Journal

Journal of medical genetics
ISSN: 1468-6244
Titre abrégé: J Med Genet
Pays: England
ID NLM: 2985087R

Informations de publication

Date de publication:
01 2020
Historique:
received: 19 01 2019
revised: 11 06 2019
accepted: 18 06 2019
pubmed: 14 7 2019
medline: 11 6 2020
entrez: 14 7 2019
Statut: ppublish

Résumé

Capillary malformation-arteriovenous malformation is an autosomal dominant disorder, characterised by capillary malformations and increased risk of fast-flow vascular malformations, caused by loss-of-function mutations in the DNA was extracted from peripheral blood lymphocytes, saliva or vascular malformation tissues from four patients. Four distinct mosaic This study shows that

Sections du résumé

BACKGROUND
Capillary malformation-arteriovenous malformation is an autosomal dominant disorder, characterised by capillary malformations and increased risk of fast-flow vascular malformations, caused by loss-of-function mutations in the
METHODS
DNA was extracted from peripheral blood lymphocytes, saliva or vascular malformation tissues from four patients.
RESULTS
Four distinct mosaic
CONCLUSION
This study shows that

Identifiants

pubmed: 31300548
pii: jmedgenet-2019-106024
doi: 10.1136/jmedgenet-2019-106024
doi:

Substances chimiques

RASA1 protein, human 0
p120 GTPase Activating Protein 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

48-52

Informations de copyright

© Author(s) (or their employer(s)) 2020. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: None declared.

Auteurs

Nicole Revencu (N)

Center for Human Genetics, Cliniques universitaires Saint-Luc, Université catholique de Louvain, Brussels, Belgium nicole.revencu@uclouvain.be.
Center for Vascular Anomalies, Division of Plastic Surgery, Cliniques universitaires Saint-Luc, Université catholique de Louvain, Brussels, Belgium; VASCERN VASCA European Reference Center.

Elodie Fastre (E)

Center for Human Genetics, Cliniques universitaires Saint-Luc, Université catholique de Louvain, Brussels, Belgium.

Marie Ravoet (M)

Center for Human Genetics, Cliniques universitaires Saint-Luc, Université catholique de Louvain, Brussels, Belgium.

Raphaël Helaers (R)

Human Molecular Genetics, de Duve Institute, Université catholique de Louvain, Brussels, Belgium.

Pascal Brouillard (P)

Human Molecular Genetics, de Duve Institute, Université catholique de Louvain, Brussels, Belgium.

Annouk Bisdorff-Bresson (A)

Neuroradiology, Center for arteriovenous malformations in children and adults, Hopital Lariboisiere, Paris, France.

Clara W T Chung (CWT)

Department of Clinical Genetics, Liverpool Hospital, Liverpool, New South Wales, Australia.

Marion Gerard (M)

Service de Génétique Médicale, Centre Hospitalier Universitaire de Caen, Caen, France.

Veronika Dvorakova (V)

Dermatology Clinic, Our Lady's Children's Hospital Crumlin, Dublin, Ireland.

Alan D Irvine (AD)

Dermatology Clinic, Our Lady's Children's Hospital Crumlin, Dublin, Ireland.

Laurence M Boon (LM)

Human Molecular Genetics, de Duve Institute, Université catholique de Louvain, Brussels, Belgium.
Center for Vascular Anomalies, Division of Plastic Surgery, Cliniques universitaires Saint-Luc, Université catholique de Louvain, Brussels, Belgium; VASCERN VASCA European Reference Center.

Miikka Vikkula (M)

Center for Vascular Anomalies, Division of Plastic Surgery, Cliniques universitaires Saint-Luc, Université catholique de Louvain, Brussels, Belgium; VASCERN VASCA European Reference Center.
Human Molecular Genetics, de Duve Institute, Université catholique de Louvain, Brussels, Belgium.

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Classifications MeSH