Syndrome des mouvements périodiques nocturnes des membres : Questions médicales fréquentes
Nom anglais: Nocturnal Myoclonus Syndrome
Descriptor UI:D020189
Tree Number:C10.886.659.618
Termes MeSH sélectionnés :
Vulvitis
Questions fréquentes et termes MeSH associés
Diagnostic
5
#1
Comment diagnostique-t-on ce syndrome ?
Le diagnostic repose sur l'observation des mouvements nocturnes et des études du sommeil.
Syndrome des mouvements périodiquesPolysomnographie
#2
Quels tests sont utilisés pour le diagnostic ?
La polysomnographie est le test principal pour évaluer les mouvements et les cycles de sommeil.
PolysomnographieTroubles du sommeil
#3
Quels critères sont utilisés pour le diagnostic ?
Les critères incluent la fréquence des mouvements et leur impact sur la qualité du sommeil.
Syndrome des mouvements périodiquesQualité du sommeil
#4
Le syndrome est-il confondu avec d'autres troubles ?
Oui, il peut être confondu avec le syndrome des jambes sans repos ou d'autres troubles du sommeil.
Syndrome des jambes sans reposTroubles du sommeil
#5
Les antécédents médicaux influencent-ils le diagnostic ?
Oui, des antécédents de troubles du sommeil ou neurologiques peuvent influencer le diagnostic.
Antécédents médicauxTroubles neurologiques
Symptômes
5
#1
Quels sont les symptômes principaux ?
Les symptômes incluent des mouvements involontaires des membres et des réveils fréquents.
Mouvements involontairesRéveils nocturnes
#2
Les mouvements se produisent-ils à des moments précis ?
Oui, ils se produisent généralement pendant les phases de sommeil léger.
Phases de sommeilSommeil léger
#3
Y a-t-il des douleurs associées aux mouvements ?
Les mouvements peuvent causer des douleurs ou de l'inconfort, perturbant le sommeil.
DouleurPerturbation du sommeil
#4
Les symptômes varient-ils d'une personne à l'autre ?
Oui, l'intensité et la fréquence des mouvements peuvent varier considérablement.
Variabilité des symptômesTroubles du sommeil
#5
Les symptômes affectent-ils la qualité de vie ?
Oui, ils peuvent entraîner une fatigue diurne et affecter la qualité de vie globale.
Fatigue diurneQualité de vie
Prévention
5
#1
Peut-on prévenir ce syndrome ?
Il n'existe pas de méthode de prévention garantie, mais une bonne hygiène du sommeil peut aider.
PréventionHygiène du sommeil
#2
Le stress influence-t-il le syndrome ?
Oui, le stress peut aggraver les symptômes, donc la gestion du stress est conseillée.
StressGestion du stress
#3
L'alimentation joue-t-elle un rôle ?
Une alimentation équilibrée peut contribuer à un meilleur sommeil et réduire les symptômes.
Alimentation équilibréeSommeil
#4
L'exercice physique aide-t-il ?
Oui, l'exercice régulier peut améliorer la qualité du sommeil et réduire les mouvements nocturnes.
Exercice physiqueQualité du sommeil
#5
Les habitudes de sommeil influencent-elles le syndrome ?
Oui, des habitudes de sommeil régulières peuvent aider à réduire l'incidence des mouvements.
Habitudes de sommeilMouvements nocturnes
Traitements
5
#1
Quels traitements sont disponibles ?
Les traitements incluent des médicaments comme les benzodiazépines et des thérapies comportementales.
BenzodiazépinesThérapies comportementales
#2
Les changements de mode de vie aident-ils ?
Oui, des changements comme une meilleure hygiène du sommeil peuvent réduire les symptômes.
Hygiène du sommeilChangements de mode de vie
#3
Les médicaments sont-ils toujours nécessaires ?
Pas toujours, certains patients peuvent gérer les symptômes avec des approches non médicamenteuses.
Approches non médicamenteusesGestion des symptômes
#4
Y a-t-il des effets secondaires aux traitements ?
Oui, certains médicaments peuvent provoquer des effets secondaires comme la somnolence.
Effets secondairesSomnolence
#5
Les traitements sont-ils efficaces à long terme ?
L'efficacité peut varier, et un suivi régulier est souvent nécessaire pour ajuster le traitement.
Suivi médicalEfficacité des traitements
Complications
5
#1
Quelles complications peuvent survenir ?
Les complications incluent la fatigue chronique et des troubles de l'humeur comme l'anxiété.
Fatigue chroniqueTroubles de l'humeur
#2
Le syndrome peut-il affecter la santé mentale ?
Oui, les troubles du sommeil peuvent contribuer à des problèmes de santé mentale.
Santé mentaleTroubles du sommeil
#3
Y a-t-il un risque accru d'autres maladies ?
Oui, les troubles du sommeil peuvent augmenter le risque de maladies cardiovasculaires.
Maladies cardiovasculairesTroubles du sommeil
#4
Les complications sont-elles réversibles ?
Certaines complications peuvent être réversibles avec un traitement approprié et des changements de mode de vie.
RéversibilitéTraitement
#5
Comment les complications sont-elles gérées ?
La gestion des complications implique souvent une approche multidisciplinaire incluant médecins et psychologues.
Gestion des complicationsApproche multidisciplinaire
Facteurs de risque
5
#1
Quels sont les facteurs de risque connus ?
Les facteurs incluent l'âge avancé, des troubles neurologiques et des antécédents familiaux.
Âge avancéAntécédents familiaux
#2
Le sexe influence-t-il le risque ?
Oui, les hommes sont souvent plus touchés que les femmes par ce syndrome.
SexePrévalence
#3
Les troubles du sommeil augmentent-ils le risque ?
Oui, des troubles comme l'apnée du sommeil peuvent augmenter le risque de ce syndrome.
Apnée du sommeilTroubles du sommeil
#4
Les médicaments peuvent-ils être un facteur de risque ?
Oui, certains médicaments, comme les antidépresseurs, peuvent exacerber les symptômes.
AntidépresseursFacteurs de risque
#5
Le mode de vie influence-t-il le risque ?
Oui, un mode de vie sédentaire et une mauvaise hygiène du sommeil peuvent augmenter le risque.
Mode de vie sédentaireHygiène du sommeil
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},
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"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un mode de vie sédentaire et une mauvaise hygiène du sommeil peuvent augmenter le risque."
}
}
]
}
]
}
From the Children's Neurosciences (T.R., M.L.), Evelina London Children's Hospital at Guy's and St Thomas' NHS Foundation Trust, King's Health Partners Academic Health Science Centre; Department Women and Children's Health (T.R., M.L.), School of Life Course Sciences (SoLCS), King's College London, UK; Division of Neurology (E.A.Y.), Department of Pediatrics, Neurosciences and Mental Health (RI), The Hospital for Sick Children; Faculty of Medicine (E.A.Y.), The University of Toronto, Ontario, Canada; Department of Pediatrics (Y.K.) and Department of Neurology (Y.K.), Memorial Sloan Kettering Cancer Center, New York, NY; Department of Pediatrics (Y.K.), Weill Medical College of Cornell University, New York; Children and Young People's Unit (Paola Angelini), The Royal Marsden, Downs Road, Sutton, Surrey; UCL Great Ormond Street Institute of Child Health (C.H.), Department of Neurology, Great Ormond Street Hospital for Children, London; Oxford Autoimmune Neurology Group (S.R.I.), Nuffield Department of Clinical Neurosciences, University of Oxford; Department of Neurology (S.R.I.), Oxford University Hospitals NHS Foundation Trust, UK; SiRIC RTOP (G.S.), Translational Research Department, PSL Research University, Institut Curie Research Center; INSERM U830 (G.S.), PSL Research University, Institut Curie Research Center; SIREDO Center: Care (G.S.), Innovation and Research for Children, Adolescents and Young Adults with Cancer, Institut Curie, Paris, France; Department of Child and Adolescent Psychiatry (P.S.), King's College London; Centre for Interventional Paediatric Psychopharmacology and Rare Diseases (CIPPRD) Research Team (P.S.), South London and Maudsley NHS Foundation Trust, London, UK; Baylor College of Medicine (T.L.), Texas Children's Hospital, Houston; Kids Neuroscience Centre (R.C.D.), The Children's Hospital at Westmead, Westmead, NSW, Australia; TY Nelson Department of Neurology and Neurosurgery (R.C.D.), The Children's Hospital at Westmead; The Children's Hospital at Westmead Clinical School (R.C.D.), Faculty of Medicine, University of Sydney, NSW, Australia; Pediatric Neurology Department (K.D.), Assistance Publique-Hôpitaux de Paris, Hôpitaux Universitaires Paris Saclay, Bicêtre Hospital; National Referral Center for Rare Inflammatory and Auto-Immune Brain and Spinal Diseases (K.D.); Inserm UMR 1184 (K.D.), Immunology of Viral Infections and Autoimmune Diseases, CEA, IDMIT, Le Kremlin Bicêtre, France; Department of Pediatric Hematology and Oncology (B.H.), University Children's Hospital, Koln; Division of Child Neurology (A.K.), University Children's Hospital Bern Inselspital, University of Bern; Department of Pediatric Neurology (A.K.), University Children's Hospital Basel, Switzerland; Department of Pediatrics (Pedro de Alarcon), University of Illinois College of Medicine at Peoria, Peoria IL; Department of Neurology (M.P.G.), Boston Children's Hospital, Harvard Medical School, MA; Division of Neurology (W.G.M.), Department of Pediatrics, Children's Hospital Los Angeles; and Department of Neurology (W.G.M.), Keck School of Medicine at the University of Southern California, Los Angeles.
Publications dans "Syndrome des mouvements périodiques nocturnes des membres" :
From the Children's Neurosciences (T.R., M.L.), Evelina London Children's Hospital at Guy's and St Thomas' NHS Foundation Trust, King's Health Partners Academic Health Science Centre; Department Women and Children's Health (T.R., M.L.), School of Life Course Sciences (SoLCS), King's College London, UK; Division of Neurology (E.A.Y.), Department of Pediatrics, Neurosciences and Mental Health (RI), The Hospital for Sick Children; Faculty of Medicine (E.A.Y.), The University of Toronto, Ontario, Canada; Department of Pediatrics (Y.K.) and Department of Neurology (Y.K.), Memorial Sloan Kettering Cancer Center, New York, NY; Department of Pediatrics (Y.K.), Weill Medical College of Cornell University, New York; Children and Young People's Unit (Paola Angelini), The Royal Marsden, Downs Road, Sutton, Surrey; UCL Great Ormond Street Institute of Child Health (C.H.), Department of Neurology, Great Ormond Street Hospital for Children, London; Oxford Autoimmune Neurology Group (S.R.I.), Nuffield Department of Clinical Neurosciences, University of Oxford; Department of Neurology (S.R.I.), Oxford University Hospitals NHS Foundation Trust, UK; SiRIC RTOP (G.S.), Translational Research Department, PSL Research University, Institut Curie Research Center; INSERM U830 (G.S.), PSL Research University, Institut Curie Research Center; SIREDO Center: Care (G.S.), Innovation and Research for Children, Adolescents and Young Adults with Cancer, Institut Curie, Paris, France; Department of Child and Adolescent Psychiatry (P.S.), King's College London; Centre for Interventional Paediatric Psychopharmacology and Rare Diseases (CIPPRD) Research Team (P.S.), South London and Maudsley NHS Foundation Trust, London, UK; Baylor College of Medicine (T.L.), Texas Children's Hospital, Houston; Kids Neuroscience Centre (R.C.D.), The Children's Hospital at Westmead, Westmead, NSW, Australia; TY Nelson Department of Neurology and Neurosurgery (R.C.D.), The Children's Hospital at Westmead; The Children's Hospital at Westmead Clinical School (R.C.D.), Faculty of Medicine, University of Sydney, NSW, Australia; Pediatric Neurology Department (K.D.), Assistance Publique-Hôpitaux de Paris, Hôpitaux Universitaires Paris Saclay, Bicêtre Hospital; National Referral Center for Rare Inflammatory and Auto-Immune Brain and Spinal Diseases (K.D.); Inserm UMR 1184 (K.D.), Immunology of Viral Infections and Autoimmune Diseases, CEA, IDMIT, Le Kremlin Bicêtre, France; Department of Pediatric Hematology and Oncology (B.H.), University Children's Hospital, Koln; Division of Child Neurology (A.K.), University Children's Hospital Bern Inselspital, University of Bern; Department of Pediatric Neurology (A.K.), University Children's Hospital Basel, Switzerland; Department of Pediatrics (Pedro de Alarcon), University of Illinois College of Medicine at Peoria, Peoria IL; Department of Neurology (M.P.G.), Boston Children's Hospital, Harvard Medical School, MA; Division of Neurology (W.G.M.), Department of Pediatrics, Children's Hospital Los Angeles; and Department of Neurology (W.G.M.), Keck School of Medicine at the University of Southern California, Los Angeles.
Publications dans "Syndrome des mouvements périodiques nocturnes des membres" :
From the Children's Neurosciences (T.R., M.L.), Evelina London Children's Hospital at Guy's and St Thomas' NHS Foundation Trust, King's Health Partners Academic Health Science Centre; Department Women and Children's Health (T.R., M.L.), School of Life Course Sciences (SoLCS), King's College London, UK; Division of Neurology (E.A.Y.), Department of Pediatrics, Neurosciences and Mental Health (RI), The Hospital for Sick Children; Faculty of Medicine (E.A.Y.), The University of Toronto, Ontario, Canada; Department of Pediatrics (Y.K.) and Department of Neurology (Y.K.), Memorial Sloan Kettering Cancer Center, New York, NY; Department of Pediatrics (Y.K.), Weill Medical College of Cornell University, New York; Children and Young People's Unit (Paola Angelini), The Royal Marsden, Downs Road, Sutton, Surrey; UCL Great Ormond Street Institute of Child Health (C.H.), Department of Neurology, Great Ormond Street Hospital for Children, London; Oxford Autoimmune Neurology Group (S.R.I.), Nuffield Department of Clinical Neurosciences, University of Oxford; Department of Neurology (S.R.I.), Oxford University Hospitals NHS Foundation Trust, UK; SiRIC RTOP (G.S.), Translational Research Department, PSL Research University, Institut Curie Research Center; INSERM U830 (G.S.), PSL Research University, Institut Curie Research Center; SIREDO Center: Care (G.S.), Innovation and Research for Children, Adolescents and Young Adults with Cancer, Institut Curie, Paris, France; Department of Child and Adolescent Psychiatry (P.S.), King's College London; Centre for Interventional Paediatric Psychopharmacology and Rare Diseases (CIPPRD) Research Team (P.S.), South London and Maudsley NHS Foundation Trust, London, UK; Baylor College of Medicine (T.L.), Texas Children's Hospital, Houston; Kids Neuroscience Centre (R.C.D.), The Children's Hospital at Westmead, Westmead, NSW, Australia; TY Nelson Department of Neurology and Neurosurgery (R.C.D.), The Children's Hospital at Westmead; The Children's Hospital at Westmead Clinical School (R.C.D.), Faculty of Medicine, University of Sydney, NSW, Australia; Pediatric Neurology Department (K.D.), Assistance Publique-Hôpitaux de Paris, Hôpitaux Universitaires Paris Saclay, Bicêtre Hospital; National Referral Center for Rare Inflammatory and Auto-Immune Brain and Spinal Diseases (K.D.); Inserm UMR 1184 (K.D.), Immunology of Viral Infections and Autoimmune Diseases, CEA, IDMIT, Le Kremlin Bicêtre, France; Department of Pediatric Hematology and Oncology (B.H.), University Children's Hospital, Koln; Division of Child Neurology (A.K.), University Children's Hospital Bern Inselspital, University of Bern; Department of Pediatric Neurology (A.K.), University Children's Hospital Basel, Switzerland; Department of Pediatrics (Pedro de Alarcon), University of Illinois College of Medicine at Peoria, Peoria IL; Department of Neurology (M.P.G.), Boston Children's Hospital, Harvard Medical School, MA; Division of Neurology (W.G.M.), Department of Pediatrics, Children's Hospital Los Angeles; and Department of Neurology (W.G.M.), Keck School of Medicine at the University of Southern California, Los Angeles.
Publications dans "Syndrome des mouvements périodiques nocturnes des membres" :
From the Department of Neurology (J.D.S.), Massachusetts General Hospital, Boston; Department of Neurology (J.D.S., J.M.K., M.P.G.), Boston Children's Hospital, MA; Harvard Medical School (J.D.S., K.D.M.), Boston, MA; Division of Neurology (J.D.S.), Department of Pediatrics, Children's Hospital of Los Angeles, CA; Department of Neurology (J.D.S.), Keck School of Medicine at the University of Southern California, Los Angeles; Department of Pediatrics (R.C., T.C.C.), University of Utah School of Medicine, Salt Lake City; Department of Neurology and Neurotherapeutics (B.M.G.), The University of Texas Southwestern Medical Center at Dallas, TX; UCSF Weill Institute for Neurosciences (E.W.), Department of Neurology, University of California San Francisco, CA; Computational Health Informatics Program (S.W.K., K.D.M.), Boston Children's Hospital, MA; and Department of Pediatrics (S.W.K., K.D.M.), Boston Children's Hospital, MA. jdsantoro@chla.usc.edu.
Publications dans "Syndrome des mouvements périodiques nocturnes des membres" :
Plasma cell vulvitis (PCV) is a rare chronic inflammatory disorder, where the symptoms can be severe and may affect patient's quality of life. However, there are currently no evidence-based treatment ...
A systematic search was conducted of publication between 1952 and August 2020 via MEDLINE, Embase, and Emcare. All publications that evaluated the efficacy of treatments for patients with PCV were inc...
To date, there are no randomized controlled trials evaluating the efficacy of different treatment options. There are also no studies that assess the impact of treatment on quality of life. Topical cor...
Although descriptive studies support the use of topical corticosteroids and, to a lesser degree, topical calcineurin inhibitors and imiquimod, this review highlights the need for standardized outcome ...
The combination of lichenoid and granulomatous inflammation is uncommon in vulval biopsies. We present a series of 5 patients with lichenoid and granulomatous vulvitis, presenting with clinical change...
This systematic review aimed to present the available literature on plasma cell vulvitis (PCV), a relatively uncommon form of inflammatory vulvovaginal dermatitis....
A literature search was performed in PubMed, Science Direct, and Google Scholar using the following key words: "plasma cell vulvitis," "Zoon vulvitis," and "vulvitis circumscripta plasmacellularis." S...
Thirty-nine articles met inclusion criteria, including 38 case reports and 1 observational study, with a total of 96 cases of PCV reported. The mean age of diagnosis was 52.9 years, with an age range ...
Clinical research is needed to better determine the diagnostic criteria and to assess the efficacy of treatment options for PCV....
The etiology of plasma cell vulvitis (PCV) is debated. The authors aimed to test the hypothesis that PCV could be divided into 2 clinical phenotypes....
Patients with a clinico-pathological diagnosis of PCV and with available vulvar photos seen in a vulvar clinic were retrospectively studied. The cases of PCV were divided into 2 groups: non-lichen-ass...
Thirty-five patients (20 primary and 15 secondary PCV) were included. The 2 groups did not differ in terms of age (mean, 65; range, 50-85) or menopausal status. Primary PCV was located exclusively on ...
Plasma cell vulvitis can be divided clinically into 2 phenotypes. Primary non-lichen-associated PCV is restricted to the vestibule and could be the vulvar counterpart of atrophic vaginitis. Secondary ...
The aim of the study was to identify whether desquamative inflammatory vaginitis (DIV) and plasma cell vulvitis (PCV) are distinct clinicopathologic entities....
The pathology database identified biopsies described as "vaginitis" or "vulvitis" occurring in nonkeratinized epithelium or mucocutaneous junction. Exclusions were age less than 18 years, unavailable ...
There were 36 specimens classified as DIV and 18 as PCV from 51 women with mean age of 51 years; 3 (6%) had concurrent biopsies with both. Pain was more common in PCV, but rates of discharge, itch, an...
Desquamative inflammatory vaginitis and PCV have overlapping symptoms, signs, and histopathologic features. They may represent a single condition of hemorrhagic vestibulovaginitis with varying manifes...
Group A streptococcus (GAS) vulvitis is rare, mainly reported in association with vaginitis. We examined the clinical features of GAS vulvitis in adults, the presence of other infected sites, and its ...
We retrospectively analyzed the medical files and photographs of adult patients with bacteriologically confirmed GAS vulvitis seen at 3 private clinics. Coexisting infected sites, associated dermatolo...
Nineteen patients (mean age = 52.2 [range = 23-83] years) with vulvar GAS infections were identified. The vulvar symptoms consisted of pain (11 cases), pruritus (9), burning (4), and discharge (10). T...
In most adult women, GAS vulvitis is associated with a vaginal infection that may be asymptomatic. A bilateral, oozing, and edematous or fissured erythema involving the vulvar or anovulvar area is sug...
A 37-yr-old patient previously diagnosed with human immunodeficiency virus initially presented with a genital lesion which upon histologic assessment was diagnosed as a pseudotumor associated with her...
Mucinous metaplasia of the vulva (MMV) is a histopathologic finding that has been reported previously in only 3 patients and needs to be distinguished from vulvar extramammary Paget disease. We report...
Sodium-glucose co-transporter 2 (SGLT2) inhibitors, or gliflozins, are used as mono or combined therapy in the management of diabetes. Genital infections are the most common reported adverse effect, a...
Demographic and treatment outcomes of 11 patients with characteristic inflammatory changes after starting SGLT2 inhibitors were extracted from electronic records. Ninety-one percent (n = 10) had candi...
SGLT2 inhibitors can result in characteristic inflammatory vulvitis. Treatment with topical agents and single-dose antifungals may allow patients to continue their therapy to achieve improved glycemic...
Plasma cell vulvitis (PCV) is a rare inflammatory vulvar condition. The aim of this study was to describe the natural history, treatment, impact on quality of life, and factors associated with poorer ...
A mixed-methods approach was used combining a retrospective case note review with a cross-sectional telephone questionnaire. All women diagnosed with PCV attending the vulvar disorders clinic at the R...
During the 10-year study period, 7,500 women were seen at the vulval disorders clinic, of whom 21 were diagnosed with PCV (0.28%). Of these women, 12 who were followed up for more than 12 months agree...
Women with PCV can remain symptomatic for many years with significant impacts on quality of life, which may consequently require long-term support and follow-up....