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Hémopathies et maladies lymphatiques
Hémopathies
Anémie
Érythroblastopénie chronique acquise
Érythroblastopénie chronique acquise : Questions médicales fréquentes
Diagnostic
5
Érythroblastopénie
Biopsie de la moelle osseuse
Numération globulaire
Réticulocytes
Biopsie de la moelle osseuse
Pathologies hématologiques
Symptômes
5
Enfants
Retard de croissance
Qualité de vie
Dépression
Personnes âgées
Comorbidités
Prévention
5
Antibiotiques
Anti-inflammatoires
Mode de vie sain
Système immunitaire
Traitements
5
Corticostéroïdes
Transfusions sanguines
Transfusions sanguines
Anémie
Immunosuppresseurs
Moelle osseuse
Thérapie génique
Essais cliniques
Surveillance
Analyses sanguines
Complications
5
Leucémie
Cancers hématologiques
Facteurs de risque
5
Maladies auto-immunes
Infections virales
Antécédents familiaux
Maladies sanguines
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"@type": "Question",
"name": "Quels tests sanguins sont nécessaires ?",
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"@type": "Question",
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"@type": "Question",
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"position": 9,
"acceptedAnswer": {
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"@type": "Question",
"name": "Les symptômes varient-ils selon l'âge ?",
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"name": "Quels médicaments sont à éviter ?",
"position": 12,
"acceptedAnswer": {
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"text": "Certains antibiotiques et anti-inflammatoires peuvent déclencher cette condition chez certains patients."
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"name": "Y a-t-il des facteurs environnementaux à surveiller ?",
"position": 13,
"acceptedAnswer": {
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}
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{
"@type": "Question",
"name": "Comment un mode de vie sain aide-t-il ?",
"position": 14,
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"text": "Un mode de vie sain renforce le système immunitaire et peut réduire le risque d'infections."
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"name": "Les vaccinations sont-elles importantes ?",
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"name": "Les transfusions sont-elles toujours nécessaires ?",
"position": 17,
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}
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{
"@type": "Question",
"name": "Quel rôle jouent les immunosuppresseurs ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
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}
},
{
"@type": "Question",
"name": "Y a-t-il des traitements expérimentaux ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des thérapies géniques et des traitements ciblés sont en cours d'évaluation dans des essais cliniques."
}
},
{
"@type": "Question",
"name": "Comment surveiller l'efficacité du traitement ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des analyses sanguines régulières permettent d'évaluer la réponse au traitement."
}
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{
"@type": "Question",
"name": "Quelles complications peuvent survenir ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent des infections, des saignements et des problèmes cardiaques."
}
},
{
"@type": "Question",
"name": "Comment l'anémie affecte-t-elle le cœur ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Une anémie sévère peut entraîner une surcharge cardiaque et des arythmies."
}
},
{
"@type": "Question",
"name": "Les infections sont-elles fréquentes ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les patients peuvent être plus susceptibles aux infections en raison d'une immunité réduite."
}
},
{
"@type": "Question",
"name": "Y a-t-il un risque de leucémie ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Bien que rare, il existe un risque accru de développer des cancers hématologiques."
}
},
{
"@type": "Question",
"name": "Comment gérer les complications ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Un suivi médical régulier et un traitement précoce des infections sont essentiels."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque connus ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des maladies auto-immunes, des infections virales et certains médicaments."
}
},
{
"@type": "Question",
"name": "L'âge influence-t-il le risque ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le risque augmente avec l'âge, surtout chez les personnes de plus de 60 ans."
}
},
{
"@type": "Question",
"name": "Les antécédents familiaux jouent-ils un rôle ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des antécédents familiaux de maladies sanguines peuvent augmenter le risque d'érythroblastopénie."
}
},
{
"@type": "Question",
"name": "Les femmes sont-elles plus à risque ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines études suggèrent que les femmes peuvent être plus touchées, surtout après la grossesse."
}
},
{
"@type": "Question",
"name": "Les infections antérieures augmentent-elles le risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des infections comme le VIH ou l'hépatite peuvent prédisposer à l'érythroblastopénie."
}
}
]
}
]
}
Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 07/03/2025
Contenu vérifié selon les dernières recommandations médicales
5 publications dans cette catégorie
Affiliations :
Department of Hematology and Clinical Oncology, Shinshu University School of Medicine, Matsumoto, Nagano, Japan; Department of Health and Medical Sciences, Graduate School of Medicine, Shinshu University, Matsumoto, Nagano, Japan; Department of Biomedical Laboratory Sciences, Shinshu University School of Medicine, Matsumoto, Japan. Electronic address: fumishi@shinshu-u.ac.jp.
Publications dans "Érythroblastopénie chronique acquise" :
5 publications dans cette catégorie
Affiliations :
Department of Hematology, Peking union medical college hospital, Chinese academy of medical sciences and Peking union medical college, Beijing, 100730, China. hanbingpumch@sina.com.
Publications dans "Érythroblastopénie chronique acquise" :
4 publications dans cette catégorie
Affiliations :
Department of Hematology, Key Laboratory of Hematology of Nanjing Medical University, Collaborative Innovation Center for Cancer Personalized Medicine, The First Affiliated Hospital of Nanjing Medical University, Jiangsu Province Hospital, Guangzhou Road 300#, Nanjing, 210029, Jiangsu Province, China. heguangsheng1972@sina.com.
Publications dans "Érythroblastopénie chronique acquise" :
3 publications dans cette catégorie
Affiliations :
Division of Blood Transfusion, Akita University Hospital.
Publications dans "Érythroblastopénie chronique acquise" :
3 publications dans cette catégorie
Affiliations :
Service de médecine interne, Hôpital Estaing, Centre Hospitalier Universitaire de Clermont-Ferrand, Clermont-Ferrand, France; Université Clermont Auvergne, CHU Clermont-Ferrand, CNRS, Institut Pascal, 63000 Clermont-Ferrand, France. Electronic address: hlobbes@chu-clermontferrand.fr.
Publications dans "Érythroblastopénie chronique acquise" :
3 publications dans cette catégorie
Affiliations :
Department of Hematology, Peking union medical college hospital, Chinese academy of medical sciences and Peking union medical college, Beijing, 100730, China.
Publications dans "Érythroblastopénie chronique acquise" :
3 publications dans cette catégorie
Affiliations :
Department of Hematology, Key Laboratory of Hematology of Nanjing Medical University, Collaborative Innovation Center for Cancer Personalized Medicine, The First Affiliated Hospital of Nanjing Medical University, Jiangsu Province Hospital, Guangzhou Road 300#, Nanjing, 210029, Jiangsu Province, China.
Publications dans "Érythroblastopénie chronique acquise" :
3 publications dans cette catégorie
Affiliations :
Department of Hematology, Key Laboratory of Hematology of Nanjing Medical University, Collaborative Innovation Center for Cancer Personalized Medicine, The First Affiliated Hospital of Nanjing Medical University, Jiangsu Province Hospital, Guangzhou Road 300#, Nanjing, 210029, Jiangsu Province, China.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
King Edward VIII Hospital, Durban, South Africa.
Department of Infectious Diseases, University of KwaZulu-Natal, Durban, South Africa.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
King Edward VIII Hospital, Durban, South Africa.
Department of Infectious Diseases, University of KwaZulu-Natal, Durban, South Africa.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
Department of Infectious Diseases, University of KwaZulu-Natal, Durban, South Africa.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
Department of Infectious Diseases, University of KwaZulu-Natal, Durban, South Africa.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
King Edward VIII Hospital, Durban, South Africa.
Department of Infectious Diseases, University of KwaZulu-Natal, Durban, South Africa.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
Department of Hematology and Clinical Oncology, Shinshu University School of Medicine, Matsumoto, Nagano, Japan.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
Department of Cellular Transplantation Biology, Kanazawa University Graduate School of Medicine, Kanazawa, Japan.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
Department of Hemato-Oncology, International Medical Center, Saitama Medical University, Saitama, Japan.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
Division of Public Health, Department of Social Medicine, Saitama Medical University, Saitama, Japan.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
Department of Hematology, NTT Medical Center Tokyo, Tokyo, Japan.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
Department of Hematology and Oncology, Dokkyo Medical University, Tochigi, Japan.
Publications dans "Érythroblastopénie chronique acquise" :
2 publications dans cette catégorie
Affiliations :
Department of Hematology, General Hospital, Tianjin Medical University, Tianjin, People's Republic of China.
Publications dans "Érythroblastopénie chronique acquise" :
Pure red cell aplasia (PRCA) is a rare hematologic syndrome, characterized by an isolated normocytic anemia with severe reticulocytopenia, and defined by absence or near absence of erythroid precursor...
Acquired pure red cell aplasia (PRCA) is a syndrome characterized by anemia and a marked reduction of erythroid progenitor cells with various etiologies. The 3 major subtypes of PRCA are idiopathic PR...
Pure red cell aplasia (PRCA) is a rare anemia characterised by profound reticulocytopenia caused by a marked reduction in bone marrow erythroblasts, without abnormalities in other blood lineages. Blac...
Pure red cell aplasia (PRCA) is a hematological disorder characterized by anemia with severe reticulocytopenia caused by a marked reduction in erythroid precursors in the bone marrow. PRCA is known to...
A 37-year-old primiparous woman with severe anemia was referred to our center at 27 weeks' gestation. She was diagnosed with PRCA based on bone aspiration findings at 33 weeks' gestation. Magnetic res...
A very rare case of thymoma-associated PRCA during pregnancy was diagnosed without any subjective symptoms and was expectantly managed, resulting in a good prognosis. Although bone marrow aspiration d...
Chronic lymphocytic leukemia (CLL) has long been known for its complications related to immune deregulation, of which autoimmune cytopenias (AIC) were frequently reported. Ibrutinib has dramatically c...
A 70-year-old female was diagnosed with CLL with indications to initiate ibrutinib treatment given progressive bulky disease. She was admitted for advanced fatigue on the 14th day of ibrutinib monothe...
Ibrutinib was discontinued on the day of admission. At the same time, the patient received prednisone and intravenous immunoglobulin (IVIg). Five days later, the Hb did not improve. Cyclosporine A (Cs...
Our case demonstrates a need to evaluate the risk of developing AIC before initiating ibrutinib. For patients with high-risk factors for AIC episodes, the transient addition of other immunosuppressive...
Pure red cell aplasia (PRCA) in neuromyelitis optica spectrum disorder (NMOSD) has not been reported before. This study presents a patient with NMOSD who developed PRCA....
A 54-year-old female was admitted in January 2023 for dysuria and progressive numbness and weakness of lower limbs. She had difficulty standing and walking in a straight line. Both lower limbs were po...
This case suggests that PRCA can be secondary to NMOSD. A comprehensive immune function and bone marrow evaluation might be necessary if abnormal blood cells are found while managing NMOSD....
BACKGROUND Immunotherapy is a novel treatment offering an alternative to traditional chemotherapeutic agents for different malignancies. Hematologic adverse reactions (HARs) related to immune checkpoi...
Pure red-cell aplasia (PRCA) is a syndrome associated with reduced erythroid precursors. This report presents the case of an elderly PRCA patient with significantly proliferated γδT cells and clonal T...
Autoimmune hemolytic anemia (AIHA) and pure red cell aplasia (PRCA) are rare complications of coronavirus disease 2019 (COVID-19). Herein, we report the case of a 28-year-old Japanese man who showed s...
Pure red cell aplasia (PRCA) is characterised by severe normochromic, normocytic anaemia and partial or complete absence of reticulocytes from the peripheral blood. With bone marrow of normal cellular...
To describe the clinical characteristics, treatment and outcomes of adult patients diagnosed with PRCA at Universitas Academic Hospital (UAH) in Bloemfontein, South Africa, from 2010 to 2018....
A retrospective descriptive file review was performed. All adult patients diagnosed with PRCA and treated in the Division of Clinical Haematology at UAH during the study period were included. Variable...
Twenty-seven patients' files were included, with a female predominance (n=22; 81.5%). The median age at diagnosis was 35 years (range 20 - 62). The median number of days from onset of symptoms to date...
In this population, women were disproportionately affected by PRCA. HIV was the single most important cause of acquired PRCA, which was independent of virological control. Parvovirus B19 and drugs wer...