Complete Heart Block in Systemic Sclerosis with Characterization on Cardiac MRI.
Adult
Atrioventricular Block
/ diagnostic imaging
Cardiac Pacing, Artificial
Cardiomyopathies
/ diagnostic imaging
Disease Progression
Fatal Outcome
Glucocorticoids
/ therapeutic use
Humans
Immunosuppressive Agents
/ therapeutic use
Magnetic Resonance Imaging
Male
Predictive Value of Tests
Scleroderma, Systemic
/ complications
Treatment Outcome
complete heart block
infiltrative disease
systemic sclerosis
Journal
Methodist DeBakey cardiovascular journal
ISSN: 1947-6108
Titre abrégé: Methodist Debakey Cardiovasc J
Pays: United States
ID NLM: 101508600
Informations de publication
Date de publication:
Historique:
entrez:
17
7
2020
pubmed:
17
7
2020
medline:
9
9
2020
Statut:
ppublish
Résumé
Cardiac involvement of infiltrative disease, such as systemic sclerosis, carries significant morbidity and mortality. All parts of the heart may be affected, although the conduction system is less commonly involved. We report a rare case of systemic sclerosis causing third-degree atrioventricular block and the first known reported case to use cardiac magnetic resonance imaging (CMR) as a diagnostic and prognostic instrument. It is not known whether using cardiac CMR in systemic sclerosis with cardiac involvement could lead to earlier intervention with escalation of medical therapy or earlier referral for transplant evaluation.
Identifiants
pubmed: 32670478
doi: 10.14797/mdcj-16-2-162
pmc: PMC7350807
doi:
Substances chimiques
Glucocorticoids
0
Immunosuppressive Agents
0
Types de publication
Case Reports
Langues
eng
Sous-ensembles de citation
IM
Pagination
162-166Informations de copyright
© 2020 Houston Methodist Hospital Houston, Texas.
Déclaration de conflit d'intérêts
Conflict of Interest Disclosure: The authors have completed and submitted the Methodist DeBakey Cardiovascular Journal Conflict of Interest Statement and none were reported.
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