questionsmedicales.fr
États, signes et symptômes pathologiques
Processus pathologiques
Fibrose
Fibrose : Questions médicales fréquentes
Termes MeSH sélectionnés :
Diagnostic
5
Fibrose pulmonaire
Biopsie
Imagerie médicale
Tests sanguins
Inflammation
Fonction hépatique
Échographie
Fibrose hépatique
Imagerie
Radiologie
Fibrose
Opacités
Pneumonie
Cirrhose
Diagnostic différentiel
Symptômes
5
Fibrose pulmonaire
Toux
Essoufflement
Fibrose hépatique
Douleur abdominale
Symptômes
Fibrose cardiaque
Palpitations
Œdèmes
Perte de poids
Fibrose
Malabsorption
Fibrose systémique
Douleurs articulaires
Raideur cutanée
Prévention
5
Prévention
Tabagisme
Polluants
Fibrose hépatique
Mode de vie sain
Vaccination
Examens réguliers
Détection précoce
Fibrose
Alimentation
Antioxydants
Prévention
Maladies chroniques
Diabète
Hypertension
Traitements
5
Fibrose pulmonaire
Antifibrotiques
Réhabilitation pulmonaire
Transplantation
Chirurgie
Fibrose
Fibrose hépatique
Antiviraux
Médicaments
Physiothérapie
Fibrose
Qualité de vie
Traitements naturels
Antioxydants
Consultation médicale
Complications
5
Complications
Insuffisance respiratoire
Infections pulmonaires
Cirrhose
Fibrose hépatique
Complications
Fibrose cardiaque
Insuffisance cardiaque
Accidents vasculaires cérébraux
Qualité de vie
Fibrose
Limitations
Complications psychologiques
Anxiété
Dépression
Facteurs de risque
5
Facteurs de risque
Tabagisme
Infections
Âge
Fibrose
Facteurs de risque
Maladies auto-immunes
Sclérodermie
Fibrose
Diabète
Fibrose hépatique
Stéatose
Exposition professionnelle
Fibrose
Produits chimiques
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"text": "Le diagnostic repose sur des examens d'imagerie, des tests fonctionnels pulmonaires et parfois une biopsie."
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"@type": "Question",
"name": "Quels tests sanguins sont utiles pour la fibrose ?",
"position": 2,
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"@type": "Question",
"name": "La fibrose peut-elle être détectée par échographie ?",
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"@type": "Question",
"name": "Quels sont les signes radiologiques de la fibrose ?",
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"@type": "Question",
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"@type": "Question",
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"position": 6,
"acceptedAnswer": {
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"text": "Les symptômes incluent une toux persistante, un essoufflement et une fatigue chronique."
}
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"@type": "Question",
"name": "La fibrose hépatique provoque-t-elle des douleurs ?",
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"@type": "Answer",
"text": "Oui, elle peut causer des douleurs abdominales et une sensation de lourdeur dans l'abdomen."
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{
"@type": "Question",
"name": "Quels signes indiquent une fibrose cardiaque ?",
"position": 8,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les signes incluent des palpitations, un essoufflement à l'effort et des œdèmes."
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"@type": "Question",
"name": "La fibrose peut-elle entraîner une perte de poids ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la fibrose peut causer une perte de poids due à une mauvaise absorption des nutriments."
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"@type": "Question",
"name": "Quels symptômes sont associés à la fibrose systémique ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les symptômes incluent des douleurs articulaires, une raideur cutanée et des troubles circulatoires."
}
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"@type": "Question",
"name": "Comment prévenir la fibrose pulmonaire ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Éviter le tabagisme, réduire l'exposition à des polluants et traiter les infections respiratoires."
}
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{
"@type": "Question",
"name": "Peut-on prévenir la fibrose hépatique ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, en adoptant un mode de vie sain, en évitant l'alcool et en se vaccinant contre l'hépatite."
}
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"@type": "Question",
"name": "Les examens réguliers aident-ils à prévenir la fibrose ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des examens réguliers peuvent détecter précocement des maladies pouvant mener à la fibrose."
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"@type": "Question",
"name": "L'alimentation joue-t-elle un rôle dans la prévention ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, une alimentation équilibrée riche en antioxydants peut aider à prévenir la fibrose."
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"@type": "Question",
"name": "Le contrôle des maladies chroniques aide-t-il ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, bien gérer des maladies comme le diabète ou l'hypertension peut réduire le risque de fibrose."
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"@type": "Question",
"name": "Quels traitements existent pour la fibrose pulmonaire ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les traitements incluent des médicaments antifibrotiques, la réhabilitation pulmonaire et l'oxygénothérapie."
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"@type": "Question",
"name": "La chirurgie est-elle une option pour la fibrose ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, dans certains cas avancés, une transplantation d'organe peut être envisagée."
}
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{
"@type": "Question",
"name": "Quels médicaments sont utilisés pour la fibrose hépatique ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des médicaments pour traiter la cause sous-jacente, comme les antiviraux pour l'hépatite, sont utilisés."
}
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"@type": "Question",
"name": "La physiothérapie aide-t-elle en cas de fibrose ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la physiothérapie peut améliorer la fonction pulmonaire et la qualité de vie."
}
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"@type": "Question",
"name": "Y a-t-il des traitements naturels pour la fibrose ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines approches comme les antioxydants peuvent aider, mais il faut consulter un médecin."
}
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{
"@type": "Question",
"name": "Quelles sont les complications de la fibrose pulmonaire ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent l'insuffisance respiratoire, les infections pulmonaires et les embolies."
}
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"@type": "Question",
"name": "La fibrose hépatique peut-elle entraîner une cirrhose ?",
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"acceptedAnswer": {
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"text": "Oui, la fibrose hépatique peut évoluer vers une cirrhose, entraînant des complications graves."
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"@type": "Question",
"name": "Quels risques sont associés à la fibrose cardiaque ?",
"position": 23,
"acceptedAnswer": {
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"text": "Les risques incluent l'insuffisance cardiaque, les arythmies et les accidents vasculaires cérébraux."
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"@type": "Question",
"name": "La fibrose peut-elle affecter la qualité de vie ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, elle peut réduire la qualité de vie en limitant les activités quotidiennes et en causant de la douleur."
}
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{
"@type": "Question",
"name": "Y a-t-il des complications psychologiques liées à la fibrose ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les patients peuvent éprouver de l'anxiété et de la dépression en raison de leur état de santé."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque de la fibrose pulmonaire ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent le tabagisme, l'exposition à des substances toxiques et des infections antérieures."
}
},
{
"@type": "Question",
"name": "L'âge est-il un facteur de risque pour la fibrose ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le risque de fibrose augmente avec l'âge, surtout après 50 ans."
}
},
{
"@type": "Question",
"name": "Les maladies auto-immunes augmentent-elles le risque de fibrose ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des maladies comme la sclérodermie peuvent prédisposer à la fibrose dans divers organes."
}
},
{
"@type": "Question",
"name": "Le diabète est-il un facteur de risque pour la fibrose hépatique ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le diabète peut augmenter le risque de fibrose hépatique en raison de la stéatose."
}
},
{
"@type": "Question",
"name": "L'exposition professionnelle influence-t-elle le risque de fibrose ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des professions exposant à des poussières ou des produits chimiques peuvent augmenter le risque."
}
}
]
}
]
}
Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 02/04/2025
Contenu vérifié selon les dernières recommandations médicales
4 publications dans cette catégorie
Affiliations :
The Wilf Family Cardiovascular Research Institute, Department of Medicine (Cardiology), Albert Einstein College of Medicine, Bronx, NY, USA. Electronic address: nikolaos.frangogiannis@einsteinmed.org.
Publications dans "Fibrose" :
2 publications dans cette catégorie
Affiliations :
Université Paris Cité and Institut Cochin, Inserm U1016, Paris, France.
Department of Respiratory Medicine and National Reference Center for Cystic Fibrosis, Cochin Hospital, Assistance Publique Hôpitaux de Paris (AP-HP), Paris, France.
Publications dans "Fibrose" :
2 publications dans cette catégorie
Affiliations :
National Heart & Lung Institute, Imperial College London, London, UK.
St Thomas' NHS Trust, London, UK.
Royal Brompton Hospital, Part of Guy's & St Thomas' Trust, London, UK.
Publications dans "Fibrose" :
2 publications dans cette catégorie
Affiliations :
Department of Infectious Disease and Liver Disease, The Second Hospital of Nanjing, Nanjing, Jiangsu, China.
Publications dans "Fibrose" :
2 publications dans cette catégorie
Affiliations :
The Wilf Family Cardiovascular Research Institute, Department of Medicine (Cardiology), Albert Einstein College of Medicine, Bronx, NY, United States of America.
Publications dans "Fibrose" :
2 publications dans cette catégorie
Affiliations :
1Key Laboratory of Prevention and Management of Chronic Kidney Disease of Zhanjiang, Institute of Nephrology, Affiliated Hospital of Guangdong Medical University, Zhanjiang, Guangdong, China.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Adult Cystic Fibrosis Centre, Royal Brompton Hospital and Imperial College, London SW3 6NP, United Kingdom. Electronic address: n.simmonds@imperial.ac.uk.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Department of Biomedical Engineering, University at Buffalo, The State University of New York, Buffalo, NY, USA.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Department of Biomedical Engineering, University at Buffalo, The State University of New York, Buffalo, NY, USA. rgzhao@buffalo.edu.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Section of Pulmonary and Critical Care, Department at University of Chicago, 5841 South Maryland Avenue, MC 6076, Chicago, IL 60637, USA.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Interstitial Lung Disease Program, Section of Pulmonary/Critical Care, University of Chicago, Chicago, IL, USA. Electronic address: deji@uchicago.edu.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiac, Thoracic, Vascular Sciences and Public Health, University Hospital of Padova, Padua, Italy.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Department of Medical and Surgical Sciences, University Hospital of Modena, Respiratory Diseases Unit and Centre for Rare Lung Diseases, University of Modena Reggio Emilia, Modena, Italy.
Clinical and Experimental Medicine PhD Program, University of Modena Reggio Emilia, Modena, Italy.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Department of Medical and Surgical Sciences, University Hospital of Modena, Internal Medicine Unit, University of Modena Reggio Emilia, Modena, Italy.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Department of Medical and Surgical Sciences, University Hospital of Modena, Respiratory Diseases Unit and Centre for Rare Lung Diseases, University of Modena Reggio Emilia, Modena, Italy.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Department of Medical and Surgical Sciences, University Hospital of Modena, Respiratory Diseases Unit and Centre for Rare Lung Diseases, University of Modena Reggio Emilia, Modena, Italy.
Clinical and Experimental Medicine PhD Program, University of Modena Reggio Emilia, Modena, Italy.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Department of Surgical, Oncological and Gastroenterological Sciences, Unit of Gastroenterology, University of Padova, Padua, Italy.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Department of Surgical, Oncological and Gastroenterological Sciences, Unit of Gastroenterology, University of Padova, Padua, Italy.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Department of Medical and Surgical Sciences, University Hospital of Modena, Internal Medicine Unit, University of Modena Reggio Emilia, Modena, Italy.
Publications dans "Fibrose" :
1 publication dans cette catégorie
Affiliations :
Department of Cardiac, Thoracic, Vascular Sciences and Public Health, University Hospital of Padova, Padua, Italy.
Publications dans "Fibrose" :
Valid, responsive blood biomarkers specific to peripheral nerve damage would improve management of peripheral nervous system (PNS) diseases. Neurofilament light chain (NfL) is sensitive for detecting ...
The light-sensitive outer segment organelle of photoreceptor cells contains a stack of hundreds of flat, disc-shaped membranes called discs. The rims of these discs contain a photoreceptor-specific te...
To describe the clinical, electrophysiological and genetic spectrum of inherited retinal diseases associated with variants in the PRPH2 gene....
A total of 241 patients from 168 families across 15 sites in 9 countries with pathogenic or likely pathogenic variants in PRPH2 were included. Records were reviewed for age at symptom onset, visual ac...
The median age at symptom onset was 40 years (range, 4-78 years). FAF phenotypes included normal (5%), butterfly pattern dystrophy, or vitelliform macular dystrophy (11%), central areolar choroidal dy...
We described six distinct FAF phenotypes associated with variants in the PRPH2 gene. One FAF phenotype may have multiple ERG phenotypes, demonstrating a discordance between structure and function. Giv...
More than 200 different mutations in peripherin-2 (PRPH2) are associated with multiple subtypes of inherited retinal diseases (IRDs), including retinitis pigmentosa and cone or macular diseases. Our g...
Eleven patients had clinical assessments including best-corrected visual acuity (BCVA), full field and multifocal electroretinography (ERG), static (spot size V) and kinetic perimetry (Octopus 900), a...
Patients with the P210R mutation had BCVA (Snellen) ranging from 20/15 to 20/80. Perimetry showed a reduction in sensitivity, while ERG findings suggested that cone function was more impaired than rod...
Rod and cone sensitivities were decreased in subjects with the P210R mutation in PRPH2. There was scotomatous vision loss that occurred within the macula, likely due to atrophy that occurs after druse...
Heterozygous peripherin mutation is associated with a wide range of typically adult-onset retinal phenotypes which can include asymptomatic maculopathy. There are few reports of biallelic peripherin m...
Retrospective case series....
A 13-year-old Emirati boy was referred for low vision. The parents felt he was blind at birth but noted improvement with time. Retinal examination was significant for central macula horizontal ovoid d...
The experience with this family highlights clinical features suggestive for biallelic peripherin mutations, documents cone-rod dysfunction as associated with homozygosity for the p.Arg220Gln peripheri...
Intermediate filaments are the most heterogeneous class among cytoskeletal elements. While some of them have been well-characterized, little is known about peripherin. Peripherin is a class III interm...
Mutations in peripherin 2 (PRPH2) are associated with a spectrum of inherited retinal diseases (IRDs) including retinitis pigmentosa (RP) and macular degeneration. As PRPH2 is localized to cone and ro...
We sought to explore whether sex imbalances are discernible in several autosomally inherited macular dystrophies....
We searched the electronic patient records of our large inherited retinal disease cohort, quantifying numbers of males and females with the more common (non-ABCA4) inherited macular dystrophies (assoc...
Of 325 patients included, numbers for BEST1, EFEMP1, PROM1, PRPH2, RP1L1, and TIMP3 were 152, 35, 30, 50, 14, and 44, respectively. For autosomal dominant Best disease (n = 115), there were fewer fema...
This exploratory study found significant sex imbalances in two autosomal macular dystrophies, suggesting that sex could be a modifier. Our findings invite replication in further cohorts and the invest...
The present study investigated retinal glia and choroidal vessels in flatmounts and sections from individuals with clinically diagnosed Stargardt disease (STGD)....
Eyes from three donors clinically diagnosed with STGD were obtained through the Foundation Fighting Blindness (FFB). Genetic testing was performed to determine the disease-causing mutations. Eyes were...
Genetic testing confirmed the STGD diagnosis in donor 1, whereas a mutation in peripherin 2 was identified in donor 3. Genetic testing was not successful on donor 2. Therefore, only donor 1 can defini...
Despite bearing different genetic mutations, all donors demonstrated choriocapillaris loss and Müller cell membranes correlating with RPE loss. Müller cell remodeling was most extensive in the donor w...
Prph2 is a photoreceptor-specific tetraspanin with an essential role in the structure and function of photoreceptor outer segments. PRPH2 mutations cause a multitude of retinal diseases characterized ...