Accurate Molecular Diagnosis of Gaucher Disease Using Clinical Exome Sequencing as a First-Tier Test.


Journal

International journal of molecular sciences
ISSN: 1422-0067
Titre abrégé: Int J Mol Sci
Pays: Switzerland
ID NLM: 101092791

Informations de publication

Date de publication:
24 May 2021
Historique:
received: 19 04 2021
revised: 18 05 2021
accepted: 20 05 2021
entrez: 2 6 2021
pubmed: 3 6 2021
medline: 25 6 2021
Statut: epublish

Résumé

Gaucher disease (GD) is an autosomal recessive lysosomal disorder due to beta-glucosidase gene (

Identifiants

pubmed: 34073924
pii: ijms22115538
doi: 10.3390/ijms22115538
pmc: PMC8197298
pii:
doi:

Substances chimiques

beta-Glucosidase EC 3.2.1.21

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Déclaration de conflit d'intérêts

The authors declare no conflict of interest.

Références

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Auteurs

Stefania Zampieri (S)

Regional Coordinator Centre for Rare Diseases, University Hospital of Udine, 33100 Udine, Italy.

Silvia Cattarossi (S)

Regional Coordinator Centre for Rare Diseases, University Hospital of Udine, 33100 Udine, Italy.

Eleonora Pavan (E)

Regional Coordinator Centre for Rare Diseases, University Hospital of Udine, 33100 Udine, Italy.

Antonio Barbato (A)

Department of Clinical Medicine and Surgery, Federico II University Hospital, 80131 Naples, Italy.

Agata Fiumara (A)

Pediatric Unit, Regional Referral Center for Inherited Metabolic Disease, University of Catania, 95123 Catania, Italy.

Paolo Peruzzo (P)

Regional Coordinator Centre for Rare Diseases, University Hospital of Udine, 33100 Udine, Italy.

Maurizio Scarpa (M)

Regional Coordinator Centre for Rare Diseases, University Hospital of Udine, 33100 Udine, Italy.

Giovanni Ciana (G)

Regional Coordinator Centre for Rare Diseases, University Hospital of Udine, 33100 Udine, Italy.

Andrea Dardis (A)

Regional Coordinator Centre for Rare Diseases, University Hospital of Udine, 33100 Udine, Italy.

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Classifications MeSH