questionsmedicales.fr
Phénomènes chimiques
Phénomènes biochimiques
Conformation moléculaire
Conformation des protéines
Conformation des protéines : Questions médicales fréquentes
Termes MeSH sélectionnés :
Diagnostic
5
Protéines
Spectroscopie
Cristallographie
Électrophorèse
Chromatographie
Protéines
Biomarqueurs
Protéines
Maladies protéiques
Imagerie par résonance magnétique
Protéines
Diagnostic
Symptômes
Protéines
Maladies
Symptômes
5
Symptômes
Maladies protéiques
Troubles neurologiques
Dysfonctionnement cellulaire
Maladies dégénératives
Protéines
Alzheimer
Protéines
Troubles cognitifs
Maladie de prion
Troubles neurologiques
Comportement
Myopathie
Douleurs musculaires
Protéines
Prévention
5
Prévention
Alimentation
Exercice
Tests génétiques
Prédispositions
Maladies protéiques
Éducation
Symptômes
Traitement
Vaccinations
Infections
Protéines
Stress oxydatif
Protéines
Maladies
Traitements
5
Thérapie génique
Médicaments
Maladies protéiques
Médicaments
Protéines
Repliement
Thérapies biologiques
Protéines
Fonction cellulaire
Chaperonnes
Protéines
Agrégats
Alimentation
Antioxydants
Protéines
Complications
5
Complications
Maladies neurodégénératives
Troubles métaboliques
Maladies de prion
Démences
Troubles neurologiques
Système immunitaire
Anomalies protéiques
Vulnérabilité
Complications cardiovasculaires
Protéines
Maladies
Troubles métaboliques
Protéines
Perturbation
Facteurs de risque
5
Facteurs de risque
Prédispositions génétiques
Toxines
Vieillissement
Protéines
Anomalies
Alimentation
Nutriments
Risque
Stress environnemental
Pollution
Protéines
Infections virales
Maladies protéiques
Protéines
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"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, elle aide à reconnaître les symptômes précoces et à chercher un traitement."
}
},
{
"@type": "Question",
"name": "Les vaccinations peuvent-elles prévenir des maladies liées aux protéines ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines vaccinations peuvent réduire le risque d'infections qui affectent les protéines."
}
},
{
"@type": "Question",
"name": "Le stress peut-il influencer la conformation des protéines ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le stress oxydatif peut perturber le repliement des protéines et causer des maladies."
}
},
{
"@type": "Question",
"name": "Quels traitements existent pour les maladies liées à la conformation protéique ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les traitements incluent des thérapies géniques, des médicaments et des approches symptomatiques."
}
},
{
"@type": "Question",
"name": "Peut-on corriger la conformation des protéines par des médicaments ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certains médicaments peuvent stabiliser ou corriger le repliement des protéines."
}
},
{
"@type": "Question",
"name": "Les thérapies biologiques sont-elles efficaces contre les anomalies protéiques ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, elles peuvent cibler des protéines spécifiques et améliorer la fonction cellulaire."
}
},
{
"@type": "Question",
"name": "Quels rôles jouent les chaperonnes dans le traitement des maladies protéiques ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les chaperonnes aident à replier correctement les protéines, réduisant les agrégats."
}
},
{
"@type": "Question",
"name": "Les approches diététiques peuvent-elles influencer la conformation des protéines ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, une alimentation riche en antioxydants peut aider à maintenir la santé protéique."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir avec des anomalies protéiques ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des complications incluent des maladies neurodégénératives et des troubles métaboliques."
}
},
{
"@type": "Question",
"name": "Les maladies de prion entraînent-elles des complications graves ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, elles peuvent causer des démences rapides et des troubles neurologiques sévères."
}
},
{
"@type": "Question",
"name": "Comment les anomalies protéiques affectent-elles le système immunitaire ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Elles peuvent altérer la réponse immunitaire, rendant l'organisme plus vulnérable."
}
},
{
"@type": "Question",
"name": "Les complications cardiovasculaires sont-elles liées à des anomalies protéiques ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines protéines mal conformées peuvent contribuer à des maladies cardiovasculaires."
}
},
{
"@type": "Question",
"name": "Les troubles métaboliques peuvent-ils résulter d'anomalies protéiques ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des protéines mal repliées peuvent perturber le métabolisme et causer des troubles."
}
},
{
"@type": "Question",
"name": "Quels facteurs de risque sont associés aux maladies protéiques ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des prédispositions génétiques, l'âge et l'exposition à des toxines."
}
},
{
"@type": "Question",
"name": "Le vieillissement est-il un facteur de risque pour les anomalies protéiques ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le vieillissement peut affecter le repliement et la fonction des protéines."
}
},
{
"@type": "Question",
"name": "L'alimentation influence-t-elle le risque de maladies protéiques ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, une alimentation pauvre en nutriments essentiels peut augmenter le risque."
}
},
{
"@type": "Question",
"name": "Le stress environnemental peut-il affecter la conformation des protéines ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des facteurs comme la pollution peuvent perturber le repliement des protéines."
}
},
{
"@type": "Question",
"name": "Les infections virales sont-elles un facteur de risque pour les maladies protéiques ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines infections peuvent induire des modifications dans la conformation des protéines."
}
}
]
}
]
}
Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 25/02/2025
Contenu vérifié selon les dernières recommandations médicales
2 publications dans cette catégorie
Affiliations :
Departamento de Ciencia y Tecnología, Universidad Nacional de Quilmes, CONICET, Bernal, Argentina.
Publications dans "Conformation des protéines" :
2 publications dans cette catégorie
Affiliations :
Structural Bioinformatics Unit, Fundación Instituto Leloir, CONICET, Buenos Aires, Argentina.
Publications dans "Conformation des protéines" :
2 publications dans cette catégorie
Affiliations :
Departamento de Ciencia y Tecnología, Universidad Nacional de Quilmes, CONICET, Bernal, Argentina. gusparisi@gmail.com.
Publications dans "Conformation des protéines" :
2 publications dans cette catégorie
Affiliations :
Computer Science and Engineering Department, Koc University, Istanbul, Turkey. agursoy@ku.edu.tr.
Publications dans "Conformation des protéines" :
2 publications dans cette catégorie
Affiliations :
Chemical and Biological Engineering Department, Koc University, Istanbul, Turkey.
Publications dans "Conformation des protéines" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, North Carolina Agricultural and Technical State University, Greensboro, NC, USA.
Publications dans "Conformation des protéines" :
2 publications dans cette catégorie
Affiliations :
Department of Biochemistry, University of Washington, Seattle, WA 98105; dabaker@uw.edu so@fas.harvard.edu.
Institute for Protein Design, University of Washington, Seattle, WA 98105.
Howard Hughes Medical Institute, University of Washington, Seattle, WA 98105.
Publications dans "Conformation des protéines" :
2 publications dans cette catégorie
Affiliations :
Center for Research Computing, Center for Drug Discovery, Design, and Delivery (CD4), Department of Chemistry, Southern Methodist University, Dallas, TX, United States.
Publications dans "Conformation des protéines" :
2 publications dans cette catégorie
Affiliations :
Center for Research Computing, Center for Drug Discovery, Design, and Delivery (CD4), Department of Chemistry, Southern Methodist University, Dallas, TX, United States.
Publications dans "Conformation des protéines" :
2 publications dans cette catégorie
Affiliations :
Center for Research Computing, Center for Drug Discovery, Design, and Delivery (CD4), Department of Chemistry, Southern Methodist University, Dallas, TX, United States.
Publications dans "Conformation des protéines" :
1 publication dans cette catégorie
Affiliations :
Departamento de Ciencia y Tecnología, Universidad Nacional de Quilmes, CONICET, Bernal, Argentina.
Publications dans "Conformation des protéines" :
1 publication dans cette catégorie
Affiliations :
Department of Chemistry and Chemical Biology, Baker Laboratory, Cornell University, Ithaca, New York, USA.
Publications dans "Conformation des protéines" :
1 publication dans cette catégorie
Affiliations :
Department of Chemistry and Chemical Biology, Baker Laboratory, Cornell University, Ithaca, New York, USA.
Department of Biochemistry and Biophysics, University of Rochester School of Medicine and Dentistry, Rochester, New York, USA.
Publications dans "Conformation des protéines" :
1 publication dans cette catégorie
Affiliations :
Department of Pharmacological Sciences, Icahn School of Medicine at Mount Sinai, New York, United States.
Publications dans "Conformation des protéines" :
1 publication dans cette catégorie
Affiliations :
Department of Structural Biology and Chemistry, Institut Pasteur, Université Paris Cité, Paris, France.
Publications dans "Conformation des protéines" :
1 publication dans cette catégorie
Affiliations :
Department of Biotechnology, University of Verona, 37134 Verona, Italy.
Publications dans "Conformation des protéines" :
1 publication dans cette catégorie
Affiliations :
Departamento de Ciencia y Tecnología, Universidad Nacional de Quilmes and Grupo de Biología Estructural y Biotecnología, IMBICE, CONICET, Universidad Nacional de Quilmes, Argentina.
Publications dans "Conformation des protéines" :
1 publication dans cette catégorie
Affiliations :
Departamento de Ciencia y Tecnología, Universidad Nacional de Quilmes and Grupo de Biología Estructural y Biotecnología, IMBICE, CONICET, Universidad Nacional de Quilmes, Argentina.
Publications dans "Conformation des protéines" :
1 publication dans cette catégorie
Affiliations :
Departamento de Ciencia y Tecnología, Universidad Nacional de Quilmes and Grupo de Biología Estructural y Biotecnología, IMBICE, CONICET, Universidad Nacional de Quilmes, Argentina.
Publications dans "Conformation des protéines" :
1 publication dans cette catégorie
Affiliations :
Departamento de Ciencia y Tecnología, Universidad Nacional de Quilmes and Grupo de Biología Estructural y Biotecnología, IMBICE, CONICET, Universidad Nacional de Quilmes, Argentina.
Publications dans "Conformation des protéines" :
Previous studies have suggested that patients with pulmonary sarcomatoid carcinoma (PSC)may benefit from immune checkpoint inhibitors (ICIs); however, relevant data are lacking. This study aimed to es...
A retrospective analysis of pathologically confirmed PSC cases from two centers was performed from January 2009 to May 2021. According to the infiltration of CD8+ T cells in different spatial regions,...
A total of 32 patients with PSC were included in the final analysis. Of these patients, 65.6% (21/32), 15.6% (5/32), and 18.8% (6/32) were classified as immune-inflamed, immune-excluded, and immune-de...
Patients with PSC are characterized by immune-inflamed type and type I (PD-L1+/CD8+, adaptive immune resistance), explaining the intrinsic reasons for their high response rate to immunotherapy....
Atrial fibrillation (AF) is a relatively common arrhythmia in clinical practice. Although significant progress has been achieved in the treatment of AF and its associated complications, research on AF...
To characterize the immunophenotypic profile of acute leukemias in the population of the state of Bahia, Brazil....
This is a descriptive, retrospective study. From 2014 to 2018, 796 new cases of acute leukemia were evaluated. The data were obtained from analysis of reports and records of tests performed by flow cy...
Most cases were diagnosed as acute myeloid leukemia and 42.7% as acute lymphoblastic leukemia. Significant differences were found in expression of markers in acute leukemias when age groups were compa...
Significant differences were found as to several antigens when comparing adults and children, and these findings may contribute to future studies correlating the phenotypic profile to genetic characte...
Flow cytometry enables multiparametric characterization of hematopoietic cell immunophenotype. Deviations from normal immunophenotypic patterns comprise a cardinal feature of many hematopoietic neopla...
Plasma cell myeloma (PCM) is defined as a clonal disease of terminally differentiated plasma cells that secrete immunoglobulin. The biologic underpinnings of IgA-type multiple myeloma's (IgAMM) aggres...
ASD reconstructions are a major, sterile traumatic insult, likely causing perturbations to the immune systems. The immune response to surgery is associated with outcomes. The purpose of this study was...
Consecutive patients undergoing ASD surgery were approached and enrolled. Peripheral blood was drawn before incision, 4 h after, and 24 h after incision. Blood was stabilized and comprehensive flow cy...
Thirteen patients were enrolled; 11(85%) F, 65.4 years (± 7.5), surgical duration 418 ± 83 min, EBL 1928 ± 1253 mL. Hierarchical clustering and PCA found consistent time from incision-dependent change...
Despite surgery and patient heterogeneity, we identified an immune signature associated with the sterile trauma of ASD surgery. Circulating leukocyte populations change in composition and signaling pr...
We aimed to provide an autophagy-related signature to seek immunophenotyping biomarkers in osteoarthritis (OA)....
Microarray expression profiling of OA subchondral bone samples and screening of an autophagy database for autophagy-related differentially expressed genes (au-DEGs) between OA and normal samples were ...
We screened 754 au-DEGs between OA and control samples, and co-expression networks were constructed using au-DEGs. Three OA-related autophagy hub genes (HSPA5, HSP90AA1, and ITPKB) were identified. Ba...
Three autophagy-related markers of OA were identified using bioinformatics methods, and these markers may be useful for the autophagy-related immunophenotyping of OA. The present data may facilitate t...
Prompt diagnosis of acute promyelocytic leukemia (APL) is critical for patient care. In this study, we aimed to characterize the immunophenotype of APL and explore immunophenotypic difference between ...
Eighty-five cases were collected, including 47 APL, 26 NPM1-mutated acute myeloid leukemia (AML) and 12 KMT2A-rearranged AML with an APL-like immunophenotype. Immunophenotypes were analyzed using flow...
APL showed four distinct patterns (designated a-d) based on CD45/SSC plots. Blasts in patterns a-c showed high side scatter, whereas blasts in pattern d had low side scatter and were located in the tr...
APL and its immunophenotypic mimics share some immunophenotypic similarities but can be distinguished by CD2, CD13, CD34, CD64, and MPO....
Acute myeloid leukemia (AML) with RAM immunophenotype is a distinct subtype of AML, as described by the Children's Oncology Group (COG), with characteristic morphological and immunophenotypic properti...
Seven cases with the characteristic RAM immunophenotype were identified in this retrospective analysis of newly diagnosed pediatric AML cases from January 2019 to December 2021. Herein, we have critic...
Of 302 cases of pediatric AML (age <18 years), seven cases (2.3%) with the distinct RAM phenotype were observed, with age ranging from 9 months to 5 years. Two patients were misdiagnosed earlier as sm...
AML with RAM immunophenotype, a distinct form of pediatric AML with a poor prognosis, may pose a diagnostic challenge if presented as a soft tissue mass. A comprehensive immunophenotypic evaluation, i...
Tγδ large granular lymphocyte leukemia (Tγδ LGLL) is a rare lymphoproliferative disease, scantily described in literature. A deep-analysis, in an initial cohort of 9 Tγδ LGLL compared to 23 healthy co...