Poly(ADP-ribose) promotes toxicity of


Journal

Science translational medicine
ISSN: 1946-6242
Titre abrégé: Sci Transl Med
Pays: United States
ID NLM: 101505086

Informations de publication

Date de publication:
14 09 2022
Historique:
entrez: 14 9 2022
pubmed: 15 9 2022
medline: 17 9 2022
Statut: ppublish

Résumé

Arginine-rich dipeptide repeat proteins (R-DPRs), abnormal translational products of a GGGGCC hexanucleotide repeat expansion in

Identifiants

pubmed: 36103513
doi: 10.1126/scitranslmed.abq3215
pmc: PMC10359073
mid: NIHMS1891926
doi:

Substances chimiques

C9orf72 Protein 0
C9orf72 protein, human 0
DNA-Binding Proteins 0
Dipeptides 0
Poly Adenosine Diphosphate Ribose 26656-46-2
Arginine 94ZLA3W45F

Types de publication

Journal Article Research Support, Non-U.S. Gov't Research Support, U.S. Gov't, Non-P.H.S. Research Support, N.I.H., Extramural

Langues

eng

Sous-ensembles de citation

IM

Pagination

eabq3215

Subventions

Organisme : NINDS NIH HHS
ID : R01 NS085207
Pays : United States
Organisme : NIGMS NIH HHS
ID : R01 GM104135
Pays : United States
Organisme : NINDS NIH HHS
ID : RF1 NS121143
Pays : United States
Organisme : NINDS NIH HHS
ID : R01 NS099320
Pays : United States
Organisme : NIH HHS
ID : P40 OD018537
Pays : United States
Organisme : NINDS NIH HHS
ID : K99 NS123242
Pays : United States
Organisme : NINDS NIH HHS
ID : P01 NS084974
Pays : United States
Organisme : Motor Neurone Disease Association
ID : TALBOT-MUTIHAC/APR15/832-791
Pays : United Kingdom
Organisme : NINDS NIH HHS
ID : P30 NS050274
Pays : United States
Organisme : NINDS NIH HHS
ID : R01 NS094239
Pays : United States
Organisme : NINDS NIH HHS
ID : R37 NS067525
Pays : United States
Organisme : NINDS NIH HHS
ID : R01 NS082563
Pays : United States
Organisme : NINDS NIH HHS
ID : U24 NS078736
Pays : United States
Organisme : NINDS NIH HHS
ID : P01 NS099114
Pays : United States
Organisme : NINDS NIH HHS
ID : R01 NS117461
Pays : United States
Organisme : NINDS NIH HHS
ID : R01 NS121125
Pays : United States

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Auteurs

Junli Gao (J)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.

Quinlan T Mewborne (QT)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.

Amandeep Girdhar (A)

Department of Biochemistry and Molecular Biology, Thomas Jefferson University, Philadelphia, PA 19107, USA.

Udit Sheth (U)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.

Alyssa N Coyne (AN)

Department of Neurology, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.
Brain Science Institute, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.

Ritika Punathil (R)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.

Bong Gu Kang (BG)

Department of Neurology, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.

Morgan Dasovich (M)

Department of Biochemistry and Molecular Biology, Bloomberg School of Public Health, Johns Hopkins University, Baltimore, MD 21205, USA.
Department of Chemistry, Krieger School of Arts and Sciences, Johns Hopkins University, Baltimore, MD 21218, USA.

Austin Veire (A)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.

Mariely DeJesus Hernandez (M)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.

Shuaichen Liu (S)

Department of Biochemistry and Molecular Biology, Bloomberg School of Public Health, Johns Hopkins University, Baltimore, MD 21205, USA.

Zheng Shi (Z)

Department of Chemistry and Chemical Biology, Rutgers University, Piscataway, NJ 08854, USA.

Ruxandra Dafinca (R)

Nuffield Department of Clinical Neurosciences, John Radcliffe Hospital, University of Oxford, Oxford OX3 9DU, UK.

Elise Fouquerel (E)

Department of Biochemistry and Molecular Biology, Thomas Jefferson University, Philadelphia, PA 19107, USA.

Kevin Talbot (K)

Nuffield Department of Clinical Neurosciences, John Radcliffe Hospital, University of Oxford, Oxford OX3 9DU, UK.

Tae-In Kam (TI)

Department of Neurology, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.

Yong-Jie Zhang (YJ)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.

Dennis Dickson (D)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.

Leonard Petrucelli (L)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.
Neuroscience Graduate Program, Mayo Clinic Graduate School of Biomedical Sciences, Jacksonville, FL 32224, USA.

Marka van Blitterswijk (M)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.

Lin Guo (L)

Department of Biochemistry and Molecular Biology, Thomas Jefferson University, Philadelphia, PA 19107, USA.

Ted M Dawson (TM)

Department of Neurology, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.
Neuroregeneration and Stem Cell Programs, Institute for Cell Engineering, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.
Department of Neuroscience, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.

Valina L Dawson (VL)

Department of Neurology, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.
Neuroregeneration and Stem Cell Programs, Institute for Cell Engineering, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.
Department of Neuroscience, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.

Anthony K L Leung (AKL)

Department of Biochemistry and Molecular Biology, Bloomberg School of Public Health, Johns Hopkins University, Baltimore, MD 21205, USA.
McKusick-Nathans Department of Genetic Medicine, Johns Hopkins University School of Medicine, Baltimore, MD 21205, USA.
Department of Oncology, Johns Hopkins University School of Medicine, Baltimore, MD 21205, USA.
Department of Molecular Biology and Genetics, Johns Hopkins University School of Medicine, Baltimore, MD 21205, USA.

Thomas E Lloyd (TE)

Department of Neurology, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.
Department of Neuroscience, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.

Tania F Gendron (TF)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.
Neuroscience Graduate Program, Mayo Clinic Graduate School of Biomedical Sciences, Jacksonville, FL 32224, USA.

Jeffrey D Rothstein (JD)

Department of Neurology, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.
Brain Science Institute, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.
Department of Neuroscience, Johns Hopkins University, School of Medicine, Baltimore, MD 21205, USA.

Ke Zhang (K)

Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.
Neuroscience Graduate Program, Mayo Clinic Graduate School of Biomedical Sciences, Jacksonville, FL 32224, USA.
Institute of Neurological Diseases, Shenzhen Bay Laboratory, Shenzhen, Guangdong, 518132, China.

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Classifications MeSH