Anti-signal Recognition Particle Antibody-positive Necrotizing Myopathy with Secondary Cardiomyopathy: The First Myocardial Biopsy- and Multimodal Imaging-proven Case.
Aged
Autoantibodies
/ blood
Biopsy
Cardiomyopathies
/ diagnostic imaging
Contrast Media
Echocardiography
Female
Gadolinium
Humans
Immunoglobulins, Intravenous
/ therapeutic use
Immunosuppressive Agents
/ therapeutic use
Magnetic Resonance Imaging
Multimodal Imaging
Muscle Weakness
/ pathology
Muscle, Skeletal
/ pathology
Muscular Diseases
/ complications
Positron Emission Tomography Computed Tomography
Signal Recognition Particle
/ immunology
Tacrolimus
/ therapeutic use
anti-signal recognition particle (SRP) antibody
cardiomyopathy
myocardial biopsy
necrotizing myopathy
positron-emission tomography (PET)
Journal
Internal medicine (Tokyo, Japan)
ISSN: 1349-7235
Titre abrégé: Intern Med
Pays: Japan
ID NLM: 9204241
Informations de publication
Date de publication:
01 Nov 2019
01 Nov 2019
Historique:
pubmed:
12
7
2019
medline:
12
2
2020
entrez:
12
7
2019
Statut:
ppublish
Résumé
A 69-year-old Japanese woman was admitted to our hospital with progressive muscle weakness and dysphagia. She was taking pitavastatin for dyslipidemia. Her serum creatine kinase was 6,300 U/L. Pitavastatin was stopped, but her symptoms deteriorated, and cardiac congestion appeared. A muscle biopsy showed necrotizing myopathy (NM), and anti-signal recognition particle (SRP) antibody was positive.
Identifiants
pubmed: 31292376
doi: 10.2169/internalmedicine.2564-18
pmc: PMC6875452
doi:
Substances chimiques
Autoantibodies
0
Contrast Media
0
Immunoglobulins, Intravenous
0
Immunosuppressive Agents
0
Signal Recognition Particle
0
Gadolinium
AU0V1LM3JT
Tacrolimus
WM0HAQ4WNM
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
3189-3194Références
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