A case of complete atrioventricular block in secondary hemophagocytic syndrome/hemophagocytic lymphohistiocytosis recovered by plasma exchange and cytokine absorbing therapy with AN69ST continuous hemodiafiltration.
Adult
Anti-Bacterial Agents
/ therapeutic use
Atrioventricular Block
/ etiology
Cytokines
/ isolation & purification
Glucocorticoids
/ administration & dosage
Hemodiafiltration
/ methods
Humans
Lupus Erythematosus, Systemic
/ complications
Lymphohistiocytosis, Hemophagocytic
/ etiology
Male
Plasma Exchange
/ methods
Sorption Detoxification
/ methods
Treatment Outcome
Young Adult
AN69ST
Staphylococcus aureus bacteremia
Systemic lupus erythematosus
complete atrioventricular block
plasma exchange
Journal
Immunological medicine
ISSN: 2578-5826
Titre abrégé: Immunol Med
Pays: England
ID NLM: 101736847
Informations de publication
Date de publication:
Dec 2020
Dec 2020
Historique:
pubmed:
7
5
2020
medline:
24
11
2020
entrez:
7
5
2020
Statut:
ppublish
Résumé
We report a case of incipient systemic lupus erythematosus (SLE) that rapidly progressed to complete atrioventricular block (cAVB). A 20-year-old man was admitted with facial erythema, painless oral aphtha, polyarthritis, and myalgia of each extremity. On admission, he developed first-degree atrioventricular block, pericarditis, pleuritis, renal failure, hemophagocytic lymphohistiocytosis, neurophychiatric SLE (left cerebellar infarction), and
Identifiants
pubmed: 32374660
doi: 10.1080/25785826.2020.1761145
doi:
Substances chimiques
Anti-Bacterial Agents
0
Cytokines
0
Glucocorticoids
0
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM