Steroid-Refractory Protein-Losing Enteropathy with Gastrointestinal Bleeding in a Patient with Fontan Circulation.
Administration, Oral
Anemia, Refractory
/ etiology
Cardiac Catheterization
/ methods
Child
Fontan Procedure
/ adverse effects
Gastrointestinal Hemorrhage
/ complications
Glucocorticoids
/ administration & dosage
Humans
Hypoalbuminemia
/ etiology
Hypoplastic Left Heart Syndrome
/ surgery
Male
Prednisolone
/ administration & dosage
Protein-Losing Enteropathies
/ drug therapy
Remission, Spontaneous
Treatment Outcome
Anemia
Hypoalbuminemia
Hypoplastic left heart syndrome
Steroid
Total cavopulmonary connection
Journal
International heart journal
ISSN: 1349-3299
Titre abrégé: Int Heart J
Pays: Japan
ID NLM: 101244240
Informations de publication
Date de publication:
2020
2020
Historique:
entrez:
31
7
2020
pubmed:
31
7
2020
medline:
8
8
2020
Statut:
ppublish
Résumé
Protein-losing enteropathy (PLE) is one of the major complications after a Fontan operation. Some PLE patients suffer from concurrent gastrointestinal bleeding. An effective treatment regimen for such patients has not been established yet. Further, it remains unknown whether PLE and gastrointestinal bleeding coexist independently, or protein losing is associated with gastrointestinal bleeding. We report a 7-year-old steroid-refractory post-Fontan PLE case suggesting the latter pathogenesis together with a literature review.
Substances chimiques
Glucocorticoids
0
Prednisolone
9PHQ9Y1OLM
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM