Aged, 80 and over
Airway Obstruction
/ drug therapy
Antifibrinolytic Agents
/ therapeutic use
Cyclophosphamide
/ therapeutic use
Glucocorticoids
/ therapeutic use
Hematoma
/ drug therapy
Hemophilia A
/ complications
Humans
Male
Partial Thromboplastin Time
Prednisone
/ therapeutic use
Tranexamic Acid
/ therapeutic use
adult intensive care
ear, nose and throat/otolaryngology
haematology (incl blood transfusion)
Journal
BMJ case reports
ISSN: 1757-790X
Titre abrégé: BMJ Case Rep
Pays: England
ID NLM: 101526291
Informations de publication
Date de publication:
04 May 2020
04 May 2020
Historique:
entrez:
7
5
2020
pubmed:
7
5
2020
medline:
20
1
2021
Statut:
epublish
Résumé
Acquired haemophilia A is a rare but important diagnosis, carrying a mortality rate of 22%. Life-threatening sequalae of this diagnosis includes airway compromise, which can rapidly lead to demise of the patient if left untreated. Our case examines an 80-year-old man presenting with a supraglottic haematoma resulting from acquired haemophilia A causing airway compromise and necessitating definitive airway control. A review of current understanding and management of the disease is also ddiscussed.
Identifiants
pubmed: 32371415
pii: 13/5/e233345
doi: 10.1136/bcr-2019-233345
pmc: PMC7222884
pii:
doi:
Substances chimiques
Antifibrinolytic Agents
0
Glucocorticoids
0
Tranexamic Acid
6T84R30KC1
Cyclophosphamide
8N3DW7272P
Prednisone
VB0R961HZT
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Informations de copyright
© BMJ Publishing Group Limited 2020. No commercial re-use. See rights and permissions. Published by BMJ.
Déclaration de conflit d'intérêts
Competing interests: None declared.
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