questionsmedicales.fr
Cellules
Neurones
Neurofibres
Gaine de myéline
Gaine de myéline : Questions médicales fréquentes
Termes MeSH sélectionnés :
Diagnostic
5
Démence
Imagerie par résonance magnétique
Potentiels évoqués
Évaluation neurologique
Sclérose en plaques
Neuropathie
Biopsie
Maladies neurologiques
Symptômes
5
Fatigue
Troubles de la vision
Douleur neuropathique
Syndrome douloureux
Coordination
Troubles de l'équilibre
Troubles cognitifs
Mémoire
Variabilité des symptômes
Sclérose en plaques
Prévention
5
Prévention
Mode de vie sain
Exercice physique
Santé neurologique
Traitements
5
Médicaments immunomodulateurs
Thérapies symptomatiques
Rééducation
Thérapie physique
Corticostéroïdes
Inflammation
Thérapie génique
Cellules souches
Gestion des symptômes
Progrès de la maladie
Complications
5
Infections
Douleurs chroniques
Troubles visuels
Progression de la maladie
Handicap
Fonction cognitive
Réversibilité
Gestion des complications
Facteurs de risque
5
Antécédents familiaux
Infections virales
Sexe
Maladies démyélinisantes
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"description": "Comment diagnostiquer une démyélinisation ?\nQuels tests sont utilisés pour évaluer la myéline ?\nQuels signes indiquent une atteinte de la myéline ?\nLa biopsie nerveuse est-elle nécessaire ?\nQuels marqueurs biologiques sont associés à la démyélinisation ?",
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"name": "Comment diagnostiquer une démyélinisation ?",
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"text": "Un IRM peut révéler des lésions de myéline dans le système nerveux central."
}
},
{
"@type": "Question",
"name": "Quels tests sont utilisés pour évaluer la myéline ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les potentiels évoqués et les tests neurologiques aident à évaluer la fonction myélinique."
}
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{
"@type": "Question",
"name": "Quels signes indiquent une atteinte de la myéline ?",
"position": 3,
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{
"@type": "Question",
"name": "La biopsie nerveuse est-elle nécessaire ?",
"position": 4,
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"@type": "Question",
"name": "Quels sont les symptômes d'une démyélinisation ?",
"position": 6,
"acceptedAnswer": {
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"text": "Les symptômes incluent fatigue, troubles de la vision, et faiblesse musculaire."
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"@type": "Question",
"name": "La douleur est-elle un symptôme courant ?",
"position": 7,
"acceptedAnswer": {
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"text": "Oui, des douleurs neuropathiques peuvent survenir en raison de la démyélinisation."
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{
"@type": "Question",
"name": "Comment la démyélinisation affecte-t-elle la coordination ?",
"position": 8,
"acceptedAnswer": {
"@type": "Answer",
"text": "Elle peut provoquer des troubles de l'équilibre et des mouvements maladroits."
}
},
{
"@type": "Question",
"name": "Les troubles cognitifs sont-ils liés à la démyélinisation ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des problèmes de mémoire et de concentration peuvent survenir."
}
},
{
"@type": "Question",
"name": "Les symptômes varient-ils d'une personne à l'autre ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'intensité et le type de symptômes peuvent varier considérablement."
}
},
{
"@type": "Question",
"name": "Peut-on prévenir la démyélinisation ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'existe pas de méthode garantie, mais un mode de vie sain peut réduire les risques."
}
},
{
"@type": "Question",
"name": "L'alimentation joue-t-elle un rôle ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Une alimentation riche en oméga-3 et en antioxydants peut être bénéfique."
}
},
{
"@type": "Question",
"name": "Le stress influence-t-il la démyélinisation ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le stress peut aggraver les symptômes et déclencher des poussées."
}
},
{
"@type": "Question",
"name": "L'exercice physique est-il recommandé ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'exercice régulier peut améliorer la santé neurologique et physique."
}
},
{
"@type": "Question",
"name": "Les vaccinations sont-elles importantes ?",
"position": 15,
"acceptedAnswer": {
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"text": "Certaines vaccinations peuvent aider à prévenir des infections qui aggravent la démyélinisation."
}
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"name": "Quels traitements existent pour la démyélinisation ?",
"position": 16,
"acceptedAnswer": {
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"text": "Les traitements incluent des médicaments immunomodulateurs et des thérapies symptomatiques."
}
},
{
"@type": "Question",
"name": "La rééducation est-elle utile ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la rééducation physique peut aider à améliorer la fonction et la mobilité."
}
},
{
"@type": "Question",
"name": "Les corticostéroïdes sont-ils efficaces ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Ils peuvent réduire l'inflammation et accélérer la récupération lors des poussées."
}
},
{
"@type": "Question",
"name": "Y a-t-il des traitements expérimentaux ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des thérapies géniques et des traitements à base de cellules souches sont en cours d'étude."
}
},
{
"@type": "Question",
"name": "Les traitements sont-ils curatifs ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Non, ils visent principalement à gérer les symptômes et à ralentir la progression."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des complications incluent des infections, des troubles de la mobilité et des douleurs chroniques."
}
},
{
"@type": "Question",
"name": "La dépression est-elle une complication fréquente ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la dépression est courante chez les personnes atteintes de démyélinisation."
}
},
{
"@type": "Question",
"name": "Les troubles de la vision peuvent-ils s'aggraver ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des troubles visuels peuvent s'aggraver avec la progression de la maladie."
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{
"@type": "Question",
"name": "Y a-t-il un risque accru de handicap ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la démyélinisation peut entraîner un handicap physique ou cognitif à long terme."
}
},
{
"@type": "Question",
"name": "Les complications sont-elles réversibles ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines complications peuvent être gérées, mais beaucoup ne sont pas réversibles."
}
},
{
"@type": "Question",
"name": "Quels sont les principaux facteurs de risque ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des antécédents familiaux, l'âge et des infections virales."
}
},
{
"@type": "Question",
"name": "Le sexe influence-t-il le risque ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les femmes sont plus susceptibles de développer des maladies démyélinisantes."
}
},
{
"@type": "Question",
"name": "Le tabagisme est-il un facteur de risque ?",
"position": 28,
"acceptedAnswer": {
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"text": "Oui, le tabagisme est associé à un risque accru de démyélinisation."
}
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"name": "L'exposition à des toxines joue-t-elle un rôle ?",
"position": 29,
"acceptedAnswer": {
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"text": "Oui, l'exposition à certaines toxines environnementales peut augmenter le risque."
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"@type": "Question",
"name": "Le climat a-t-il un impact sur le risque ?",
"position": 30,
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"text": "Oui, des études montrent que les personnes vivant dans des climats froids ont un risque plus élevé."
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Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 29/04/2025
Contenu vérifié selon les dernières recommandations médicales
4 publications dans cette catégorie
Affiliations :
Department of Pediatrics, Section of Developmental Biology, University of Colorado, Aurora, CO, USA. bruce.appel@cuanschutz.edu.
Publications dans "Gaine de myéline" :
3 publications dans cette catégorie
Affiliations :
Section on Nervous System Development and Plasticity, The Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD), National Institutes of Health (NIH), Bethesda, MD 20892, USA. Electronic address: fieldsd@mail.nih.gov.
Publications dans "Gaine de myéline" :
3 publications dans cette catégorie
Publications dans "Gaine de myéline" :
3 publications dans cette catégorie
Affiliations :
Centre for Discovery Brain Sciences, University of Edinburgh, Edinburgh EH8 9XD, United Kingdom.
Publications dans "Gaine de myéline" :
3 publications dans cette catégorie
Affiliations :
McConnell Brain Imaging Centre, Montreal Neurological Institute and Hospital, Montreal, Quebec, Canada.
Department of Neurology and Neurosurgery, McGill University, Montreal, Quebec, Canada.
Publications dans "Gaine de myéline" :
3 publications dans cette catégorie
Affiliations :
Department of Radiology, University of British Columbia, Vancouver, British Columbia, Canada.
Publications dans "Gaine de myéline" :
3 publications dans cette catégorie
Affiliations :
Department of Physics and Astronomy, University of British Columbia, Vancouver, British Columbia, Canada.
International Collaboration on Repair Discoveries, University of British Columbia, Vancouver, British Columbia, Canada.
Department of Radiology, University of British Columbia, Vancouver, British Columbia, Canada.
Department of Medicine, University of British Columbia, Vancouver, British Columbia, Canada.
Publications dans "Gaine de myéline" :
3 publications dans cette catégorie
Affiliations :
Department of Medicine, University of British Columbia, Vancouver, British Columbia, Canada.
Publications dans "Gaine de myéline" :
3 publications dans cette catégorie
Affiliations :
Department of Physics and Astronomy, University of British Columbia, Vancouver, British Columbia, Canada.
International Collaboration on Repair Discoveries, University of British Columbia, Vancouver, British Columbia, Canada.
Department of Radiology, University of British Columbia, Vancouver, British Columbia, Canada.
Department of Medicine, University of British Columbia, Vancouver, British Columbia, Canada.
Department of Pathology & Laboratory Medicine, University of British Columbia, Vancouver, British Columbia, Canada.
Publications dans "Gaine de myéline" :
2 publications dans cette catégorie
Affiliations :
Neuroscience Graduate Program, University of Colorado, Aurora, CO, USA.
Publications dans "Gaine de myéline" :
2 publications dans cette catégorie
Publications dans "Gaine de myéline" :
2 publications dans cette catégorie
Publications dans "Gaine de myéline" :
2 publications dans cette catégorie
Publications dans "Gaine de myéline" :
2 publications dans cette catégorie
Publications dans "Gaine de myéline" :
2 publications dans cette catégorie
Publications dans "Gaine de myéline" :
2 publications dans cette catégorie
Publications dans "Gaine de myéline" :
2 publications dans cette catégorie
Publications dans "Gaine de myéline" :
2 publications dans cette catégorie
Publications dans "Gaine de myéline" :
2 publications dans cette catégorie
Publications dans "Gaine de myéline" :
2 publications dans cette catégorie
Affiliations :
Centre for Regenerative Medicine, Institute for Regeneration and Repair, University of Edinburgh, Edinburgh EH16 4UU, United Kingdom M.R.Livesey@Sheffield.ac.uk m.swire@ucl.ac.uk.
Centre for Discovery Brain Sciences, University of Edinburgh, Edinburgh EH8 9XD, United Kingdom.
Wolfson Institute for Biomedical Research, University College London, London WC1E 6BT, United Kingdom.
Publications dans "Gaine de myéline" :
The role and potential molecular mechanism of inflammatory cells in pediatric localized scleroderma are poorly investigated. In this study, we first investigated the profiling of inflammatory cells in...
Connective tissue nevi (CTN) are congenital hamartomas caused by excessive proliferation of dermis components. In children, CTN can mimic juvenile localized scleroderma (JLS), an immune mediated skin ...
Aim of our study was to describe a series of pediatric patients with CTN misdiagnosed as JLS and the discerning characteristics between the two conditions....
Retrospective analysis of children referred to our Center during the last two decades for JLS who received a final diagnosis of CTN. Clinical, laboratory, histopathological and instrumental data (MRI ...
Seventeen patients with mean age at onset 4.6 years entered the study. All came to our Center with a certain diagnosis of JLS (n = 15) or suspected JLS (n = 2). The indurated skin lesions were flat an...
CTN can be misdiagnosed as JLS and therefore aggressively treated with prolonged and inappropriate immunosuppression. The absence of inflammatory appearance of the skin lesions, normal instrumental an...
Juvenile localized scleroderma (JLS) or morphoea, a rare chronic autoimmune disease predominantly affects skin, subcutaneous tissue and occasionally the adjacent muscle, fascia and bone. We report the...
Patients who were diagnosed to have JLS were enrolled from the Paediatric Dermatology Clinic and the Paediatric Rheumatology Clinic of a tertiary care referral hospital in India. Collected data includ...
We analysed 84 patients with Juvenile localized scleroderma. Median age of disease onset was 5 years, and median age at diagnosis was 8 years. Commonest subtype was linear scleroderma (57 patients, 67...
Early use of systemic corticosteroids along with methotrexate may be more beneficial than methotrexate therapy alone....
Current treatment for localized scleroderma (LS) has been shown to halt disease activity, but little is still known about patient experiences with these treatments, nor is there consensus about optima...
Conduct a scoping review of the literature for the types of outcomes and measures (i.e. clinician-, patient-, and caregiver-reported) utilized in published treatment studies of LS....
Online databases were searched for articles related to the evaluation of treatment efficacy in LS with a special focus on pediatrics....
Of the 168 studies, the most common outcomes used were cutaneous disease activity and damage measured via clinician-reported assessments. The most frequently cited measure was the Localized Scleroderm...
Some studies only vaguely reported the measures utilized, and the review yielded a low number of clinical trials....
In addition to evaluating disease activity with clinician-reported measures, the field could obtain critical knowledge on the patient experience by including high-quality PROMs of symptoms and functio...
Infrared thermography (IRT) is a useful method to detect activity/inflammation in localized scleroderma (LoS); however, inactive skin lesions with a severe degree of dermal and subcutaneous atrophy ma...
The aim of this research was to compare the spectrophotometric results with thermographic examination of LoS lesions....
The lesions were assessed using the Localized Scleroderma Assessment Tool (LoSCAT), Dyspigmentation, Induration, Erythema, and Telangiectasias (DIET) score, NBRS and IRT. The difference in the erythem...
Fifty-five patients with 49 active and 64 inactive LoS lesions were examined. The ΔEI strongly correlated with the erythema (r...
Narrow-band reflectance spectrophotometry may be a complementary method for determining erythema in LoS active lesions, although this technique remains inferior to IRT, because is unable to distinct b...
Localized scleroderma (LS) is an autoimmune disease with both inflammatory and fibrotic components causing an abnormal deposition of collagen in the skin and underlying tissue, often leading to disfig...
Localized scleroderma (LS) is characterized by skin fibrosis, hyperpigmentation and soft tissue atrophy. Fat grafting has been widely used to correct LS deformity....
To investigate the effect of fat grafting on the skin pigmentation of LS lesions....
A prospective self-controlled study was conducted. Skin melanin and erythema indexes were measured by Mexameter® MX18 before and 3 months after surgery. Differences between lesions and contralateral n...
Fourteen frontal linear LS patients participated in the study. Before surgery, the melanin index of the lesions was significantly higher than the contralateral sites (p = 0.023), while the erythema in...
Fat grafting could alleviate skin hyperpigmentation and skin damage of LS lesions while having little effect on skin erythema and disease activity....
This journal requires that authors assign a level of evidence to each article. For a full description of these Evidence-Based Medicine ratings, please refer to the Table of Contents or the online Inst...
Scleroderma is a rare complication in taxanes therapy. Although individual cases of taxanes-induced scleroderma have been reported, the clinical manifestation and treatment outcomes were reviewed and ...
A PubMed literature review on published cases of taxanes-induced scleroderma up until April 2022 was included for analysis....
The search identified 27 patients with adequate information for analysis. Of the 28 patients, including the one presented here, 22 were female. Peripheral edema was the most common symptom in all but ...
Taxanes-induced scleroderma is different from idiopathic scleroderma. Physicians should be aware of this condition in order to provide early diagnosis and apply appropriate management in order to avoi...
Localized scleroderma (LS) is an autoimmune disease characterized by inflammation and fibrosis, leading to severe cutaneous manifestations such as skin hardening, tightness, discoloration, and other t...
Juvenile localized and systemic scleroderma are rare autoimmune diseases which cause significant disability and morbidity in children. The mechanisms driving juvenile scleroderma remain unclear, neces...