London, Dawson Hall, Charterhouse Square, London EC1M 6BQ, UK.

Melissa A Haendel (MA)

Monarch Initiative, monarchinitiative.org.
Oregon Health & Science University, Portland, OR 97217, USA.
Linus Pauling institute, Oregon State University, Corvallis, OR, USA.

Chris Mungall (C)

Monarch Initiative, monarchinitiative.org.
Environmental Genomics and Systems Biology, Lawrence Berkeley National Laboratory, Berkeley, CA 94720, USA.

Peter N Robinson (PN)

Monarch Initiative, monarchinitiative.org.
The Jackson Laboratory for Genomic Medicine, Farmington, CT 06032, USA.
Institute for Systems Genomics, University of Connecticut, Farmington, CT, USA.

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Classifications MeSH