questionsmedicales.fr
Maladies du système nerveux
Maladies du système nerveux central
Encéphalopathies
Épilepsie
Syndromes épileptiques
Épilepsies myocloniques
Épilepsies myocloniques : Questions médicales fréquentes
Termes MeSH sélectionnés :
Diagnostic
5
Épilepsie
Électroencéphalographie
Crises épileptiques
Symptômes neurologiques
Électroencéphalographie
Épilepsie
Symptômes
5
Myoclonies
Crises épileptiques
Myoclonies
Symptômes neurologiques
Crises épileptiques
Épilepsie
Épilepsie
Variabilité des symptômes
Crises nocturnes
Épilepsie
Prévention
5
Prévention des crises
Épilepsie
Déclencheurs de crises
Stress
Éducation des patients
Épilepsie
Activité physique
Sécurité
Traitements
5
Anticonvulsivants
Traitement de l'épilepsie
Thérapie comportementale
Diète cétogène
Évaluation du traitement
Épilepsie
Traitement à long terme
Épilepsie
Effets secondaires
Anticonvulsivants
Complications
5
Complications
Troubles psychologiques
Soutien psychologique
Thérapies
Facteurs de risque
5
Facteurs de risque
Traumatismes crâniens
Troubles neurologiques
Épilepsie
Stress
Déclencheurs de crises
Infections cérébrales
Méningite
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"@type": "Question",
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"@type": "Question",
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"name": "Quels sont les symptômes principaux ?",
"position": 6,
"acceptedAnswer": {
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"@type": "Question",
"name": "Les myoclonies sont-elles douloureuses ?",
"position": 7,
"acceptedAnswer": {
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"text": "Les myoclonies ne sont généralement pas douloureuses, mais peuvent être gênantes."
}
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{
"@type": "Question",
"name": "Peut-on avoir des crises sans myoclonies ?",
"position": 8,
"acceptedAnswer": {
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"text": "Oui, certaines personnes peuvent avoir des crises généralisées sans myoclonies."
}
},
{
"@type": "Question",
"name": "Les symptômes varient-ils d'une personne à l'autre ?",
"position": 9,
"acceptedAnswer": {
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"text": "Oui, l'intensité et la fréquence des symptômes peuvent varier considérablement."
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"@type": "Question",
"name": "Les crises peuvent-elles survenir la nuit ?",
"position": 10,
"acceptedAnswer": {
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}
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{
"@type": "Question",
"name": "Peut-on prévenir les crises myocloniques ?",
"position": 11,
"acceptedAnswer": {
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"text": "La prévention passe par un traitement adéquat et l'évitement des déclencheurs."
}
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{
"@type": "Question",
"name": "Quels déclencheurs sont à éviter ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le stress, la fatigue, et la consommation d'alcool peuvent déclencher des crises."
}
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{
"@type": "Question",
"name": "L'éducation est-elle importante pour la prévention ?",
"position": 13,
"acceptedAnswer": {
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"@type": "Question",
"name": "Le suivi médical est-il essentiel ?",
"position": 14,
"acceptedAnswer": {
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}
},
{
"@type": "Question",
"name": "Les activités physiques sont-elles sûres ?",
"position": 15,
"acceptedAnswer": {
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"text": "Certaines activités peuvent être sûres, mais il faut éviter les sports à risque."
}
},
{
"@type": "Question",
"name": "Quels médicaments sont utilisés pour traiter ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les anticonvulsivants comme le valproate et le lamotrigine sont couramment prescrits."
}
},
{
"@type": "Question",
"name": "Y a-t-il des traitements non médicamenteux ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des approches comme la thérapie comportementale et la diététique peuvent aider."
}
},
{
"@type": "Question",
"name": "Comment évaluer l'efficacité du traitement ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'efficacité est évaluée par la réduction des crises et les effets secondaires."
}
},
{
"@type": "Question",
"name": "Les traitements sont-ils à vie ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Souvent, le traitement est à long terme, mais certains peuvent réduire ou arrêter."
}
},
{
"@type": "Question",
"name": "Quels effets secondaires des médicaments ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les effets secondaires peuvent inclure fatigue, vertiges et troubles gastro-intestinaux."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent des blessures dues aux crises et des troubles psychologiques."
}
},
{
"@type": "Question",
"name": "L'épilepsie myoclonique peut-elle affecter la vie quotidienne ?",
"position": 22,
"acceptedAnswer": {
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"text": "Oui, elle peut impacter la vie sociale, professionnelle et la qualité de vie."
}
},
{
"@type": "Question",
"name": "Y a-t-il un risque accru de dépression ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les personnes épileptiques ont un risque plus élevé de dépression et d'anxiété."
}
},
{
"@type": "Question",
"name": "Les crises peuvent-elles entraîner des accidents ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les crises peuvent provoquer des accidents, notamment lors de la conduite."
}
},
{
"@type": "Question",
"name": "Comment gérer les complications psychologiques ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Un soutien psychologique et des thérapies adaptées peuvent aider à gérer ces complications."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque connus ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les antécédents familiaux, les traumatismes crâniens et certaines infections sont des facteurs."
}
},
{
"@type": "Question",
"name": "L'âge influence-t-il le risque d'épilepsie myoclonique ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'épilepsie myoclonique peut débuter à tout âge, mais souvent dans l'enfance ou l'adolescence."
}
},
{
"@type": "Question",
"name": "Les troubles neurologiques augmentent-ils le risque ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, d'autres troubles neurologiques peuvent augmenter le risque d'épilepsie myoclonique."
}
},
{
"@type": "Question",
"name": "Le stress est-il un facteur de risque ?",
"position": 29,
"acceptedAnswer": {
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"text": "Oui, le stress peut déclencher des crises chez les personnes prédisposées."
}
},
{
"@type": "Question",
"name": "Les infections cérébrales sont-elles un risque ?",
"position": 30,
"acceptedAnswer": {
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"text": "Certaines infections, comme la méningite, peuvent augmenter le risque d'épilepsie."
}
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}
]
}
Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 23/04/2025
Contenu vérifié selon les dernières recommandations médicales
10 publications dans cette catégorie
Affiliations :
IRCCS Istituto "Giannina Gaslini", Genova, Italy; Department of Neurosciences, Rehabilitation, Ophthalmology, Genetics, Maternal and Child Health, University of Genova, Genova, Italy.
9 publications dans cette catégorie
Affiliations :
Department of Neurology, Drammen Hospital, Vestre Viken Health Trust, Oslo, Norway.
9 publications dans cette catégorie
Affiliations :
Department of Basic & Clinical Neurosciences, Institute of Psychiatry, Psychology & Neuroscience, King's College London, UK.
MRC Centre for Neurodevelopmental Disorders, King's College London, UK.
King's College Hospital, London, UK.
Evelina London Children's Hospital, London, UK.
7 publications dans cette catégorie
6 publications dans cette catégorie
Affiliations :
Department of Neurology, Drammen Hospital, Vestre Viken Health Trust, Oslo, Norway.
University of Oslo, Oslo, Norway.
6 publications dans cette catégorie
Affiliations :
Department of Radiology, Haeundae Paik Hospital, Inje University College of Medicine, Busan, Republic of Korea.
6 publications dans cette catégorie
Affiliations :
Department of Neurology, Haeundae Paik Hospital, Inje University College of Medicine, Haeundae-ro 875, Haeundae-gu, Busan, 48108, Republic of Korea. smilepkm@hanmail.net.
5 publications dans cette catégorie
Affiliations :
Department of Basic & Clinical Neurosciences, Institute of Psychiatry, Psychology & Neuroscience, King's College London, UK.
MRC Centre for Neurodevelopmental Disorders, King's College London, UK.
Publications dans "Épilepsies myocloniques" :
5 publications dans cette catégorie
Affiliations :
Cardiff & Vale University Health Board, UK.
Publications dans "Épilepsies myocloniques" :
5 publications dans cette catégorie
Affiliations :
Department of Clinical & Experimental Medicine, Pisa University Hospital, Italy.
Publications dans "Épilepsies myocloniques" :
5 publications dans cette catégorie
Affiliations :
Department of Basic & Clinical Neurosciences, Institute of Psychiatry, Psychology & Neuroscience, King's College London, UK.
MRC Centre for Neurodevelopmental Disorders, King's College London, UK.
King's College Hospital, London, UK.
Publications dans "Épilepsies myocloniques" :
4 publications dans cette catégorie
Affiliations :
Toronto Western Hospital, Canada.
Publications dans "Épilepsies myocloniques" :
4 publications dans cette catégorie
Affiliations :
Odense University Hospital, Odense, Denmark.
Publications dans "Épilepsies myocloniques" :
4 publications dans cette catégorie
Affiliations :
Division of Paediatric Neurology, Department of Paediatrics, Faculty of Medicine, University of Malaya, Kuala Lumpur, Malaysia.
Publications dans "Épilepsies myocloniques" :
4 publications dans cette catégorie
Affiliations :
Odense University Hospital, Odense, Denmark.
Publications dans "Épilepsies myocloniques" :
4 publications dans cette catégorie
Affiliations :
Nationwide Children's Hospital, Ohio.
Publications dans "Épilepsies myocloniques" :
4 publications dans cette catégorie
Affiliations :
Division of Neurology, Department of Medicine, Faculty of Medicine, University of Malaya, Kuala Lumpur, Malaysia.
Publications dans "Épilepsies myocloniques" :
4 publications dans cette catégorie
Affiliations :
Danish Epilepsy Centre, Dianalund, Denmark.
University of Copenhagen, Denmark.
Publications dans "Épilepsies myocloniques" :
4 publications dans cette catégorie
Affiliations :
Department of Research and Innovation, Division of Clinical Neuroscience, Oslo University Hospital, Norway.
National Centre for Epilepsy, Oslo University Hospital, Norway.
Publications dans "Épilepsies myocloniques" :
4 publications dans cette catégorie
Affiliations :
Newcastle upon Tyne NHS Foundation Trust, Newcastle, UK.
Publications dans "Épilepsies myocloniques" :
Temporal bone trauma represents a potentially underrecognized condition during head injuries and remains an important consideration during the evaluation of these patients. The temporal bone contains ...
Temporal bone anatomy is highly complex, with a complicated configuration of minute anatomic structures housed in a dense osseous structure. Nevertheless, a robust understanding of this anatomy is ess...
Temporal bone paragangliomas (TBPs) are indolent, classically benign and highly vascular neoplasms of the temporal bone. There are two types of TBPs, tympanomastoid paragangliomas (TMPs) and tympanoju...
Aneurysmal bone cysts are expansile benign lesions associated with compressive destruction and obscure pathogenesis. The most common sites of temporal bone involvement are the petrous apex, squamous p...
This paper reports a right temporal aneurysmal bone cyst in a 51-year-old man who presented clinically with facial palsy, and hearing loss and impaired vestibular function. Magnetic resonance imaging ...
To our knowledge, this is the first report of aneurysmal bone cyst invasion of the inner auditory canal. Our clinical experience indicates that vestibular nerve damage recovery is relatively uncommon....
Dizziness is a common disease. However, approximately 10-40% of patients were diagnosed unknown dizziness even though general, neurological, and otological examinations were performed. The aim of this...
Eighteen temporal bone specimens from 9 patients with undiagnosed dizziness and 20 temporal bone specimens from age-matched 10 normal controls were selected. Cases with a history of dizziness and vert...
Fifteen ears of 9 patients had the findings of vestibular pathology such as a basophilic deposit on cupula (8 ears), on canal wall (7 ears), vestibular nerve loss (8 ears), or vestibular atelectasis (...
We demonstrated some peripheral vestibular pathological findings such as deposit within the semicircular canal, vestibular nerve loss, and vestibular atelectasis and suggested the possible diagnosis o...
Under bone conduction (BC) stimulation, the otic capsule, and surrounding temporal bone, undergoes a complex 3-dimentional (3D) motion that depends on the frequency, location and coupling of the stimu...
Experiments were conducted in 3 fresh frozen cadaver heads, individually on each temporal bone, resulting in a total of 6 samples. The skull bone was stimulated, via the actuator of a BC hearing aid (...
While there were limited differences in the magnitude of the motion across the skull base, there were major differences in the deformation of different sections of the skull. Specifically, the bone ne...
The area around the otic capsule appears rigid up to significantly higher frequencies than the rest of the skull surface, resulting in primarily inertial loading of the cochlear fluid. Further work sh...
Temporal bone mucosal melanomas (MMs) are rare, and patients may experience delays in diagnosis and treatment. Our objective was to better characterize the presentation, diagnosis, treatment modalitie...
PubMed/Medline, CINAHL (EBSCOhost), and Web of Science databases were searched in all languages without restriction of publication dates....
Inclusion criteria included that the article was either a case report or a case series with individual case data. All non-English articles were excluded if the corresponding abstract lacked data on de...
After full-text analysis, data pertaining to demographics, diagnosis, medical and surgical management modalities, and outcomes were extracted....
Data were qualitatively synthesized, and means and averages were obtained for all continuous variables. Overall survival was measured by the Kaplan-Meier method, and significance was measured through ...
Clinicians should suspect temporal bone MM in the differential diagnosis of patients with bloody otorrhea in the context of a chronic serous otitis media or an associated cranial nerve palsy. If suspe...
Giant cell tumor (GCT) is a benign tumor that originates from undifferentiated mesenchymal cells of the bone marrow. The craniums as well as temporal bone are extremely rare locations for GCTs. Clinic...
IgG4-related disease (IgG4-RD) involving the temporal bone is an uncommon and underrecognized pathology often mistaken for malignancy. This systematic review is the first that aims to thoroughly analy...
Ovid MEDLINE, EMBASE, Cochrane Library, and Google Scholar....
We used the following search keywords: "lgG4-RD," "skull," "skull base," "cranial," "temporal bone," "inner ear." We additionally manually searched the bibliographies of relevant articles. The JBI Cri...
We identified 17 studies with 22 cases with temporal bone involvement. The most common presenting symptoms were hearing loss, otalgia, and headache. The mastoid and petrous bone were the most affected...
IgG4-RD of the temporal bone radiologically manifests as space-occupying, lytic lesions; clinically, it presents with vague otological symptoms. Diagnosis involves a thorough workup, with histopatholo...
To evaluate ancillary MRI features which may aid the identification of lateral temporal bone cephaloceles (LTBCs)....
A retrospective cohort study analysed patients with MRI evidence of surgically confirmed spontaneous LTBCs as defined by intracranial contents traversing the tegmen tympani or mastoideum. Cases were i...
Eighteen patients (11 female, 7 male; mean age 59.3 years, age range 42-86 years) with 20 surgically confirmed spontaneous LTBCs (2 bilateral;16 unilateral) were evaluated. A temporal lobe sulcus or o...
A temporal lobe sulcus or CSF cleft extending to or traversing the defect may aid the identification of LTBCs. Isointense CSF tympanomastoid signal, superior semi-circular canal dehiscence and MRI fea...
The study details novel ancillary MRI features of LTBCs which may aid their identification....