Journal

Journal of medical genetics
ISSN: 1468-6244
Titre abrégé: J Med Genet
Pays: England
ID NLM: 2985087R

Informations de publication

Date de publication:
27 Nov 2023
Historique:
received: 25 04 2023
accepted: 18 06 2023
medline: 29 11 2023
pubmed: 5 7 2023
entrez: 4 7 2023
Statut: epublish

Résumé

The We report five new unrelated patients with All patients had attenuated colorectal adenomatous polyposis, with duodenal polyposis in two cases. Both women had breast carcinomas. EMAST phenotype was present at various levels in different samples of the five patients, confirming the This report lends further credence to biallelic

Sections du résumé

BACKGROUND BACKGROUND
The
METHODS METHODS
We report five new unrelated patients with
RESULTS RESULTS
All patients had attenuated colorectal adenomatous polyposis, with duodenal polyposis in two cases. Both women had breast carcinomas. EMAST phenotype was present at various levels in different samples of the five patients, confirming the
CONCLUSION CONCLUSIONS
This report lends further credence to biallelic

Identifiants

pubmed: 37402566
pii: jmg-2023-109341
doi: 10.1136/jmg-2023-109341
doi:

Substances chimiques

MSH3 protein, human 0
MutS Homolog 3 Protein 0

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

1198-1205

Informations de copyright

© Author(s) (or their employer(s)) 2023. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: None declared.

Auteurs

Marie-Charlotte Villy (MC)

Department of Genetics, Université Paris Cité, Institut Curie, Paris, France marie-charlotte.villy@curie.fr.

Julien Masliah-Planchon (J)

Department of Genetics, PSL University, Institut Curie, Paris, France.

Anne Schnitzler (A)

Department of Genetics, PSL University, Institut Curie, Paris, France.

Hélène Delhomelle (H)

Department of Genetics, PSL University, Institut Curie, Paris, France.

Bruno Buecher (B)

Department of Genetics, PSL University, Institut Curie, Paris, France.

Mathilde Filser (M)

Department of Genetics, PSL University, Institut Curie, Paris, France.

Kevin Merchadou (K)

Clinical Bioinformatics Unit, Institut Curie, Paris, France.

Lisa Golmard (L)

Department of Genetics, PSL University, Institut Curie, Paris, France.

Samia Melaabi (S)

Department of Genetics, PSL University, Institut Curie, Paris, France.

Sophie Vacher (S)

Department of Genetics, PSL University, Institut Curie, Paris, France.

Maud Blanluet (M)

Department of Genetics, PSL University, Institut Curie, Paris, France.

Voreak Suybeng (V)

Department of Genetics, PSL University, Institut Curie, Paris, France.

Carole Corsini (C)

Medical Genetics Department, Centre Hospitalier Regional Universitaire de Montpellier, Montpellier, France.

Marion Dhooge (M)

Oncogenetic Unit, Department of Gastroenterology, AP-HP Centre-Université de Paris, Hopital Cochin, Paris, France.

Nadim Hamzaoui (N)

Department of Genetics, AP-HP Centre-Université de Paris, Hospital Cochin, Paris, France.

Solenne Farelly (S)

Oncogenetic Unit, Department of Gastroenterology, AP-HP Centre-Université de Paris, Hopital Cochin, Paris, France.

Amal Ait Omar (A)

Department of Gastroenterology, Hôpital Avicenne, Bobigny, France.

Robert Benamouzig (R)

Department of Gastroenterology, Hôpital Avicenne, Bobigny, France.

Vincent Caumette (V)

Department of Genetics, Hôpitaux Universitaires Henri Mondor, Creteil, France.

Michel Bahuau (M)

Department of Genetics, Hôpitaux Universitaires Henri Mondor, Creteil, France.

Joël Cucherousset (J)

Department of Pathology, GHI Le Raincy-Montfermeil, Montfermeil, France.

Yves Allory (Y)

Department of Pathology, Université Paris-Saclay, Institut Curie, Paris, France.

Dominique Stoppa-Lyonnet (D)

Department of Genetics, Université Paris Cité, Institut Curie, Paris, France.

Ivan Bieche (I)

Department of Genetics, Université Paris Cité, Institut Curie, Paris, France.

Chrystelle Colas (C)

Department of Genetics, PSL University, Institut Curie, Paris, France.

Articles similaires

[Redispensing of expensive oral anticancer medicines: a practical application].

Lisanne N van Merendonk, Kübra Akgöl, Bastiaan Nuijen
1.00
Humans Antineoplastic Agents Administration, Oral Drug Costs Counterfeit Drugs

Smoking Cessation and Incident Cardiovascular Disease.

Jun Hwan Cho, Seung Yong Shin, Hoseob Kim et al.
1.00
Humans Male Smoking Cessation Cardiovascular Diseases Female
Humans United States Aged Cross-Sectional Studies Medicare Part C
1.00
Humans Yoga Low Back Pain Female Male

Classifications MeSH