Genes containing hexanucleotide repeats resembling C9ORF72 and expressed in the central nervous system are frequent in the human genome.


Journal

Neurobiology of aging
ISSN: 1558-1497
Titre abrégé: Neurobiol Aging
Pays: United States
ID NLM: 8100437

Informations de publication

Date de publication:
01 2021
Historique:
received: 04 01 2020
revised: 22 07 2020
accepted: 25 07 2020
pubmed: 28 8 2020
medline: 2 9 2021
entrez: 27 8 2020
Statut: ppublish

Résumé

More than 40 human diseases, mainly diseases affecting the central nervous system, are caused by the expansion of unstable nucleotide repeats. Repeats of sequences like (CAG)

Identifiants

pubmed: 32843153
pii: S0197-4580(20)30244-X
doi: 10.1016/j.neurobiolaging.2020.07.027
pii:
doi:

Substances chimiques

C9orf72 Protein 0
C9orf72 protein, human 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

148.e1-148.e7

Informations de copyright

Copyright © 2020 Elsevier Inc. All rights reserved.

Auteurs

Patrick Vourc'h (P)

UMR 1253, Université de Tours, Inserm, Tours, France; CHRU de Tours, Laboratoire de Biochimie et de Biologie moléculaire, Tours, France. Electronic address: vourch@med.univ-tours.fr.

François Wurmser (F)

UMR 1253, Université de Tours, Inserm, Tours, France.

Céline Brulard (C)

UMR 1253, Université de Tours, Inserm, Tours, France; CHRU de Tours, Laboratoire de Biochimie et de Biologie moléculaire, Tours, France.

Kevin Mouzat (K)

CHRU de Nîmes, Laboratoire de Biochimie, Nîmes, France.

Sandra Kassem (S)

CHRU de Tours, Laboratoire de Biochimie et de Biologie moléculaire, Tours, France.

Audrey Dangoumau (A)

UMR 1253, Université de Tours, Inserm, Tours, France.

Frédéric Laumonnier (F)

UMR 1253, Université de Tours, Inserm, Tours, France.

Hélène Blasco (H)

UMR 1253, Université de Tours, Inserm, Tours, France; CHRU de Tours, Laboratoire de Biochimie et de Biologie moléculaire, Tours, France.

Philippe Corcia (P)

UMR 1253, Université de Tours, Inserm, Tours, France; CHRU de Tours, Service de Neurologie, Tours, France.

Christian R Andres (CR)

UMR 1253, Université de Tours, Inserm, Tours, France; CHRU de Tours, Laboratoire de Biochimie et de Biologie moléculaire, Tours, France.

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Classifications MeSH